Malignant melanocytic peripheral nerve sheath tumor of mediastinum

MedGen UID:: 233154
•Concept ID:: C1334600
•: Neoplastic Process

Synonyms:	Malignant Mediastinal Melanocytic Peripheral Nerve Sheath Tumor; malignant mediastinal melanocytic peripheral nerve sheath tumor; malignant mediastinal melanocytic peripheral nerve sheath tumour; malignant melanocytic neoplasm of the peripheral nerve sheath of mediastinum; Malignant Melanocytic Peripheral Nerve Sheath Tumor of Mediastinum; malignant melanocytic peripheral nerve sheath tumor of mediastinum; Malignant Melanotic Peripheral Nerve Sheath Tumor of the Mediastinum; malignant melanotic peripheral nerve sheath tumor of the mediastinum; malignant melanotic peripheral nerve sheath tumour of the mediastinum; Mediastinal Melanocytic MPNST; mediastinal melanocytic MPNST; mediastinum malignant melanocytic neoplasm of the peripheral nerve sheath

Monarch Initiative:	MONDO:0004098

Definition

A rare variant of malignant peripheral nerve sheath tumor that arises from the mediastinum. It is characterized by the presence of malignant cells that contain melanin. [from NCI]