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Teratoid Hepatoblastoma

MedGen UID:
233714
•Concept ID:
C1334786
•
Neoplastic Process
Synonym: Mixed Hepatoblastoma with Teratoid Features

Definition

A mixed epithelial and mesenchymal hepatoblastoma characterized by the presence of heterologous elements. The latter include neuroectoderm, endoderm, or melanin-holding cells. Muscle, cartilage and osteoid may or may not be present. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVTeratoid Hepatoblastoma

Professional guidelines

PubMed

Changing treatment and outcome of children with hepatoblastoma: analysis of a single center experience over the last 20 years.
Ismail H, Broniszczak D, Kaliciński P, Dembowska-Bagińska B, Perek D, Teisseyre J, Kluge P, Kościesza A, Lembas A, Markiewicz M
J Pediatr Surg 2012 Jul;47(7):1331-9. doi: 10.1016/j.jpedsurg.2011.11.073. PMID: 22813792

Recent clinical studies

Diagnosis

Teratoid Hepatoblastoma With Yolk Sac-Like and Neuroendocrine Elements.
Smith JA, Ranganathan S
Pediatr Dev Pathol 2020 Sep-Oct;23(5):387-391. Epub 2020 May 19 doi: 10.1177/1093526620915987. PMID: 32425118
Teratoid hepatoblastoma with abundant neuroendocrine and squamous differentiation with extensive parenchymal metastasis.
Rabah R
Arch Pathol Lab Med 2012 Aug;136(8):911-4. doi: 10.5858/arpa.2012-0212-CR. PMID: 22849740
Teratoid hepatoblastoma.
Buccoliero AM, Castiglione F, Maio V, Moncini D, Sardi I, Taddei A, Martin A, Messineo A, Taddei GL
Fetal Pediatr Pathol 2008;27(6):274-81. doi: 10.1080/15513810802448100. PMID: 19065325
Teratoid hepatoblastoma: multidirectional differentiation of stem cell of the liver.
Kim L, Park YN, Kim SE, Noh TW, Park C
Yonsei Med J 2001 Aug;42(4):431-5. doi: 10.3349/ymj.2001.42.4.431. PMID: 11519086

Therapy

Hepatoblastoma.
Sharma D, Subbarao G, Saxena R
Semin Diagn Pathol 2017 Mar;34(2):192-200. Epub 2016 Dec 23 doi: 10.1053/j.semdp.2016.12.015. PMID: 28126357
Teratoid hepatoblastoma with abundant cholangioblastic component in a child with full trisomy 13.
Zhou S, Ranganathan S, Venkatramani R, Gomulia E, Wang L
Pediatr Dev Pathol 2013 Nov-Dec;16(6):438-41. Epub 2013 Aug 8 doi: 10.2350/13-06-1348-CR.1. PMID: 23927400

Prognosis

Hepatoblastoma.
Sharma D, Subbarao G, Saxena R
Semin Diagn Pathol 2017 Mar;34(2):192-200. Epub 2016 Dec 23 doi: 10.1053/j.semdp.2016.12.015. PMID: 28126357
Teratoid hepatoblastoma with abundant neuroendocrine and squamous differentiation with extensive parenchymal metastasis.
Rabah R
Arch Pathol Lab Med 2012 Aug;136(8):911-4. doi: 10.5858/arpa.2012-0212-CR. PMID: 22849740
Teratoid hepatoblastoma. The nosologic dilemma of solid embryonic neoplasms of childhood.
Manivel C, Wick MR, Abenoza P, Dehner LP
Cancer 1986 Jun 1;57(11):2168-74. doi: 10.1002/1097-0142(19860601)57:11<2168::aid-cncr2820571115>3.0.co;2-m. PMID: 2421866

Clinical prediction guides

Teratoid hepatoblastoma: multidirectional differentiation of stem cell of the liver.
Kim L, Park YN, Kim SE, Noh TW, Park C
Yonsei Med J 2001 Aug;42(4):431-5. doi: 10.3349/ymj.2001.42.4.431. PMID: 11519086
Teratoid hepatoblastoma. The nosologic dilemma of solid embryonic neoplasms of childhood.
Manivel C, Wick MR, Abenoza P, Dehner LP
Cancer 1986 Jun 1;57(11):2168-74. doi: 10.1002/1097-0142(19860601)57:11<2168::aid-cncr2820571115>3.0.co;2-m. PMID: 2421866

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