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Low Grade Paranasal Sinus Sarcoma

MedGen UID:: 235263
•Concept ID:: C1334426
•: Neoplastic Process

Synonyms:

Low Grade Accessory Sinus Sarcoma; Low Grade Sarcoma of Accessory Sinus; Low Grade Sarcoma of Paranasal Sinus; Low Grade Sarcoma of the Accessory Sinus; Low Grade Sarcoma of the Paranasal Sinus

Definition

A malignant soft tissue neoplasm that arises from the paranasal sinus. It is characterized by the presence of low-grade histologic features. [from NCI]

Term Hierarchy

GTR
MeSH

CClinical test, RResearch test, OOMIM, GGeneReviews, VClinVar

CROGVLow Grade Paranasal Sinus Sarcoma

Head and Neck Disorder
- Head and neck neoplasm
  - Head and neck cancer
    - Malignant Sinonasal Neoplasm
      - Malignant Paranasal Sinus Neoplasm
        Paranasal sinus sarcoma
        Low Grade Paranasal Sinus Sarcoma

Professional guidelines

PubMed

Challenging differential diagnoses in small biopsies from the sinonasal tract.

Israel AK, Cracolici V, Griffith CC
Semin Diagn Pathol 2023 Sep;40(5):321-332. Epub 2023 Apr 14 doi: 10.1053/j.semdp.2023.04.011. PMID: 37085435

Soft Tissue Special Issue: Biphenotypic Sinonasal Sarcoma: A Review with Emphasis on Differential Diagnosis.

Gross J, Fritchie K
Head Neck Pathol 2020 Mar;14(1):33-42. Epub 2020 Jan 16 doi: 10.1007/s12105-019-01092-4. PMID: 31950469 Free PMC Article

Biphenotypic sinonasal sarcoma: A series of six cases with evaluation of role of β-catenin immunohistochemistry in differential diagnosis.

Kakkar A, Rajeshwari M, Sakthivel P, Sharma MC, Sharma SC
Ann Diagn Pathol 2018 Apr;33:6-10. Epub 2017 Nov 8 doi: 10.1016/j.anndiagpath.2017.11.005. PMID: 29566950

See all (3)

Recent clinical studies

Etiology

Risk Factors for Recurrence and the Role of Radiotherapy in Low-grade Myofibroblastic Sarcoma: A Systematic Review.

Mamikunian G, Ziegler A, Block A, Thorpe E
Am J Clin Oncol 2023 Sep 1;46(9):420-425. Epub 2023 Jun 26 doi: 10.1097/COC.0000000000001025. PMID: 37358303

Challenging differential diagnoses in small biopsies from the sinonasal tract.

Israel AK, Cracolici V, Griffith CC
Semin Diagn Pathol 2023 Sep;40(5):321-332. Epub 2023 Apr 14 doi: 10.1053/j.semdp.2023.04.011. PMID: 37085435

Biphenotypic sinonasal sarcoma: European multicentre case-series and systematic literature review.

Turri-Zanoni M, Dalfino G, Lechner M, Dallan I, Battaglia P, Facco C, Franzi F, Gravante G, Ferrari M, Terzakis D, Jay A, Forster MD, Ambrosoli AL, Bignami M, Georgalas C, Herman P, Nicolai P, Lund VJ, Castelnuovo P
Acta Otorhinolaryngol Ital 2022 Dec;42(6):545-553. doi: 10.14639/0392-100X-N2087. PMID: 36654521 Free PMC Article

A Rare Pathology: Low-Grade Fibromyxoid Sarcoma of the Maxilla.

Spalthoff S, Bredt M, Gellrich NC, Jehn P
J Oral Maxillofac Surg 2016 Jan;74(1):219.e1-10. Epub 2015 Sep 25 doi: 10.1016/j.joms.2015.09.018. PMID: 26455471

Sarcomas of the head and neck.

Potter BO, Sturgis EM
Surg Oncol Clin N Am 2003 Apr;12(2):379-417. doi: 10.1016/s1055-3207(03)00005-x. PMID: 12916461

See all (17)

Diagnosis

Challenging differential diagnoses in small biopsies from the sinonasal tract.

Israel AK, Cracolici V, Griffith CC
Semin Diagn Pathol 2023 Sep;40(5):321-332. Epub 2023 Apr 14 doi: 10.1053/j.semdp.2023.04.011. PMID: 37085435

High-grade transformation of low-grade biphenotypic sinonasal sarcoma: Radiological, morphophenotypic variation and confirmatory molecular analysis.

Bell D, Phan J, DeMonte F, Hanna EY
Ann Diagn Pathol 2022 Apr;57:151889. Epub 2022 Jan 10 doi: 10.1016/j.anndiagpath.2021.151889. PMID: 35030392

Low-grade myofibroblastic sarcoma of maxillary sinus and buccal mucosa: Two rare cases and review of the literature.

Ghosh A, Bandopadhyay A, Sarkar R
Indian J Pathol Microbiol 2019 Jan-Mar;62(1):119-121. doi: 10.4103/IJPM.IJPM_99_18. PMID: 30706874

Biphenotypic Sinonasal Sarcoma: A Review and Update.

Carter CS, East EG, McHugh JB
Arch Pathol Lab Med 2018 Oct;142(10):1196-1201. doi: 10.5858/arpa.2018-0207-RA. PMID: 30281368

Low-Grade Sinonasal Sarcoma With Neural and Myogenic Features: A Recently Discovered Entity With Unique Features and Diagnostic Challenge.

Triki M, Ayadi L
Arch Pathol Lab Med 2017 May;141(5):718-721. doi: 10.5858/arpa.2016-0133-RS. PMID: 28447903

See all (43)

Therapy

Particle beam radiation therapy for sinonasal malignancies: Single institutional experience at the Shanghai Proton and Heavy Ion Center.

Hu W, Hu J, Huang Q, Gao J, Yang J, Qiu X, Kong L, Lu JJ
Cancer Med 2020 Nov;9(21):7914-7924. Epub 2020 Sep 25 doi: 10.1002/cam4.3393. PMID: 32977357 Free PMC Article

Treatment planning and verification of proton therapy using spot scanning: initial experiences.

Lomax AJ, Böhringer T, Bolsi A, Coray D, Emert F, Goitein G, Jermann M, Lin S, Pedroni E, Rutz H, Stadelmann O, Timmermann B, Verwey J, Weber DC
Med Phys 2004 Nov;31(11):3150-7. doi: 10.1118/1.1779371. PMID: 15587667

Sarcomas of the head and neck.

Potter BO, Sturgis EM
Surg Oncol Clin N Am 2003 Apr;12(2):379-417. doi: 10.1016/s1055-3207(03)00005-x. PMID: 12916461

Present results of neutron therapy. The German experience.

Schwarz R, Krüll A, Heyer D, Baumann M, Schmidt R, Hübener KH
Acta Oncol 1994;33(3):281-7. doi: 10.3109/02841869409098418. PMID: 8018356

Status report of fast neutron therapy in the Department of Radiotherapy at the University Hospital Hamburg-Eppendorf.

Schwarz R, Krüll A, Schmidt R, Hübener KH
Strahlenther Onkol 1990 Jan;166(1):72-5. PMID: 2154051

See all (6)

Prognosis

Particle beam radiation therapy for sinonasal malignancies: Single institutional experience at the Shanghai Proton and Heavy Ion Center.

Hu W, Hu J, Huang Q, Gao J, Yang J, Qiu X, Kong L, Lu JJ
Cancer Med 2020 Nov;9(21):7914-7924. Epub 2020 Sep 25 doi: 10.1002/cam4.3393. PMID: 32977357 Free PMC Article

Expression of PAX3 Distinguishes Biphenotypic Sinonasal Sarcoma From Histologic Mimics.

Jo VY, Mariño-Enríquez A, Fletcher CDM, Hornick JL
Am J Surg Pathol 2018 Oct;42(10):1275-1285. doi: 10.1097/PAS.0000000000001092. PMID: 29863547

Hematolymphoid lesions of the sinonasal tract.

Crane GM, Duffield AS
Semin Diagn Pathol 2016 Mar;33(2):71-80. Epub 2015 Sep 9 doi: 10.1053/j.semdp.2015.09.008. PMID: 26472692 Free PMC Article

A Rare Pathology: Low-Grade Fibromyxoid Sarcoma of the Maxilla.

Spalthoff S, Bredt M, Gellrich NC, Jehn P
J Oral Maxillofac Surg 2016 Jan;74(1):219.e1-10. Epub 2015 Sep 25 doi: 10.1016/j.joms.2015.09.018. PMID: 26455471

Sarcomas of the head and neck.

Potter BO, Sturgis EM
Surg Oncol Clin N Am 2003 Apr;12(2):379-417. doi: 10.1016/s1055-3207(03)00005-x. PMID: 12916461

See all (17)

Clinical prediction guides

Biphenotypic Sinonasal Sarcoma: A Case Report and Review of Literature.

Kominsky E, Boyke AE, Madani D, Kamat A, Schiff BA, Agarwal V
Ear Nose Throat J 2023 Jun;102(6):385-390. Epub 2021 Apr 5 doi: 10.1177/0145561321999196. PMID: 33813901

Biphenotypic sinonasal sarcoma: European multicentre case-series and systematic literature review.

Clinicopathological analysis of low-grade papillary Schneiderian carcinoma: report of five new cases and review of the literature.

Zhai C, Wang H, Li S, Wang D
Histopathology 2021 Sep;79(3):370-380. Epub 2021 Apr 14 doi: 10.1111/his.14347. PMID: 33539575

Sinonasal synovial sarcoma: evaluation of the role of radiological and clinicopathological features in diagnosis.

Lin N, Liu X, Zhang F, Pan Y, Qi M, Sha Y
Clin Radiol 2021 Jan;76(1):78.e1-78.e8. Epub 2020 Sep 28 doi: 10.1016/j.crad.2020.08.007. PMID: 32896427

Sarcomas of the head and neck.

Potter BO, Sturgis EM
Surg Oncol Clin N Am 2003 Apr;12(2):379-417. doi: 10.1016/s1055-3207(03)00005-x. PMID: 12916461

See all (13)

Recent systematic reviews

Risk Factors for Recurrence and the Role of Radiotherapy in Low-grade Myofibroblastic Sarcoma: A Systematic Review.

Mamikunian G, Ziegler A, Block A, Thorpe E
Am J Clin Oncol 2023 Sep 1;46(9):420-425. Epub 2023 Jun 26 doi: 10.1097/COC.0000000000001025. PMID: 37358303

Biphenotypic sinonasal sarcoma: European multicentre case-series and systematic literature review.

See all (2)

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Low Grade Paranasal Sinus Sarcoma

Definition

Term Hierarchy

Professional guidelines

PubMed

Recent clinical studies

Etiology

Diagnosis

Therapy

Prognosis

Clinical prediction guides

Recent systematic reviews

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Practice guidelines

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