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Trigeminal autonomic cephalalgia

MedGen UID:
327950
Concept ID:
C1565172
Disease or Syndrome
Synonyms: Cephalalgia, Trigeminal Autonomic; Cephalalgias, Trigeminal Autonomic; Trigeminal Autonomic Cephalalgia; Trigeminal Autonomic Cephalalgias
SNOMED CT: Trigeminal autonomic cephalalgia (449814007); Trigeminal autonomic cephalgia (449814007)
 
Monarch Initiative: MONDO:0015530
Orphanet: ORPHA157843

Definition

A headache disorder characterized by episodes of unilateral, short lasting pain and associated ipsilateral cranial autonomic symptoms. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVTrigeminal autonomic cephalalgia
Follow this link to review classifications for Trigeminal autonomic cephalalgia in Orphanet.

Professional guidelines

PubMed

May A, Evers S, Goadsby PJ, Leone M, Manzoni GC, Pascual J, Carvalho V, Romoli M, Aleksovska K, Pozo-Rosich P, Jensen RH; European Academy of Neurology Task Force
Eur J Neurol 2023 Oct;30(10):2955-2979. Epub 2023 Jul 28 doi: 10.1111/ene.15956. PMID: 37515405
Hoffmann J, May A
Lancet Neurol 2018 Jan;17(1):75-83. Epub 2017 Nov 23 doi: 10.1016/S1474-4422(17)30405-2. PMID: 29174963
Robbins MS, Starling AJ, Pringsheim TM, Becker WJ, Schwedt TJ
Headache 2016 Jul;56(7):1093-106. doi: 10.1111/head.12866. PMID: 27432623

Recent clinical studies

Etiology

Peng KP, Schellong M, May A
Cephalalgia 2022 Jan;42(1):31-36. Epub 2021 Aug 18 doi: 10.1177/03331024211030499. PMID: 34407649Free PMC Article
Burish MJ, Rozen TD
Neurol Clin 2019 Nov;37(4):847-869. Epub 2019 Aug 24 doi: 10.1016/j.ncl.2019.07.001. PMID: 31563236
May A
Dtsch Arztebl Int 2018 Apr 27;115(17):299-308. doi: 10.3238/arztebl.2018.0299. PMID: 29789115Free PMC Article
Wei DY, Jensen RH
Neurotherapeutics 2018 Apr;15(2):346-360. doi: 10.1007/s13311-018-0618-3. PMID: 29516437Free PMC Article
Masters-Israilov A, Robbins MS
Curr Pain Headache Rep 2017 Apr;21(4):20. doi: 10.1007/s11916-017-0620-1. PMID: 28281110

Diagnosis

Iser C, Arca K
Curr Neurol Neurosci Rep 2022 Oct;22(10):625-634. Epub 2022 Aug 22 doi: 10.1007/s11910-022-01225-3. PMID: 35994191
Suri H, Ailani J
Curr Neurol Neurosci Rep 2021 May 5;21(7):31. doi: 10.1007/s11910-021-01114-1. PMID: 33948734
Burish MJ, Rozen TD
Neurol Clin 2019 Nov;37(4):847-869. Epub 2019 Aug 24 doi: 10.1016/j.ncl.2019.07.001. PMID: 31563236
May A
Dtsch Arztebl Int 2018 Apr 27;115(17):299-308. doi: 10.3238/arztebl.2018.0299. PMID: 29789115Free PMC Article
Hoffmann J, May A
Lancet Neurol 2018 Jan;17(1):75-83. Epub 2017 Nov 23 doi: 10.1016/S1474-4422(17)30405-2. PMID: 29174963

Therapy

May A, Evers S, Goadsby PJ, Leone M, Manzoni GC, Pascual J, Carvalho V, Romoli M, Aleksovska K, Pozo-Rosich P, Jensen RH; European Academy of Neurology Task Force
Eur J Neurol 2023 Oct;30(10):2955-2979. Epub 2023 Jul 28 doi: 10.1111/ene.15956. PMID: 37515405
Burish MJ, Rozen TD
Neurol Clin 2019 Nov;37(4):847-869. Epub 2019 Aug 24 doi: 10.1016/j.ncl.2019.07.001. PMID: 31563236
May A
Dtsch Arztebl Int 2018 Apr 27;115(17):299-308. doi: 10.3238/arztebl.2018.0299. PMID: 29789115Free PMC Article
Hoffmann J, May A
Lancet Neurol 2018 Jan;17(1):75-83. Epub 2017 Nov 23 doi: 10.1016/S1474-4422(17)30405-2. PMID: 29174963
Robbins MS, Starling AJ, Pringsheim TM, Becker WJ, Schwedt TJ
Headache 2016 Jul;56(7):1093-106. doi: 10.1111/head.12866. PMID: 27432623

Prognosis

Lambru G, Rantell K, O'Connor E, Levy A, Davagnanam I, Zrinzo L, Matharu M
Brain 2020 Dec 1;143(12):3619-3628. doi: 10.1093/brain/awaa331. PMID: 33301567Free PMC Article
Naegel S, Holle D, Obermann M
Curr Pain Headache Rep 2014 May;18(5):415. doi: 10.1007/s11916-014-0415-6. PMID: 24671392
Pareja JA, Álvarez M
Headache 2013 Oct;53(9):1401-14. doi: 10.1111/head.12193. PMID: 24090529
Robbins MS, Lipton RB
Semin Neurol 2010 Apr;30(2):107-19. Epub 2010 Mar 29 doi: 10.1055/s-0030-1249220. PMID: 20352581
Constantoyannis C, Kagadis G, Chroni E
Headache 2008 Jan;48(1):130-4. Epub 2007 Nov 13 doi: 10.1111/j.1526-4610.2007.00961.x. PMID: 18005140

Clinical prediction guides

Henningsen MJ, Larsen JG, Karlsson WK, Christensen RH, Al-Khazali HM, Amin FM, Ashina H
Headache 2024 Jan;64(1):5-15. Epub 2024 Jan 11 doi: 10.1111/head.14658. PMID: 38205903
Al-Khazali HM, Al-Khazali S, Iljazi A, Christensen RH, Ashina S, Lipton RB, Amin FM, Ashina H
Cephalalgia 2023 Jan;43(1):3331024221131343. doi: 10.1177/03331024221131343. PMID: 36588185
Medrea I, Christie S, Tepper SJ, Thavorn K, Hutton B
Headache 2022 Mar;62(3):329-362. doi: 10.1111/head.14284. PMID: 35315067
Franzini A, Clerici E, Navarria P, Picozzi P
Neurosurg Rev 2022 Jun;45(3):1923-1931. Epub 2022 Feb 3 doi: 10.1007/s10143-021-01725-9. PMID: 35112222
Lambru G, Rantell K, O'Connor E, Levy A, Davagnanam I, Zrinzo L, Matharu M
Brain 2020 Dec 1;143(12):3619-3628. doi: 10.1093/brain/awaa331. PMID: 33301567Free PMC Article

Recent systematic reviews

Murray M, Pahapill PA, Awad AJ
Stereotact Funct Neurosurg 2023;101(4):232-243. Epub 2023 May 26 doi: 10.1159/000530508. PMID: 37245509
Franzini A, Clerici E, Navarria P, Picozzi P
Neurosurg Rev 2022 Jun;45(3):1923-1931. Epub 2022 Feb 3 doi: 10.1007/s10143-021-01725-9. PMID: 35112222
Ghosh A, Silva E, Burish MJ
Cephalalgia 2021 Nov;41(13):1382-1395. Epub 2021 Aug 18 doi: 10.1177/03331024211027560. PMID: 34407646
Robbins MS, Starling AJ, Pringsheim TM, Becker WJ, Schwedt TJ
Headache 2016 Jul;56(7):1093-106. doi: 10.1111/head.12866. PMID: 27432623
Oomen KP, van Wijck AJ, Hordijk GJ, de Ru JA
Cephalalgia 2010 Mar;30(3):360-4. doi: 10.1111/j.1468-2982.2009.01919.x. PMID: 19614698

Supplemental Content

Table of contents

    Clinical resources

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