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Anaplastic Astroblastoma, MN1-Altered

MedGen UID:
417678
Concept ID:
C2827403
Neoplastic Process
Synonym: Anaplastic Astroblastoma

Definition

An astroblastoma, MN1-altered, characterized by the presence of high mitotic activity, cytologic atypia, and architectural distortion. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVAnaplastic Astroblastoma, MN1-Altered

Professional guidelines

PubMed

Geurts M, Snijders TJ, van den Bent MJ
Curr Opin Oncol 2021 Nov 1;33(6):621-625. doi: 10.1097/CCO.0000000000000785. PMID: 34456249
Pacenta HL, Macy ME
Drug Des Devel Ther 2018;12:3549-3561. Epub 2018 Oct 23 doi: 10.2147/DDDT.S147384. PMID: 30425456Free PMC Article
Rudà R, Reifenberger G, Frappaz D, Pfister SM, Laprie A, Santarius T, Roth P, Tonn JC, Soffietti R, Weller M, Moyal EC
Neuro Oncol 2018 Mar 27;20(4):445-456. doi: 10.1093/neuonc/nox166. PMID: 29194500Free PMC Article

Recent clinical studies

Etiology

Ellison DW, Aldape KD, Capper D, Fouladi M, Gilbert MR, Gilbertson RJ, Hawkins C, Merchant TE, Pajtler K, Venneti S, Louis DN
Brain Pathol 2020 Sep;30(5):863-866. Epub 2020 Jun 23 doi: 10.1111/bpa.12866. PMID: 32502305Free PMC Article
Cassia GSE, Alves CAPF, Taranath A, López NS, Oztekin O, Gonçalves FG, Patay Z
Top Magn Reson Imaging 2018 Dec;27(6):479-502. doi: 10.1097/RMR.0000000000000184. PMID: 30516696
Wesseling P, Capper D
Neuropathol Appl Neurobiol 2018 Feb;44(2):139-150. doi: 10.1111/nan.12432. PMID: 28815663
Perry A, Wesseling P
Handb Clin Neurol 2016;134:71-95. doi: 10.1016/B978-0-12-802997-8.00005-0. PMID: 26948349
Omuro A, DeAngelis LM
JAMA 2013 Nov 6;310(17):1842-50. doi: 10.1001/jama.2013.280319. PMID: 24193082

Diagnosis

Schaff LR, Mellinghoff IK
JAMA 2023 Feb 21;329(7):574-587. doi: 10.1001/jama.2023.0023. PMID: 36809318
Rudà R, Reifenberger G, Frappaz D, Pfister SM, Laprie A, Santarius T, Roth P, Tonn JC, Soffietti R, Weller M, Moyal EC
Neuro Oncol 2018 Mar 27;20(4):445-456. doi: 10.1093/neuonc/nox166. PMID: 29194500Free PMC Article
Wesseling P, Capper D
Neuropathol Appl Neurobiol 2018 Feb;44(2):139-150. doi: 10.1111/nan.12432. PMID: 28815663
Omuro A, DeAngelis LM
JAMA 2013 Nov 6;310(17):1842-50. doi: 10.1001/jama.2013.280319. PMID: 24193082
Ohgaki H, Kleihues P
Clin Cancer Res 2013 Feb 15;19(4):764-72. Epub 2012 Dec 3 doi: 10.1158/1078-0432.CCR-12-3002. PMID: 23209033

Therapy

Schaff LR, Mellinghoff IK
JAMA 2023 Feb 21;329(7):574-587. doi: 10.1001/jama.2023.0023. PMID: 36809318
van den Bent MJ, Tesileanu CMS, Wick W, Sanson M, Brandes AA, Clement PM, Erridge S, Vogelbaum MA, Nowak AK, Baurain JF, Mason WP, Wheeler H, Chinot OL, Gill S, Griffin M, Rogers L, Taal W, Rudà R, Weller M, McBain C, Reijneveld J, Enting RH, Caparrotti F, Lesimple T, Clenton S, Gijtenbeek A, Lim E, Herrlinger U, Hau P, Dhermain F, de Heer I, Aldape K, Jenkins RB, Dubbink HJ, Kros JM, Wesseling P, Nuyens S, Golfinopoulos V, Gorlia T, French P, Baumert BG
Lancet Oncol 2021 Jun;22(6):813-823. Epub 2021 May 14 doi: 10.1016/S1470-2045(21)00090-5. PMID: 34000245Free PMC Article
Drappatz J, Lieberman F
Prog Neurol Surg 2018;31:152-161. Epub 2018 Jan 25 doi: 10.1159/000467376. PMID: 29393183
Nayak L, Reardon DA
Continuum (Minneap Minn) 2017 Dec;23(6, Neuro-oncology):1548-1563. doi: 10.1212/CON.0000000000000554. PMID: 29200110
Taal W, Bromberg JE, van den Bent MJ
CNS Oncol 2015;4(3):179-92. Epub 2015 Apr 23 doi: 10.2217/cns.15.2. PMID: 25906059Free PMC Article

Prognosis

Appay R, Dehais C, Maurage CA, Alentorn A, Carpentier C, Colin C, Ducray F, Escande F, Idbaih A, Kamoun A, Marie Y, Mokhtari K, Tabouret E, Trabelsi N, Uro-Coste E, Delattre JY, Figarella-Branger D; POLA Network
Neuro Oncol 2019 Dec 17;21(12):1519-1528. doi: 10.1093/neuonc/noz124. PMID: 31832685Free PMC Article
Karthigeyan M, Gupta K, Salunke P
J Child Neurol 2017 Jan;32(1):53-59. Epub 2016 Sep 29 doi: 10.1177/0883073816668994. PMID: 27664193
Thom M, Blümcke I, Aronica E
Brain Pathol 2012 May;22(3):350-79. doi: 10.1111/j.1750-3639.2012.00582.x. PMID: 22497610Free PMC Article
Van den Bent MJ, Reni M, Gatta G, Vecht C
Crit Rev Oncol Hematol 2008 Jun;66(3):262-72. Epub 2008 Feb 12 doi: 10.1016/j.critrevonc.2007.11.007. PMID: 18272388
Burton EC, Prados MD
Curr Treat Options Oncol 2000 Dec;1(5):459-68. doi: 10.1007/s11864-000-0073-2. PMID: 12057153

Clinical prediction guides

Schaff LR, Mellinghoff IK
JAMA 2023 Feb 21;329(7):574-587. doi: 10.1001/jama.2023.0023. PMID: 36809318
Hsu HI, Hsu SS, Chung WY, Yip CM, Liu SH, Liao WC
World Neurosurg 2022 Feb;158:205-209. Epub 2021 Nov 26 doi: 10.1016/j.wneu.2021.11.074. PMID: 34839047
van den Bent MJ, Smits M, Kros JM, Chang SM
J Clin Oncol 2017 Jul 20;35(21):2394-2401. Epub 2017 Jun 22 doi: 10.1200/JCO.2017.72.6737. PMID: 28640702
Wick W, Wiestler B, Platten M
Cancer Treat Res 2015;163:89-101. doi: 10.1007/978-3-319-12048-5_6. PMID: 25468227
Thom M, Blümcke I, Aronica E
Brain Pathol 2012 May;22(3):350-79. doi: 10.1111/j.1750-3639.2012.00582.x. PMID: 22497610Free PMC Article

Recent systematic reviews

Bin-Alamer O, Jimenez AE, Azad TD, Bettegowda C, Mukherjee D
World Neurosurg 2022 Sep;165:e251-e264. Epub 2022 Jun 10 doi: 10.1016/j.wneu.2022.06.020. PMID: 35697228
Nieder C, Andratschke NH, Grosu AL
Anticancer Res 2016 Oct;36(10):4985-4995. doi: 10.21873/anticanres.11067. PMID: 27798857
Lecavalier-Barsoum M, Quon H, Abdulkarim B
Cochrane Database Syst Rev 2014 May 15;2014(5):CD007104. doi: 10.1002/14651858.CD007104.pub2. PMID: 24833028Free PMC Article
Seo HS, Kim JH, Lee DH, Lee YH, Suh SI, Kim SY, Na DG
AJNR Am J Neuroradiol 2010 Mar;31(3):498-503. Epub 2009 Oct 29 doi: 10.3174/ajnr.A1864. PMID: 19875469Free PMC Article
Quon H, Abdulkarim B
Cochrane Database Syst Rev 2008 Apr 16;(2):CD007104. doi: 10.1002/14651858.CD007104. PMID: 18425979

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