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Bile Duct Mucinous Cystic Neoplasm, High Grade

MedGen UID:
474704
Concept ID:
C3273071
Neoplastic Process
Synonyms: Bile Duct MCN with High Grade Intraepithelial Neoplasia; Bile Duct Mucinous Cystic Neoplasm with High Grade Intraepithelial Neoplasia; Bile Duct Mucinous Cystic Neoplasm, High-Grade

Definition

A non-invasive mucinous cystic neoplasm that arises from the intrahepatic or extrahepatic bile ducts. It is characterized by the presence of severe atypia. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVBile Duct Mucinous Cystic Neoplasm, High Grade

Professional guidelines

PubMed

Jia JJ, Cheng YF, Feng MB, Liu L, Shuai MQ, Shen XD, Tang XF, Zheng SS
Hepatobiliary Pancreat Dis Int 2024 Oct;23(5):495-501. Epub 2023 Aug 12 doi: 10.1016/j.hbpd.2023.08.011. PMID: 37652799

Recent clinical studies

Etiology

Centeno BA, Saieg M, Siddiqui MT, Perez-Machado M, Layfield LJ, Weynand B, Reid MD, Stelow EB, Lozano MD, Fukushima N, Cree IA, Mehrotra R, Schmitt FC, Field AS, Pitman MB
Cancer Cytopathol 2024 Jul;132(7):396-418. Epub 2024 May 6 doi: 10.1002/cncy.22806. PMID: 38709670
Jia JJ, Cheng YF, Feng MB, Liu L, Shuai MQ, Shen XD, Tang XF, Zheng SS
Hepatobiliary Pancreat Dis Int 2024 Oct;23(5):495-501. Epub 2023 Aug 12 doi: 10.1016/j.hbpd.2023.08.011. PMID: 37652799
Albores-Saavedra J, Córdova-Ramón JC, Chablé-Montero F, Dorantes-Heredia R, Henson DE
Ann Diagn Pathol 2015 Jun;19(3):124-9. Epub 2015 Mar 6 doi: 10.1016/j.anndiagpath.2015.03.001. PMID: 25792461
Kubota K, Nakanuma Y, Kondo F, Hachiya H, Miyazaki M, Nagino M, Yamamoto M, Isayama H, Tabata M, Kinoshita H, Kamisawa T, Inui K
J Hepatobiliary Pancreat Sci 2014 Mar;21(3):176-85. Epub 2013 Aug 1 doi: 10.1002/jhbp.23. PMID: 23908126
D'souza MA, Isaksson B, Löhr M, Enochsson L, Swahn F, Lundell L, Arnelo U
Scand J Gastroenterol 2013 Apr;48(4):473-9. Epub 2013 Jan 21 doi: 10.3109/00365521.2012.722672. PMID: 23330596

Diagnosis

Centeno BA, Saieg M, Siddiqui MT, Perez-Machado M, Layfield LJ, Weynand B, Reid MD, Stelow EB, Lozano MD, Fukushima N, Cree IA, Mehrotra R, Schmitt FC, Field AS, Pitman MB
Cancer Cytopathol 2024 Jul;132(7):396-418. Epub 2024 May 6 doi: 10.1002/cncy.22806. PMID: 38709670
Jia JJ, Cheng YF, Feng MB, Liu L, Shuai MQ, Shen XD, Tang XF, Zheng SS
Hepatobiliary Pancreat Dis Int 2024 Oct;23(5):495-501. Epub 2023 Aug 12 doi: 10.1016/j.hbpd.2023.08.011. PMID: 37652799
Kunovsky L, Kala Z, Svaton R, Moravcik P, Mazanec J, Husty J, Prochazka V
Ann Hepatol 2018 May-June;17(3):519-524. Epub 2018 Apr 9 doi: 10.5604/01.3001.0011.7397. PMID: 29735801
Reid MD, Lewis MM, Willingham FF, Adsay NV
Arch Pathol Lab Med 2017 Mar;141(3):366-380. Epub 2017 Jan 5 doi: 10.5858/arpa.2016-0262-SA. PMID: 28055239
Matsumoto Y, Miyamoto H, Fukuya A, Nakamura F, Goji T, Kitamura S, Kimura T, Okamoto K, Sogabe M, Muguruma N, Shimada M, Bando Y, Takayama T
Clin J Gastroenterol 2017 Apr;10(2):185-190. Epub 2017 Jan 4 doi: 10.1007/s12328-016-0711-2. PMID: 28054178

Prognosis

Jia JJ, Cheng YF, Feng MB, Liu L, Shuai MQ, Shen XD, Tang XF, Zheng SS
Hepatobiliary Pancreat Dis Int 2024 Oct;23(5):495-501. Epub 2023 Aug 12 doi: 10.1016/j.hbpd.2023.08.011. PMID: 37652799
Kunovsky L, Kala Z, Svaton R, Moravcik P, Mazanec J, Husty J, Prochazka V
Ann Hepatol 2018 May-June;17(3):519-524. Epub 2018 Apr 9 doi: 10.5604/01.3001.0011.7397. PMID: 29735801
Albores-Saavedra J, Córdova-Ramón JC, Chablé-Montero F, Dorantes-Heredia R, Henson DE
Ann Diagn Pathol 2015 Jun;19(3):124-9. Epub 2015 Mar 6 doi: 10.1016/j.anndiagpath.2015.03.001. PMID: 25792461
Kubota K, Nakanuma Y, Kondo F, Hachiya H, Miyazaki M, Nagino M, Yamamoto M, Isayama H, Tabata M, Kinoshita H, Kamisawa T, Inui K
J Hepatobiliary Pancreat Sci 2014 Mar;21(3):176-85. Epub 2013 Aug 1 doi: 10.1002/jhbp.23. PMID: 23908126
D'souza MA, Isaksson B, Löhr M, Enochsson L, Swahn F, Lundell L, Arnelo U
Scand J Gastroenterol 2013 Apr;48(4):473-9. Epub 2013 Jan 21 doi: 10.3109/00365521.2012.722672. PMID: 23330596

Clinical prediction guides

Zhang TT, Sadler TJ, Whitley S, Brais R, Godfrey E
Br J Radiol 2019 Nov;92(1103):20190461. Epub 2019 Aug 28 doi: 10.1259/bjr.20190461. PMID: 31430199Free PMC Article
Kunovsky L, Kala Z, Svaton R, Moravcik P, Mazanec J, Husty J, Prochazka V
Ann Hepatol 2018 May-June;17(3):519-524. Epub 2018 Apr 9 doi: 10.5604/01.3001.0011.7397. PMID: 29735801
Matsumoto Y, Miyamoto H, Fukuya A, Nakamura F, Goji T, Kitamura S, Kimura T, Okamoto K, Sogabe M, Muguruma N, Shimada M, Bando Y, Takayama T
Clin J Gastroenterol 2017 Apr;10(2):185-190. Epub 2017 Jan 4 doi: 10.1007/s12328-016-0711-2. PMID: 28054178
Kubota K, Nakanuma Y, Kondo F, Hachiya H, Miyazaki M, Nagino M, Yamamoto M, Isayama H, Tabata M, Kinoshita H, Kamisawa T, Inui K
J Hepatobiliary Pancreat Sci 2014 Mar;21(3):176-85. Epub 2013 Aug 1 doi: 10.1002/jhbp.23. PMID: 23908126
Zhong N, Zhang L, Takahashi N, Shalmiyev V, Canto MI, Clain JE, Deutsch JC, DeWitt J, Eloubeidi MA, Gleeson FC, Levy MJ, Mallery S, Raimondo M, Rajan E, Stevens T, Topazian M
Clin Gastroenterol Hepatol 2012 Feb;10(2):192-8, 198.e1-2. Epub 2011 Oct 5 doi: 10.1016/j.cgh.2011.09.029. PMID: 21982970

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