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Abnormality of the pulmonary veins

MedGen UID:
539575
•Concept ID:
C0265914
•
Congenital Abnormality
Synonyms: Abnormality of lung veins; Anomalous pulmonary vein; Congenital Anomaly of Pulmonary Veins; Congenital anomaly of pulmonary veins; Pulmonary vein abnormality; PV - Pulmonary vein abnormality
SNOMED CT: Pulmonary vein abnormality (111322000); PV - Pulmonary vein abnormality (111322000); Congenital anomaly of pulmonary veins (111322000); Anomalous pulmonary vein (128585006)
 
HPO: HP:0011718

Definition

An abnormality of the pulmonary veins. [from HPO]

Professional guidelines

PubMed

Diagnosis and endovascular management of pulmonary arteriovenous malformations.
Kramdhari H, Valakkada J, Ayyappan A
Br J Radiol 2021 Jul 1;94(1123):20200695. Epub 2021 May 26 doi: 10.1259/bjr.20200695. PMID: 34038182Free PMC Article
Pulmonary vein stenosis: Treatment and challenges.
Vanderlaan RD, Rome J, Hirsch R, Ivy D, Caldarone CA
J Thorac Cardiovasc Surg 2021 Jun;161(6):2169-2176. Epub 2020 Jun 27 doi: 10.1016/j.jtcvs.2020.05.117. PMID: 32763037
Congenital portosystemic shunts: diagnosis and treatment.
Franchi-Abella S, Gonzales E, Ackermann O, Branchereau S, Pariente D, Guérin F; International Registry of Congenital Portosystemic Shunt members
Abdom Radiol (NY) 2018 Aug;43(8):2023-2036. doi: 10.1007/s00261-018-1619-8. PMID: 29730740

Recent clinical studies

Etiology

Common pulmonary vein atresia.
Glenn T, Honold J, Printz BF, Mueller D
Cardiol Young 2022 Apr;32(4):668-670. Epub 2021 Sep 6 doi: 10.1017/S1047951121003565. PMID: 34486517
Pulmonary arteriovenous malformations.
Tellapuri S, Park HS, Kalva SP
Int J Cardiovasc Imaging 2019 Aug;35(8):1421-1428. Epub 2018 Nov 1 doi: 10.1007/s10554-018-1479-x. PMID: 30386957
Embolisation for pulmonary arteriovenous malformation.
Hsu CC, Kwan GN, Evans-Barns H, van Driel ML
Cochrane Database Syst Rev 2018 Jan 4;1(1):CD008017. doi: 10.1002/14651858.CD008017.pub5. PMID: 29298459Free PMC Article
Pulmonary vascular diseases.
Cummings KW, Bhalla S
Clin Chest Med 2015 Jun;36(2):235-48, viii. Epub 2015 Mar 26 doi: 10.1016/j.ccm.2015.02.007. PMID: 26024602
Pulmonary arteriovenous malformations.
Cartin-Ceba R, Swanson KL, Krowka MJ
Chest 2013 Sep;144(3):1033-1044. doi: 10.1378/chest.12-0924. PMID: 24008954

Diagnosis

Sinus venosus defect of the pulmonary vein-type: An easily missed diagnosis.
Metcalf MK, Ghosh RM, Harris MA, Savla JJ, Cohen MS
Echocardiography 2022 Mar;39(3):543-547. Epub 2022 Feb 15 doi: 10.1111/echo.15310. PMID: 35170076
Common pulmonary vein atresia.
Glenn T, Honold J, Printz BF, Mueller D
Cardiol Young 2022 Apr;32(4):668-670. Epub 2021 Sep 6 doi: 10.1017/S1047951121003565. PMID: 34486517
Computed Tomography Angiography and Magnetic Resonance Angiography of Congenital Anomalies of Pulmonary Veins.
Abdel Razek AAK, Al-Marsafawy H, Elmansy M, El-Latif MA, Sobh D
J Comput Assist Tomogr 2019 May/Jun;43(3):399-405. doi: 10.1097/RCT.0000000000000857. PMID: 31082945
Pulmonary arteriovenous malformations.
Tellapuri S, Park HS, Kalva SP
Int J Cardiovasc Imaging 2019 Aug;35(8):1421-1428. Epub 2018 Nov 1 doi: 10.1007/s10554-018-1479-x. PMID: 30386957
The diagnosis and interventional management of pulmonary arteriovenous malformations.
Morgan GJ, Qureshi SA
EuroIntervention 2016 May 17;12 Suppl X:X24-X27. doi: 10.4244/EIJV12SXA5. PMID: 27174107

Therapy

Diagnosis and Management of Persistent Pulmonary Arterio-venous Malformations following Embolotherapy.
Kulkarni CB, Sutphin P, Iqbal S, Kalva SP
Acad Radiol 2023 Mar;30(3):441-452. Epub 2022 Sep 9 doi: 10.1016/j.acra.2022.08.012. PMID: 36089478
Circumferential Pulmonary Vein Isolation Plus Low-Voltage Area Modification in Persistent Atrial Fibrillation: The STABLE-SR-II Trial.
Yang G, Zheng L, Jiang C, Fan J, Liu X, Zhan X, Li J, Wang L, Yang H, Zhu W, Du H, Ma G, Ma W, Kojodjojo P, Chen M; STABLE-SR-II Investigators
JACC Clin Electrophysiol 2022 Jul;8(7):882-891. Epub 2022 Apr 27 doi: 10.1016/j.jacep.2022.03.012. PMID: 35863814
Transcatheter Recanalization of Atretic Pulmonary Veins in Infants and Children.
Patel JD, Mandhani M, Gray R, Pettus J, McCracken CE, Thomas A, Bauser-Heaton H, Kim DW, Petit CJ
Circ Cardiovasc Interv 2022 Jun;15(6):e011351. Epub 2022 Jun 21 doi: 10.1161/CIRCINTERVENTIONS.121.011351. PMID: 35727880
Pulmonary arteriovenous malformations.
Tellapuri S, Park HS, Kalva SP
Int J Cardiovasc Imaging 2019 Aug;35(8):1421-1428. Epub 2018 Nov 1 doi: 10.1007/s10554-018-1479-x. PMID: 30386957
Embolisation for pulmonary arteriovenous malformation.
Hsu CC, Kwan GN, Evans-Barns H, van Driel ML
Cochrane Database Syst Rev 2018 Jan 4;1(1):CD008017. doi: 10.1002/14651858.CD008017.pub5. PMID: 29298459Free PMC Article

Prognosis

Prognosis and related risk factors analysis of total anomalous pulmonary venous connection correction.
Wang Z, Ding N, Yi H, Zhu Y, Li Z, Yan D, Li X, Bai S
J Card Surg 2022 Sep;37(9):2524-2535. Epub 2022 Jun 2 doi: 10.1111/jocs.16652. PMID: 35652889
Computed Tomography Angiography and Magnetic Resonance Angiography of Congenital Anomalies of Pulmonary Veins.
Abdel Razek AAK, Al-Marsafawy H, Elmansy M, El-Latif MA, Sobh D
J Comput Assist Tomogr 2019 May/Jun;43(3):399-405. doi: 10.1097/RCT.0000000000000857. PMID: 31082945
Pulmonary arteriovenous malformations.
Cartin-Ceba R, Swanson KL, Krowka MJ
Chest 2013 Sep;144(3):1033-1044. doi: 10.1378/chest.12-0924. PMID: 24008954
Coronary artery fistulae.
Luo L, Kebede S, Wu S, Stouffer GA
Am J Med Sci 2006 Aug;332(2):79-84. doi: 10.1097/00000441-200608000-00005. PMID: 16909054
Congenital hepatic shunts.
Gallego C, Miralles M, Marín C, Muyor P, González G, García-Hidalgo E
Radiographics 2004 May-Jun;24(3):755-72. doi: 10.1148/rg.243035046. PMID: 15143226

Clinical prediction guides

Anatomical attention-based prediction of postoperative pulmonary venous obstruction via CTA images.
Pei Y, Shi G, Li J, Sun D, Wen C, Li J, Huang M, Chen H, Wang L
Comput Med Imaging Graph 2023 Jan;103:102163. Epub 2022 Dec 15 doi: 10.1016/j.compmedimag.2022.102163. PMID: 36566530
Embolisation for pulmonary arteriovenous malformation.
Hsu CC, Kwan GN, Evans-Barns H, van Driel ML
Cochrane Database Syst Rev 2018 Jan 4;1(1):CD008017. doi: 10.1002/14651858.CD008017.pub5. PMID: 29298459Free PMC Article
Prenatal diagnosis of total and partial anomalous pulmonary venous connection: multicenter cohort study and meta-analysis.
Paladini D, Pistorio A, Wu LH, Meccariello G, Lei T, Tuo G, Donarini G, Marasini M, Xie HN
Ultrasound Obstet Gynecol 2018 Jul;52(1):24-34. doi: 10.1002/uog.18907. PMID: 28926132
Clinical implications of pulmonary shunting on saline contrast echocardiography.
Velthuis S, Buscarini E, Gossage JR, Snijder RJ, Mager JJ, Post MC
J Am Soc Echocardiogr 2015 Mar;28(3):255-63. Epub 2015 Jan 23 doi: 10.1016/j.echo.2014.12.008. PMID: 25623000
Normal and abnormal pulmonary arteriovenous shunting: occurrence and mechanisms.
Hoffman JI
Cardiol Young 2013 Oct;23(5):629-41. Epub 2013 Mar 5 doi: 10.1017/S1047951113000140. PMID: 23458130

Recent systematic reviews

Tissue factor in COVID-19-associated coagulopathy.
Subramaniam S, Kothari H, Bosmann M
Thromb Res 2022 Dec;220:35-47. Epub 2022 Oct 1 doi: 10.1016/j.thromres.2022.09.025. PMID: 36265412Free PMC Article
Embolisation for pulmonary arteriovenous malformation.
Hsu CC, Kwan GN, Evans-Barns H, van Driel ML
Cochrane Database Syst Rev 2018 Jan 4;1(1):CD008017. doi: 10.1002/14651858.CD008017.pub5. PMID: 29298459Free PMC Article
Prenatal diagnosis of total and partial anomalous pulmonary venous connection: multicenter cohort study and meta-analysis.
Paladini D, Pistorio A, Wu LH, Meccariello G, Lei T, Tuo G, Donarini G, Marasini M, Xie HN
Ultrasound Obstet Gynecol 2018 Jul;52(1):24-34. doi: 10.1002/uog.18907. PMID: 28926132
Internal mammary artery-to-pulmonary vasculature fistula: Systematic review of case reports.
Abdul Jabbar A, Patel A, Marzlin N, Altabaqchali S, Hasan M, Al-Zubaidi M, Agarwal A
Vasc Med 2017 Oct;22(5):426-431. doi: 10.1177/1358863X17724262. PMID: 28990495
Paediatric haemoptysis and the otorhinolaryngologist: Systematic review.
Bannister M
Int J Pediatr Otorhinolaryngol 2017 Jan;92:99-102. Epub 2016 Oct 24 doi: 10.1016/j.ijporl.2016.10.021. PMID: 28012543

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