U.S. flag

An official website of the United States government

Format

Send to:

Choose Destination

Abnormality of the pulmonary veins

MedGen UID:
539575
Concept ID:
C0265914
Congenital Abnormality
Synonyms: Abnormality of lung veins; Anomalous pulmonary vein; Congenital Anomaly of Pulmonary Veins; Congenital anomaly of pulmonary veins; Pulmonary vein abnormality; PV - Pulmonary vein abnormality
SNOMED CT: Pulmonary vein abnormality (111322000); PV - Pulmonary vein abnormality (111322000); Congenital anomaly of pulmonary veins (111322000); Anomalous pulmonary vein (128585006)
 
HPO: HP:0011718

Definition

An abnormality of the pulmonary veins. [from HPO]

Professional guidelines

PubMed

Schimmel K, Ali MK, Tan SY, Teng J, Do HM, Steinberg GK, Stevenson DA, Spiekerkoetter E
Int J Mol Sci 2021 Aug 21;22(16) doi: 10.3390/ijms22169037. PMID: 34445743Free PMC Article
Franchi-Abella S, Gonzales E, Ackermann O, Branchereau S, Pariente D, Guérin F; International Registry of Congenital Portosystemic Shunt members
Abdom Radiol (NY) 2018 Aug;43(8):2023-2036. doi: 10.1007/s00261-018-1619-8. PMID: 29730740
Paladini D, Pistorio A, Wu LH, Meccariello G, Lei T, Tuo G, Donarini G, Marasini M, Xie HN
Ultrasound Obstet Gynecol 2018 Jul;52(1):24-34. doi: 10.1002/uog.18907. PMID: 28926132

Recent clinical studies

Etiology

Glenn T, Honold J, Printz BF, Mueller D
Cardiol Young 2022 Apr;32(4):668-670. Epub 2021 Sep 6 doi: 10.1017/S1047951121003565. PMID: 34486517
Tellapuri S, Park HS, Kalva SP
Int J Cardiovasc Imaging 2019 Aug;35(8):1421-1428. Epub 2018 Nov 1 doi: 10.1007/s10554-018-1479-x. PMID: 30386957
Cummings KW, Bhalla S
Clin Chest Med 2015 Jun;36(2):235-48, viii. Epub 2015 Mar 26 doi: 10.1016/j.ccm.2015.02.007. PMID: 26024602
Cartin-Ceba R, Swanson KL, Krowka MJ
Chest 2013 Sep;144(3):1033-1044. doi: 10.1378/chest.12-0924. PMID: 24008954
Gallego C, Miralles M, Marín C, Muyor P, González G, García-Hidalgo E
Radiographics 2004 May-Jun;24(3):755-72. doi: 10.1148/rg.243035046. PMID: 15143226

Diagnosis

Metcalf MK, Ghosh RM, Harris MA, Savla JJ, Cohen MS
Echocardiography 2022 Mar;39(3):543-547. Epub 2022 Feb 15 doi: 10.1111/echo.15310. PMID: 35170076
Glenn T, Honold J, Printz BF, Mueller D
Cardiol Young 2022 Apr;32(4):668-670. Epub 2021 Sep 6 doi: 10.1017/S1047951121003565. PMID: 34486517
Contegiacomo A, Del Ciello A, Rella R, Attempati N, Coppolino D, Larici AR, Di Stasi C, Marano G, Manfredi R
Radiol Med 2019 Oct;124(10):973-988. Epub 2019 Jun 17 doi: 10.1007/s11547-019-01051-7. PMID: 31209790
Abdel Razek AAK, Al-Marsafawy H, Elmansy M, El-Latif MA, Sobh D
J Comput Assist Tomogr 2019 May/Jun;43(3):399-405. doi: 10.1097/RCT.0000000000000857. PMID: 31082945
Tellapuri S, Park HS, Kalva SP
Int J Cardiovasc Imaging 2019 Aug;35(8):1421-1428. Epub 2018 Nov 1 doi: 10.1007/s10554-018-1479-x. PMID: 30386957

Therapy

Kulkarni CB, Sutphin P, Iqbal S, Kalva SP
Acad Radiol 2023 Mar;30(3):441-452. Epub 2022 Sep 9 doi: 10.1016/j.acra.2022.08.012. PMID: 36089478
Yang G, Zheng L, Jiang C, Fan J, Liu X, Zhan X, Li J, Wang L, Yang H, Zhu W, Du H, Ma G, Ma W, Kojodjojo P, Chen M; STABLE-SR-II Investigators
JACC Clin Electrophysiol 2022 Jul;8(7):882-891. Epub 2022 Apr 27 doi: 10.1016/j.jacep.2022.03.012. PMID: 35863814
Patel JD, Mandhani M, Gray R, Pettus J, McCracken CE, Thomas A, Bauser-Heaton H, Kim DW, Petit CJ
Circ Cardiovasc Interv 2022 Jun;15(6):e011351. Epub 2022 Jun 21 doi: 10.1161/CIRCINTERVENTIONS.121.011351. PMID: 35727880
Tellapuri S, Park HS, Kalva SP
Int J Cardiovasc Imaging 2019 Aug;35(8):1421-1428. Epub 2018 Nov 1 doi: 10.1007/s10554-018-1479-x. PMID: 30386957
Paladini D, Pistorio A, Wu LH, Meccariello G, Lei T, Tuo G, Donarini G, Marasini M, Xie HN
Ultrasound Obstet Gynecol 2018 Jul;52(1):24-34. doi: 10.1002/uog.18907. PMID: 28926132

Prognosis

Wang Z, Ding N, Yi H, Zhu Y, Li Z, Yan D, Li X, Bai S
J Card Surg 2022 Sep;37(9):2524-2535. Epub 2022 Jun 2 doi: 10.1111/jocs.16652. PMID: 35652889
Abdel Razek AAK, Al-Marsafawy H, Elmansy M, El-Latif MA, Sobh D
J Comput Assist Tomogr 2019 May/Jun;43(3):399-405. doi: 10.1097/RCT.0000000000000857. PMID: 31082945
Cartin-Ceba R, Swanson KL, Krowka MJ
Chest 2013 Sep;144(3):1033-1044. doi: 10.1378/chest.12-0924. PMID: 24008954
Luo L, Kebede S, Wu S, Stouffer GA
Am J Med Sci 2006 Aug;332(2):79-84. doi: 10.1097/00000441-200608000-00005. PMID: 16909054
Gallego C, Miralles M, Marín C, Muyor P, González G, García-Hidalgo E
Radiographics 2004 May-Jun;24(3):755-72. doi: 10.1148/rg.243035046. PMID: 15143226

Clinical prediction guides

Topiwala KK, Patel SD, Saver JL, Streib CD, Shovlin CL
Neurology 2022 Feb 1;98(5):188-198. Epub 2021 Dec 8 doi: 10.1212/WNL.0000000000013169. PMID: 34880092Free PMC Article
Matsuoka H, Matsubara H, Onuki Y, Uchida T, Nakajima H
Gen Thorac Cardiovasc Surg 2021 Sep;69(9):1313-1319. Epub 2021 Apr 26 doi: 10.1007/s11748-021-01639-9. PMID: 33900520
Hsu CC, Kwan GN, Evans-Barns H, van Driel ML
Cochrane Database Syst Rev 2018 Jan 4;1(1):CD008017. doi: 10.1002/14651858.CD008017.pub5. PMID: 29298459Free PMC Article
Paladini D, Pistorio A, Wu LH, Meccariello G, Lei T, Tuo G, Donarini G, Marasini M, Xie HN
Ultrasound Obstet Gynecol 2018 Jul;52(1):24-34. doi: 10.1002/uog.18907. PMID: 28926132
Velthuis S, Buscarini E, Gossage JR, Snijder RJ, Mager JJ, Post MC
J Am Soc Echocardiogr 2015 Mar;28(3):255-63. Epub 2015 Jan 23 doi: 10.1016/j.echo.2014.12.008. PMID: 25623000

Recent systematic reviews

Subramaniam S, Kothari H, Bosmann M
Thromb Res 2022 Dec;220:35-47. Epub 2022 Oct 1 doi: 10.1016/j.thromres.2022.09.025. PMID: 36265412Free PMC Article
Hsu CC, Kwan GN, Evans-Barns H, van Driel ML
Cochrane Database Syst Rev 2018 Jan 4;1(1):CD008017. doi: 10.1002/14651858.CD008017.pub5. PMID: 29298459Free PMC Article
Paladini D, Pistorio A, Wu LH, Meccariello G, Lei T, Tuo G, Donarini G, Marasini M, Xie HN
Ultrasound Obstet Gynecol 2018 Jul;52(1):24-34. doi: 10.1002/uog.18907. PMID: 28926132
Abdul Jabbar A, Patel A, Marzlin N, Altabaqchali S, Hasan M, Al-Zubaidi M, Agarwal A
Vasc Med 2017 Oct;22(5):426-431. doi: 10.1177/1358863X17724262. PMID: 28990495
Bannister M
Int J Pediatr Otorhinolaryngol 2017 Jan;92:99-102. Epub 2016 Oct 24 doi: 10.1016/j.ijporl.2016.10.021. PMID: 28012543

Supplemental Content

Table of contents

    Clinical resources

    Practice guidelines

    • PubMed
      See practice and clinical guidelines in PubMed. The search results may include broader topics and may not capture all published guidelines. See the FAQ for details.
    • Bookshelf
      See practice and clinical guidelines in NCBI Bookshelf. The search results may include broader topics and may not capture all published guidelines. See the FAQ for details.

    Consumer resources

    Recent activity

    Your browsing activity is empty.

    Activity recording is turned off.

    Turn recording back on

    See more...