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Lymphatic vessel neoplasm

MedGen UID:
64616
•Concept ID:
C0206619
•
Neoplastic Process
Synonyms: Lymphatic Vessel Tumor; Lymphatic Vessel Tumors; Tumor, Lymphatic Vessel; Tumors, Lymphatic Vessel
SNOMED CT: Lymphatic vessel tumor (115236002)
 
HPO: HP:0012797
Monarch Initiative: MONDO:0036870

Definition

A benign or malignant neoplasm arising from the lymphatic vessels. [from HPO]

Professional guidelines

PubMed

Lymphangioleiomyomatosis: pathogenesis, clinical features, diagnosis, and management.
McCarthy C, Gupta N, Johnson SR, Yu JJ, McCormack FX
Lancet Respir Med 2021 Nov;9(11):1313-1327. Epub 2021 Aug 27 doi: 10.1016/S2213-2600(21)00228-9. PMID: 34461049
Overview of primary adult retroperitoneal tumours.
Improta L, Tzanis D, Bouhadiba T, Abdelhafidh K, Bonvalot S
Eur J Surg Oncol 2020 Sep;46(9):1573-1579. Epub 2020 May 21 doi: 10.1016/j.ejso.2020.04.054. PMID: 32600897
Treatment of lymphangioleiomyomatosis and Camões.
Rufino R
J Bras Pneumol 2015 Jul-Aug;41(4):295-6. doi: 10.1590/S1806-37132015000400001. PMID: 26398747Free PMC Article

Recent clinical studies

Etiology

Large retroperitoneal lymphangioma.
Chiang J, Woo JE, Vu AH, Sirsi S
BMJ Case Rep 2024 May 8;17(5) doi: 10.1136/bcr-2023-258099. PMID: 38719266Free PMC Article
Lymphangioleiomyomatosis.
Elia D, Cassandro R, Caminati A, Luisi F, Harari S
Presse Med 2023 Sep;52(3):104173. Epub 2023 Sep 9 doi: 10.1016/j.lpm.2023.104173. PMID: 37696446
Cystic lung disease.
Cabeza Martínez B, Giménez Palleiro A, Mazzini Florindez SP
Radiologia (Engl Ed) 2022 Dec;64 Suppl 3:265-276. doi: 10.1016/j.rxeng.2022.09.005. PMID: 36737165
Ventilator-Induced Hiccups.
Kyogoku M, Inata Y, Takeuchi M
J Pediatr 2017 Oct;189:238. Epub 2017 Jul 20 doi: 10.1016/j.jpeds.2017.06.065. PMID: 28735978
Childhood cervical lymphadenopathy.
Leung AK, Robson WL
J Pediatr Health Care 2004 Jan-Feb;18(1):3-7. doi: 10.1016/j.pedhc.2003.08.008. PMID: 14722499Free PMC Article

Diagnosis

Large retroperitoneal lymphangioma.
Chiang J, Woo JE, Vu AH, Sirsi S
BMJ Case Rep 2024 May 8;17(5) doi: 10.1136/bcr-2023-258099. PMID: 38719266Free PMC Article
Stewart-Treves Syndrome.
Bernia E, Rios-Viñuela E, Requena C
JAMA Dermatol 2021 Jun 1;157(6):721. doi: 10.1001/jamadermatol.2021.0341. PMID: 33909015
Splenic lymphangioma.
Ioannidis I, Kahn AG
Arch Pathol Lab Med 2015 Feb;139(2):278-82. doi: 10.5858/arpa.2013-0656-RS. PMID: 25611113
Lymphangioleiomyomatosis.
Ansótegui Barrera E, Mancheño Franch N, Vera-Sempere F, Padilla Alarcón J
Arch Bronconeumol 2011 Feb;47(2):85-93. Epub 2011 Jan 20 doi: 10.1016/j.arbres.2010.08.008. PMID: 21255897
Gastric lymphangioma.
Kim HS, Lee SY, Lee YD, Kim DH, Kwon JG, Tak WY, Kweon YO, Kim SK, Choi YH, Chung JM
J Korean Med Sci 2001 Apr;16(2):229-32. doi: 10.3346/jkms.2001.16.2.229. PMID: 11306753Free PMC Article

Therapy

Lymphangioleiomyomatosis (LAM).
Ataya A, Brantly M, Riley L
Am J Respir Crit Care Med 2018 Aug 15;198(4):P7-P8. doi: 10.1164/rccm.1984P7. PMID: 30109949
Pulmonary manifestations in tuberous sclerosis complex.
Gupta N, Henske EP
Am J Med Genet C Semin Med Genet 2018 Sep;178(3):326-337. Epub 2018 Jul 28 doi: 10.1002/ajmg.c.31638. PMID: 30055039Free PMC Article
Lymphangioleiomyomatosis.
Sclafani A, VanderLaan P
N Engl J Med 2018 Jun 7;378(23):2224. doi: 10.1056/NEJMicm1712581. PMID: 29874537
Update on orbital lymphatic malformations.
Lally SE
Curr Opin Ophthalmol 2016 Sep;27(5):413-5. doi: 10.1097/ICU.0000000000000291. PMID: 27219273
Optimizing treatments for lymphangioleiomyomatosis.
Taveira-DaSilva AM, Moss J
Expert Rev Respir Med 2012 Jun;6(3):267-76. doi: 10.1586/ers.12.26. PMID: 22788941Free PMC Article

Prognosis

Intra-abdominal Cystic Lymphangiomas: The Vanderbilt Experience.
Mede A, Chotai PN, Huh WJ, Tan M
J Surg Res 2023 May;285:197-204. Epub 2023 Jan 23 doi: 10.1016/j.jss.2022.12.026. PMID: 36696706
Ventilator-Induced Hiccups.
Kyogoku M, Inata Y, Takeuchi M
J Pediatr 2017 Oct;189:238. Epub 2017 Jul 20 doi: 10.1016/j.jpeds.2017.06.065. PMID: 28735978
Splenic lymphangioma.
Ioannidis I, Kahn AG
Arch Pathol Lab Med 2015 Feb;139(2):278-82. doi: 10.5858/arpa.2013-0656-RS. PMID: 25611113
Pancreatic hemolymphangioma.
Figueroa RM, Lopez GJ, Servin TE, Esquinca MH, Gómez-Pedraza A
JOP 2014 Jul 28;15(4):399-402. doi: 10.6092/1590-8577/2649. PMID: 25076353
Lymphangioleiomyomatosis.
Kitaichi M, Izumi T
Curr Opin Pulm Med 1995 Sep;1(5):417-24. PMID: 9363104

Clinical prediction guides

Lymphangioleiomyomatosis: pathogenesis, clinical features, diagnosis, and management.
McCarthy C, Gupta N, Johnson SR, Yu JJ, McCormack FX
Lancet Respir Med 2021 Nov;9(11):1313-1327. Epub 2021 Aug 27 doi: 10.1016/S2213-2600(21)00228-9. PMID: 34461049
A review of the management of lymphangiomas.
Ha J, Yu YC, Lannigan F
Curr Pediatr Rev 2014;10(3):238-48. doi: 10.2174/1573396309666131209210751. PMID: 25088344
Diffuse cystic lung diseases.
Ryu JH, Tian X, Baqir M, Xu K
Front Med 2013 Sep;7(3):316-27. Epub 2013 May 11 doi: 10.1007/s11684-013-0269-z. PMID: 23666611
Lymphangioleiomyomatosis: what do we know and what are we looking for?
Harari S, Torre O, Moss J
Eur Respir Rev 2011 Mar;20(119):34-44. doi: 10.1183/09059180.00011010. PMID: 21357890Free PMC Article
Pulmonary lymphangioleiomyomatosis.
Viskum K
Monaldi Arch Chest Dis 1993;48(3):233-6. PMID: 8369788

Recent systematic reviews

Traumatic subdural hygroma and chronic subdural hematoma: A systematic review and meta-analysis.
Yu J, Tang J, Chen M, Ren Q, He J, Tang M, Zhang X, Liu Z, Ding H
J Clin Neurosci 2023 Jan;107:23-33. Epub 2022 Nov 30 doi: 10.1016/j.jocn.2022.11.010. PMID: 36462413
Clinical features and outcomes of male patients with lymphangioleiomyomatosis: A review.
Zhang H, Hu Z, Wang S, Wu K, Yang Q, Song X
Medicine (Baltimore) 2022 Dec 30;101(52):e32492. doi: 10.1097/MD.0000000000032492. PMID: 36596036Free PMC Article
A Systematic Review of Lymphangioleiomyomatosis on Diagnosis and Molecular Mechanism.
Dong X, Jin L, Wang A, Wu L, Fan X, Hou Q, Li T, Zhao R, Zhang Y
Biomed Res Int 2021;2021:6612776. Epub 2021 Feb 10 doi: 10.1155/2021/6612776. PMID: 33628792Free PMC Article
Sentinel lymphatic mapping among women with early-stage cervical cancer: A systematic review.
Cheng-Yen Lai J, Lai KJ, Yi-Yung Yu E, Hung ST, Chu CY, Wang KL
Taiwan J Obstet Gynecol 2018 Oct;57(5):636-643. doi: 10.1016/j.tjog.2018.08.004. PMID: 30342642
Nonsurgical therapies for lymphangiomas: a systematic review.
Acevedo JL, Shah RK, Brietzke SE
Otolaryngol Head Neck Surg 2008 Apr;138(4):418-24. doi: 10.1016/j.otohns.2007.11.018. PMID: 18359347

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