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Uterine ligament papillary cystadenoma associated with von Hippel-Lindau disease

MedGen UID:
770964
•Concept ID:
C3642324
•
Neoplastic Process
Synonyms: uterine ligament papillary cystadenoma; Uterine Ligament Papillary Cystadenoma Associated with von Hippel-Lindau Disease; uterine ligament papillary cystadenoma associated with von Hippel-Lindau disease
 
Monarch Initiative: MONDO:0003611

Definition

A benign mesonephric neoplasm that arises from the broad or other uterine ligaments and occurs in women with von Hippel-Lindau disease. It is a cystic lesion characterized by the presence of multiple papillary excrescences. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVUterine ligament papillary cystadenoma associated with von Hippel-Lindau disease

Recent clinical studies

Etiology

Uncommon hereditary gynaecological tumour syndromes: pathological features in tumours that may predict risk for a germline mutation.
Garg K, Karnezis AN, Rabban JT
Pathology 2018 Feb;50(2):238-256. Epub 2018 Jan 17 doi: 10.1016/j.pathol.2017.10.009. PMID: 29373116

Diagnosis

Uncommon hereditary gynaecological tumour syndromes: pathological features in tumours that may predict risk for a germline mutation.
Garg K, Karnezis AN, Rabban JT
Pathology 2018 Feb;50(2):238-256. Epub 2018 Jan 17 doi: 10.1016/j.pathol.2017.10.009. PMID: 29373116

Prognosis

Uncommon hereditary gynaecological tumour syndromes: pathological features in tumours that may predict risk for a germline mutation.
Garg K, Karnezis AN, Rabban JT
Pathology 2018 Feb;50(2):238-256. Epub 2018 Jan 17 doi: 10.1016/j.pathol.2017.10.009. PMID: 29373116

Clinical prediction guides

Uncommon hereditary gynaecological tumour syndromes: pathological features in tumours that may predict risk for a germline mutation.
Garg K, Karnezis AN, Rabban JT
Pathology 2018 Feb;50(2):238-256. Epub 2018 Jan 17 doi: 10.1016/j.pathol.2017.10.009. PMID: 29373116

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