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Pulmonary granulomatosis

MedGen UID:
830594
Concept ID:
C0856628
Disease or Syndrome
HPO: HP:0030250

Definition

The presence of multiple granulomata (small nodular inflammatory lesions containing grouped mononuclear phagocytes) in the lung. [from HPO]

Professional guidelines

PubMed

Silva-Carmona M, Sayad E, Vogel TP
J Clin Rheumatol 2021 Sep 1;27(6):e243-e244. doi: 10.1097/RHU.0000000000001378. PMID: 32251052
Rossman MD
Environ Health Perspect 1996 Oct;104 Suppl 5(Suppl 5):945-7. doi: 10.1289/ehp.96104s5945. PMID: 8933039Free PMC Article
Siltzbach LE
Adv Cardiopulm Dis 1969;4:306-19. PMID: 5762797

Recent clinical studies

Etiology

Bode SFN, Rohr J, Müller Quernheim J, Seidl M, Speckmann C, Heinzmann A
Eur Respir Rev 2021 Jun 30;30(160) Epub 2021 Apr 29 doi: 10.1183/16000617.0152-2020. PMID: 33927005Free PMC Article
Vaszar LT, Orzechowski NM, Specks U, Ytterberg SR, Loftus EV Jr, Mark EJ, Tazelaar HD
Am J Surg Pathol 2014 Mar;38(3):354-9. doi: 10.1097/PAS.0000000000000135. PMID: 24525506
Pelegrín I, Ayats J, Xiol X, Cuenca-Estrella M, Jucglà A, Boluda S, Fernàndez-Sabé N, Rafecas A, Gudiol F, Cabellos C
Transpl Infect Dis 2011 Oct;13(5):507-14. Epub 2011 Feb 15 doi: 10.1111/j.1399-3062.2011.00611.x. PMID: 21323828
Lee JY, Atochina O, King B, Taylor L, Elloso M, Scott P, Rossman MD
Infect Immun 2000 Jul;68(7):4032-9. doi: 10.1128/IAI.68.7.4032-4039.2000. PMID: 10858219Free PMC Article
Rossman MD, Kern JA, Elias JA, Cullen MR, Epstein PE, Preuss OP, Markham TN, Daniele RP
Ann Intern Med 1988 May;108(5):687-93. doi: 10.7326/0003-4819-108-5-687. PMID: 3282464

Diagnosis

Bode SFN, Rohr J, Müller Quernheim J, Seidl M, Speckmann C, Heinzmann A
Eur Respir Rev 2021 Jun 30;30(160) Epub 2021 Apr 29 doi: 10.1183/16000617.0152-2020. PMID: 33927005Free PMC Article
Vaszar LT, Orzechowski NM, Specks U, Ytterberg SR, Loftus EV Jr, Mark EJ, Tazelaar HD
Am J Surg Pathol 2014 Mar;38(3):354-9. doi: 10.1097/PAS.0000000000000135. PMID: 24525506
Tseng W, Sutter ME, Albertson TE
Clin Rev Allergy Immunol 2014 Feb;46(1):82-100. doi: 10.1007/s12016-013-8376-9. PMID: 23760760
de Kerviler E, Trédaniel J, Revlon G, Groussard O, Zalcman G, Ortoli JM, Espié M, Hirsch A, Frija J
Eur Respir J 1996 Mar;9(3):615-7. doi: 10.1183/09031936.96.09030615. PMID: 8730028
Dunnill MS
Histopathology 1991 Oct;19(4):297-301. doi: 10.1111/j.1365-2559.1991.tb00043.x. PMID: 1937409

Therapy

Linkova N, Diatlova A, Zinchenko Y, Kornilova A, Snetkov P, Morozkina S, Medvedev D, Krasichkov A, Polyakova V, Yablonskiy P
Int J Mol Sci 2023 Jul 10;24(14) doi: 10.3390/ijms241411267. PMID: 37511027Free PMC Article
Blin T, De Muret A, Teulier M, Ferreira M, Vincent M, Catinon M, Legras A, Diot P, Marchand-Adam S
Sarcoidosis Vasc Diffuse Lung Dis 2020;37(1):79-84. Epub 2020 Mar 15 doi: 10.36141/svdld.v37i1.9103. PMID: 33093772Free PMC Article
Tseng W, Sutter ME, Albertson TE
Clin Rev Allergy Immunol 2014 Feb;46(1):82-100. doi: 10.1007/s12016-013-8376-9. PMID: 23760760
de Kerviler E, Trédaniel J, Revlon G, Groussard O, Zalcman G, Ortoli JM, Espié M, Hirsch A, Frija J
Eur Respir J 1996 Mar;9(3):615-7. doi: 10.1183/09031936.96.09030615. PMID: 8730028
Reeves AL
Ann Clin Lab Sci 1976 May-Jun;6(3):256-62. PMID: 942183

Prognosis

Lazzaro MC, Romanò S, Santoro S, Camuto C, Carbone A, Casamassima R, Abate S, De-Giorgio F
Virchows Arch 2021 Feb;478(2):361-366. Epub 2020 Jun 9 doi: 10.1007/s00428-020-02863-z. PMID: 32519036
Vaszar LT, Orzechowski NM, Specks U, Ytterberg SR, Loftus EV Jr, Mark EJ, Tazelaar HD
Am J Surg Pathol 2014 Mar;38(3):354-9. doi: 10.1097/PAS.0000000000000135. PMID: 24525506
Pelegrín I, Ayats J, Xiol X, Cuenca-Estrella M, Jucglà A, Boluda S, Fernàndez-Sabé N, Rafecas A, Gudiol F, Cabellos C
Transpl Infect Dis 2011 Oct;13(5):507-14. Epub 2011 Feb 15 doi: 10.1111/j.1399-3062.2011.00611.x. PMID: 21323828
Rossman MD
Environ Health Perspect 1996 Oct;104 Suppl 5(Suppl 5):945-7. doi: 10.1289/ehp.96104s5945. PMID: 8933039Free PMC Article
Rolfes DB, Weiss MA, Sanders MA
Am J Clin Pathol 1984 Nov;82(5):602-7. doi: 10.1093/ajcp/82.5.602. PMID: 6093497

Clinical prediction guides

Kim HS, Gil BM, Kang HS, Kim J, Kim CH, Chung MH
Respiration 2024;103(1):41-46. Epub 2024 Jan 5 doi: 10.1159/000535594. PMID: 38185117
Guneyli S, Ceylan N, Bayraktaroglu S, Gucenmez S, Aksu K, Kocacelebi K, Acar T, Savas R, Alper H
Wien Klin Wochenschr 2016 Nov;128(21-22):809-815. Epub 2015 Apr 10 doi: 10.1007/s00508-015-0747-1. PMID: 25860849
Vaszar LT, Orzechowski NM, Specks U, Ytterberg SR, Loftus EV Jr, Mark EJ, Tazelaar HD
Am J Surg Pathol 2014 Mar;38(3):354-9. doi: 10.1097/PAS.0000000000000135. PMID: 24525506
Lie JT
Mod Pathol 1996 May;9(5):469-74. PMID: 8733760
Chen WJ, Monnat RJ Jr, Chen M, Mottet NK
Hum Pathol 1978 Nov;9(6):705-11. doi: 10.1016/s0046-8177(78)80053-7. PMID: 730152

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