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Calcifying epithelial odontogenic tumor

MedGen UID:
87266
Concept ID:
C0334574
Neoplastic Process
Synonym: Pindborg tumor
SNOMED CT: CEOT - Calcifying epithelial odontogenic tumor (83048004); Calcifying epithelial odontogenic tumor (83048004); Pindborg tumor (83048004)
 
Monarch Initiative: MONDO:0022057

Definition

A slow growing, locally invasive neoplasm arising from tooth-forming tissues. It most often grows intraosseously in the mandible and less frequently in the maxilla. In a minority of cases it grows extraosseously in the gingiva. It is characterized by the presence of a fibrous stroma, epithelial cells with abundant eosinophilic cytoplasm, and amyloid material which is often calcified. Small tumors may be successfully treated with enucleation. Local resection is usually required for larger tumors. Recurrences have been reported in a minority of cases. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVCalcifying epithelial odontogenic tumor

Recent clinical studies

Etiology

Magliocca KR
Head Neck Pathol 2023 Jun;17(2):313-324. Epub 2023 Jun 6 doi: 10.1007/s12105-023-01561-x. PMID: 37278887Free PMC Article
Siriwardena BSMS, Speight PM, Franklin CD, Abdelkarim R, Khurram SA, Hunter KD
Head Neck Pathol 2021 Mar;15(1):186-201. Epub 2020 Jul 8 doi: 10.1007/s12105-020-01200-9. PMID: 32642935Free PMC Article
Rosa ACG, Soares AB, Furuse C, Lima SRR, de Araújo VC, Passador-Santos F
Head Neck Pathol 2017 Dec;11(4):519-524. Epub 2016 Nov 5 doi: 10.1007/s12105-016-0767-9. PMID: 27817004Free PMC Article
Guimarães DM, Antunes DM, Saturno JL, Massuda F, Paiva KB, Nunes FD
Acta Histochem 2015 Oct;117(8):667-74. Epub 2015 Nov 7 doi: 10.1016/j.acthis.2015.10.006. PMID: 26558991
Franklin CD, Pindborg JJ
Oral Surg Oral Med Oral Pathol 1976 Dec;42(6):753-65. doi: 10.1016/0030-4220(76)90098-0. PMID: 792760

Diagnosis

Xie N, Chen Z, Liu Y, Huo J, Chen X, Lam AK
Head Neck Pathol 2023 Dec;17(4):1011-1020. Epub 2023 Nov 27 doi: 10.1007/s12105-023-01602-5. PMID: 38010475Free PMC Article
Ruddocks LA, Fitzpatrick SG, Bhattacharyya I, Cohen DM, Islam MN
Oral Surg Oral Med Oral Pathol Oral Radiol 2021 Jun;131(6):684-693. Epub 2021 Jan 9 doi: 10.1016/j.oooo.2021.01.007. PMID: 33737014
de Arruda JAA, Abreu LG, Silva LVO, Schuch LF, Monteiro JLGC, Arantes DAC, da Costa AAS, Nóbrega KHS, Vasconcelos ACU, de Andrade BAB, Romañach MJ, Sobral APV, Rivero ERC, da Silva TA, Batista AC, Mesquita RA
Oral Dis 2019 Jan;25(1):192-205. Epub 2018 Sep 9 doi: 10.1111/odi.12958. PMID: 30113739
Chrcanovic BR, Gomez RS
J Craniomaxillofac Surg 2017 Aug;45(8):1117-1123. Epub 2017 May 12 doi: 10.1016/j.jcms.2017.05.007. PMID: 28601296
Bilodeau EA, Collins BM
Surg Pathol Clin 2017 Mar;10(1):177-222. Epub 2016 Dec 29 doi: 10.1016/j.path.2016.10.006. PMID: 28153133

Therapy

Nakano H, Ota Y, Yura Y
Br J Oral Maxillofac Surg 2009 Apr;47(3):222-4. Epub 2008 Sep 14 doi: 10.1016/j.bjoms.2008.07.201. PMID: 18790551
Kawano K, Ono K, Yada N, Takahashi Y, Kashima K, Yokoyama S, Yanagisawa S
Oral Surg Oral Med Oral Pathol Oral Radiol Endod 2007 Jul;104(1):76-81. Epub 2006 Sep 25 doi: 10.1016/j.tripleo.2006.04.014. PMID: 17577547
da Silveira EJ, Gordón-Núñez MA, Seabra FR, Bitu Filho RS, Lima EG, de Medeiros AM, Galvão HC
J Oral Maxillofac Surg 2007 Feb;65(2):341-5. doi: 10.1016/j.joms.2006.05.045. PMID: 17236947

Prognosis

Bruett CT, Roark S, Reich RF, Freedman PD
Oral Surg Oral Med Oral Pathol Oral Radiol 2024 Jan;137(1):61-66. Epub 2023 Aug 28 doi: 10.1016/j.oooo.2023.08.013. PMID: 37891119
Piskadło T, Brodowski R, Książek M, Pakla P, Dymek M, Haberko P, Franczak J, Stopyra W, Lewandowski B
Dev Period Med 2019;23(1):34-38. doi: 10.34763/devperiodmed.20192301.3438. PMID: 30954979Free PMC Article
Bilodeau EA, Collins BM
Surg Pathol Clin 2017 Mar;10(1):177-222. Epub 2016 Dec 29 doi: 10.1016/j.path.2016.10.006. PMID: 28153133
Regezi JA
Mod Pathol 2002 Mar;15(3):331-41. doi: 10.1038/modpathol.3880527. PMID: 11904346
Franklin CD, Pindborg JJ
Oral Surg Oral Med Oral Pathol 1976 Dec;42(6):753-65. doi: 10.1016/0030-4220(76)90098-0. PMID: 792760

Clinical prediction guides

Bruett CT, Roark S, Reich RF, Freedman PD
Oral Surg Oral Med Oral Pathol Oral Radiol 2024 Jan;137(1):61-66. Epub 2023 Aug 28 doi: 10.1016/j.oooo.2023.08.013. PMID: 37891119
Baykara Y, Akgun Y, Van Truong L, Corbett M, Hacking SM
R I Med J (2013) 2022 Aug 1;105(6):24-27. PMID: 35881995
Mehngi R, Rajendra K, Bhagwat P, Hegde SS, Sah D, Rathod VS
J Contemp Dent Pract 2018 Oct 1;19(10):1288-1292. PMID: 30498188
Sánchez-Romero C, Carlos R, de Almeida OP, Romañach MJ
Head Neck Pathol 2018 Dec;12(4):598-603. Epub 2017 Nov 21 doi: 10.1007/s12105-017-0868-0. PMID: 29164474Free PMC Article
Oh KY, Yoon HJ, Lee JI, Ahn SH, Hong SD
J Oral Pathol Med 2017 Feb;46(2):127-133. Epub 2016 Jul 19 doi: 10.1111/jop.12479. PMID: 27432522

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