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Retinocytoma

MedGen UID:
91105
Concept ID:
C0346396
Neoplastic Process
Synonyms: Adenoma of retinal pigment epithelium; Retinoma
SNOMED CT: Retinocytoma (128913004); Retinocytoma (416864007); Adenoma of retinal pigment epithelium (255027009); Retinoma (255027009)

Definition

A rare, unilateral or bilateral benign neoplasm that arises from the retina. There is an increased risk of malignant transformation to retinoblastoma; therefore, patients with a diagnosis of retinocytoma should be closely observed. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVRetinocytoma

Recent clinical studies

Etiology

Shields CL, Srinivasan A, Lucio-Alvarez JA, Shields JA
J AAPOS 2021 Jun;25(3):147.e1-147.e8. Epub 2021 May 26 doi: 10.1016/j.jaapos.2020.11.024. PMID: 34051357
Mendoza PR, Specht CS, Hubbard GB, Wells JR, Lynn MJ, Zhang Q, Kong J, Grossniklaus HE
Am J Ophthalmol 2015 Apr;159(4):764-76. Epub 2014 Dec 19 doi: 10.1016/j.ajo.2014.12.014. PMID: 25528954Free PMC Article
Zhang M, Shan BE, Yuan NF, Liu W
Chin Med J (Engl) 2013 Jan;126(2):340-4. PMID: 23324287
Eagle RC Jr
Eye (Lond) 2013 Feb;27(2):128-36. Epub 2012 Nov 16 doi: 10.1038/eye.2012.237. PMID: 23154492Free PMC Article
Singh AD, Santos CM, Shields CL, Shields JA, Eagle RC Jr
Arch Ophthalmol 2000 Feb;118(2):199-205. doi: 10.1001/archopht.118.2.199. PMID: 10676785

Diagnosis

Li X, Ju Y, Huang X
Ophthalmol Retina 2024 Jan;8(1):61. Epub 2023 Nov 10 doi: 10.1016/j.oret.2023.09.024. PMID: 37952138
Shields CL, Srinivasan A, Lucio-Alvarez JA, Shields JA
J AAPOS 2021 Jun;25(3):147.e1-147.e8. Epub 2021 May 26 doi: 10.1016/j.jaapos.2020.11.024. PMID: 34051357
Sengupta S, Pan U, Khetan V
Indian J Ophthalmol 2016 Jul;64(7):485-91. doi: 10.4103/0301-4738.190099. PMID: 27609158Free PMC Article
Singh AD, Santos CM, Shields CL, Shields JA, Eagle RC Jr
Arch Ophthalmol 2000 Feb;118(2):199-205. doi: 10.1001/archopht.118.2.199. PMID: 10676785
Abramson DH
Arch Ophthalmol 1983 Oct;101(10):1517-8. doi: 10.1001/archopht.1983.01040020519002. PMID: 6626000

Therapy

Chung J, Turaka K, Shields CL
J Pediatr Ophthalmol Strabismus 2010 Dec 22;47 Online:e1-3. doi: 10.3928/01913913-20101217-03. PMID: 21175116

Prognosis

Shields CL, Srinivasan A, Lucio-Alvarez JA, Shields JA
J AAPOS 2021 Jun;25(3):147.e1-147.e8. Epub 2021 May 26 doi: 10.1016/j.jaapos.2020.11.024. PMID: 34051357
Mendoza PR, Specht CS, Hubbard GB, Wells JR, Lynn MJ, Zhang Q, Kong J, Grossniklaus HE
Am J Ophthalmol 2015 Apr;159(4):764-76. Epub 2014 Dec 19 doi: 10.1016/j.ajo.2014.12.014. PMID: 25528954Free PMC Article
Liu Y, Zhong X, Wan S, Zhang W, Lin J, Zhang P, Li Y
Diagn Pathol 2014 Dec 11;9:180. doi: 10.1186/s13000-014-0180-1. PMID: 25499675Free PMC Article
Eagle RC Jr
Eye (Lond) 2013 Feb;27(2):128-36. Epub 2012 Nov 16 doi: 10.1038/eye.2012.237. PMID: 23154492Free PMC Article
Hadjistilianou T, De Francesco S, Martone G, Malandrini A
Eur J Ophthalmol 2006 Mar-Apr;16(2):349-51. doi: 10.1177/112067210601600227. PMID: 16703560

Clinical prediction guides

Shields CL, Srinivasan A, Lucio-Alvarez JA, Shields JA
J AAPOS 2021 Jun;25(3):147.e1-147.e8. Epub 2021 May 26 doi: 10.1016/j.jaapos.2020.11.024. PMID: 34051357
Mendoza PR, Specht CS, Hubbard GB, Wells JR, Lynn MJ, Zhang Q, Kong J, Grossniklaus HE
Am J Ophthalmol 2015 Apr;159(4):764-76. Epub 2014 Dec 19 doi: 10.1016/j.ajo.2014.12.014. PMID: 25528954Free PMC Article
Zhang M, Shan BE, Yuan NF, Liu W
Chin Med J (Engl) 2013 Jan;126(2):340-4. PMID: 23324287
Kase S, Parikh JG, Rao NA
Arch Ophthalmol 2009 Feb;127(2):187-92. doi: 10.1001/archophthalmol.2008.580. PMID: 19204237Free PMC Article
Singh AD, Santos CM, Shields CL, Shields JA, Eagle RC Jr
Arch Ophthalmol 2000 Feb;118(2):199-205. doi: 10.1001/archopht.118.2.199. PMID: 10676785

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