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Metastatic Extraskeletal Ewing Sarcoma

MedGen UID:
163504
•Concept ID:
C0855042
•
Neoplastic Process
Synonyms: Extra-Osseous Ewing's Sarcoma, Metastatic; Metastatic Extra-Osseous Ewing's Sarcoma; Metastatic Extraosseous Ewing Sarcoma; Metastatic Extraosseous Ewing's Sarcoma; Metastatic Extraskeletal Ewing's Sarcoma

Definition

An Ewing sarcoma of the soft tissues which has spread from its original site of growth to another anatomic site. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVMetastatic Extraskeletal Ewing Sarcoma

Professional guidelines

PubMed

Treatment outcomes of extraskeletal Ewing sarcoma.
Houdek MT, Heidenreich MJ, Ahmed SK, Allen-Rhoades W, Siontis BL, Robinson SI, Petersen IA, Rose PS
J Surg Oncol 2023 Jul;128(1):105-110. Epub 2023 Mar 31 doi: 10.1002/jso.27250. PMID: 36999583
Advantages in Prognosis of Adult Patients with Ewing Sarcoma: 11-years Experiences and Current Treatment Management.
Krakorova DA, Kubackova K, Dusek L, Tomas T, Janicek P, Tucek S, Prausova J, Kiss I, Zambo I
Pathol Oncol Res 2018 Jul;24(3):623-630. Epub 2017 Aug 12 doi: 10.1007/s12253-017-0291-6. PMID: 28803261
Soft tissue sarcoma in children: prognosis and management.
Koscielniak E, Morgan M, Treuner J
Paediatr Drugs 2002;4(1):21-8. doi: 10.2165/00128072-200204010-00003. PMID: 11817983

Recent clinical studies

Etiology

Treatment outcomes of extraskeletal Ewing sarcoma.
Houdek MT, Heidenreich MJ, Ahmed SK, Allen-Rhoades W, Siontis BL, Robinson SI, Petersen IA, Rose PS
J Surg Oncol 2023 Jul;128(1):105-110. Epub 2023 Mar 31 doi: 10.1002/jso.27250. PMID: 36999583
Extraskeletal Ewing Sarcoma from Head to Toe: Multimodality Imaging Review.
Wright A, Desai M, Bolan CW, Badawy M, Guccione J, Rao Korivi B, Pickhardt PJ, Mellnick VM, Lubner MG, Chen L, Elsayes KM
Radiographics 2022 Jul-Aug;42(4):1145-1160. Epub 2022 May 27 doi: 10.1148/rg.210226. PMID: 35622491
Small-Cell Malignancies of Thyroid: Challenge Solved?
Canberk S, Thodou E, Bongiovanni M
Acta Cytol 2022;66(4):307-318. Epub 2022 Jan 11 doi: 10.1159/000520876. PMID: 35016187
Extraosseous Ewing sarcoma in children and adolescents: A retrospective series from a referral pediatric oncology center.
Livellara V, Bergamaschi L, Puma N, Chiaravalli S, Podda M, Casanova M, Gasparini P, Pecori E, Alessandro O, Nigro O, Sironi G, Gattuso G, Terenziani M, Spreafico F, Meazza C, Biassoni V, Schiavello E, Massimino M, Luksch R, Ferrari A
Pediatr Blood Cancer 2022 May;69(5):e29512. Epub 2021 Dec 28 doi: 10.1002/pbc.29512. PMID: 34962687
Extraskeletal Ewing's sarcoma.
Ahmad R, Mayol BR, Davis M, Rougraff BT
Cancer 1999 Feb 1;85(3):725-31. PMID: 10091746

Diagnosis

Extraskeletal Ewing Sarcoma from Head to Toe: Multimodality Imaging Review.
Wright A, Desai M, Bolan CW, Badawy M, Guccione J, Rao Korivi B, Pickhardt PJ, Mellnick VM, Lubner MG, Chen L, Elsayes KM
Radiographics 2022 Jul-Aug;42(4):1145-1160. Epub 2022 May 27 doi: 10.1148/rg.210226. PMID: 35622491
Small-Cell Malignancies of Thyroid: Challenge Solved?
Canberk S, Thodou E, Bongiovanni M
Acta Cytol 2022;66(4):307-318. Epub 2022 Jan 11 doi: 10.1159/000520876. PMID: 35016187
Extra-skeletal Ewing's sarcoma of the submandibular gland.
Agir H, Brasch HD, Tan ST
J Plast Reconstr Aesthet Surg 2007;60(12):1345-8. Epub 2006 Jun 12 doi: 10.1016/j.bjps.2006.01.046. PMID: 18005924
Multiple cardiac metastases from Ewing's sarcoma.
Chandramohan NK, Hussain MB, Nayak N, Kattoor J, Pandey M, Krishnankutty R
Can J Cardiol 2005 May 1;21(6):525-7. PMID: 15917882
Der(16)t(1;16)(q21;q13) as a secondary structural aberration in yet a third sarcoma, extraskeletal myxoid chondrosarcoma.
Day SJ, Nelson M, Rosenthal H, Vergara GG, Bridge JA
Genes Chromosomes Cancer 1997 Dec;20(4):425-7. PMID: 9408761

Therapy

Treatment outcomes of extraskeletal Ewing sarcoma.
Houdek MT, Heidenreich MJ, Ahmed SK, Allen-Rhoades W, Siontis BL, Robinson SI, Petersen IA, Rose PS
J Surg Oncol 2023 Jul;128(1):105-110. Epub 2023 Mar 31 doi: 10.1002/jso.27250. PMID: 36999583
Extraosseous Ewing sarcoma in children and adolescents: A retrospective series from a referral pediatric oncology center.
Livellara V, Bergamaschi L, Puma N, Chiaravalli S, Podda M, Casanova M, Gasparini P, Pecori E, Alessandro O, Nigro O, Sironi G, Gattuso G, Terenziani M, Spreafico F, Meazza C, Biassoni V, Schiavello E, Massimino M, Luksch R, Ferrari A
Pediatr Blood Cancer 2022 May;69(5):e29512. Epub 2021 Dec 28 doi: 10.1002/pbc.29512. PMID: 34962687
Extraskeletal Ewing's sarcoma: a report of 18 cases and literature review.
Xie CF, Liu MZ, Xi M
Chin J Cancer 2010 Apr;29(4):420-4. doi: 10.5732/cjc.009.10402. PMID: 20346219
Multiple cardiac metastases from Ewing's sarcoma.
Chandramohan NK, Hussain MB, Nayak N, Kattoor J, Pandey M, Krishnankutty R
Can J Cardiol 2005 May 1;21(6):525-7. PMID: 15917882
Angiotensin-induced hypertension chemotherapy in children with advanced solid tumors.
Fujii Y, Hongo T, Masui H, Chiba T, Furukawa N, Nakajima H, Nasuda K, Yajima S, Horikoshi Y, Igarashi Y
Acta Paediatr Jpn 1991 Jun;33(3):381-3. doi: 10.1111/j.1442-200x.1991.tb01570.x. PMID: 1664635

Prognosis

Extraskeletal Ewing Sarcoma from Head to Toe: Multimodality Imaging Review.
Wright A, Desai M, Bolan CW, Badawy M, Guccione J, Rao Korivi B, Pickhardt PJ, Mellnick VM, Lubner MG, Chen L, Elsayes KM
Radiographics 2022 Jul-Aug;42(4):1145-1160. Epub 2022 May 27 doi: 10.1148/rg.210226. PMID: 35622491
Extraosseous Ewing sarcoma in children and adolescents: A retrospective series from a referral pediatric oncology center.
Livellara V, Bergamaschi L, Puma N, Chiaravalli S, Podda M, Casanova M, Gasparini P, Pecori E, Alessandro O, Nigro O, Sironi G, Gattuso G, Terenziani M, Spreafico F, Meazza C, Biassoni V, Schiavello E, Massimino M, Luksch R, Ferrari A
Pediatr Blood Cancer 2022 May;69(5):e29512. Epub 2021 Dec 28 doi: 10.1002/pbc.29512. PMID: 34962687
Extraskeletal Ewing's sarcoma: a report of 18 cases and literature review.
Xie CF, Liu MZ, Xi M
Chin J Cancer 2010 Apr;29(4):420-4. doi: 10.5732/cjc.009.10402. PMID: 20346219
Extra-skeletal Ewing's sarcoma of the submandibular gland.
Agir H, Brasch HD, Tan ST
J Plast Reconstr Aesthet Surg 2007;60(12):1345-8. Epub 2006 Jun 12 doi: 10.1016/j.bjps.2006.01.046. PMID: 18005924
Extraskeletal Ewing's sarcoma.
Ahmad R, Mayol BR, Davis M, Rougraff BT
Cancer 1999 Feb 1;85(3):725-31. PMID: 10091746

Clinical prediction guides

Extraskeletal, intradural, non-metastatic Ewing's sarcoma. Case report.
Ottóffy G, Komáromy H
Ideggyogy Sz 2020 Jul 30;73(7-08):286-288. doi: 10.18071/isz.73.0268. PMID: 32750246
Advantages in Prognosis of Adult Patients with Ewing Sarcoma: 11-years Experiences and Current Treatment Management.
Krakorova DA, Kubackova K, Dusek L, Tomas T, Janicek P, Tucek S, Prausova J, Kiss I, Zambo I
Pathol Oncol Res 2018 Jul;24(3):623-630. Epub 2017 Aug 12 doi: 10.1007/s12253-017-0291-6. PMID: 28803261
Cervical Primary Ewing's Sarcoma in Intradural and Extramedullary Location and Skip Metastasis to Cauda Equina.
Gong HS, Huang QS, Liu GJ, Chen FH, Zhao HB
Turk Neurosurg 2015;25(6):943-7. doi: 10.5137/1019-5149.JTN.12025-14.2. PMID: 26617147
Extraskeletal Ewing's sarcoma family of tumors in adults: prognostic factors and clinical outcome.
Tural D, Molinas Mandel N, Dervisoglu S, Oner Dincbas F, Koca S, Colpan Oksuz D, Kantarci F, Turna H, Selcukbiricik F, Hiz M
Jpn J Clin Oncol 2012 May;42(5):420-6. Epub 2012 Mar 12 doi: 10.1093/jjco/hys027. PMID: 22416252
Clinical features and outcomes in patients with Ewing sarcoma and regional lymph node involvement.
Applebaum MA, Goldsby R, Neuhaus J, DuBois SG
Pediatr Blood Cancer 2012 Oct;59(4):617-20. Epub 2011 Dec 19 doi: 10.1002/pbc.24053. PMID: 22184129Free PMC Article

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