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Metastatic Extraskeletal Ewing Sarcoma

MedGen UID:
163504
•Concept ID:
C0855042
•
Neoplastic Process
Synonyms: Extra-Osseous Ewing's Sarcoma, Metastatic; Metastatic Extra-Osseous Ewing's Sarcoma; Metastatic Extraosseous Ewing Sarcoma; Metastatic Extraosseous Ewing's Sarcoma; Metastatic Extraskeletal Ewing's Sarcoma

Definition

An Ewing sarcoma of the soft tissues which has spread from its original site of growth to another anatomic site. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVMetastatic Extraskeletal Ewing Sarcoma

Professional guidelines

PubMed

Treatment outcomes of extraskeletal Ewing sarcoma.
Houdek MT, Heidenreich MJ, Ahmed SK, Allen-Rhoades W, Siontis BL, Robinson SI, Petersen IA, Rose PS
J Surg Oncol 2023 Jul;128(1):105-110. Epub 2023 Mar 31 doi: 10.1002/jso.27250. PMID: 36999583
Advantages in Prognosis of Adult Patients with Ewing Sarcoma: 11-years Experiences and Current Treatment Management.
Krakorova DA, Kubackova K, Dusek L, Tomas T, Janicek P, Tucek S, Prausova J, Kiss I, Zambo I
Pathol Oncol Res 2018 Jul;24(3):623-630. Epub 2017 Aug 12 doi: 10.1007/s12253-017-0291-6. PMID: 28803261
A to Z of extraskeletal Ewing sarcoma family of tumors in adults: imaging features of primary disease, metastatic patterns, and treatment responses.
Javery O, Krajewski K, O'Regan K, Kis B, Giardino A, Jagannathan J, Ramaiya NH
AJR Am J Roentgenol 2011 Dec;197(6):W1015-22. doi: 10.2214/AJR.11.6667. PMID: 22109315

Recent clinical studies

Etiology

Treatment outcomes of extraskeletal Ewing sarcoma.
Houdek MT, Heidenreich MJ, Ahmed SK, Allen-Rhoades W, Siontis BL, Robinson SI, Petersen IA, Rose PS
J Surg Oncol 2023 Jul;128(1):105-110. Epub 2023 Mar 31 doi: 10.1002/jso.27250. PMID: 36999583
Extraskeletal Ewing Sarcoma from Head to Toe: Multimodality Imaging Review.
Wright A, Desai M, Bolan CW, Badawy M, Guccione J, Rao Korivi B, Pickhardt PJ, Mellnick VM, Lubner MG, Chen L, Elsayes KM
Radiographics 2022 Jul-Aug;42(4):1145-1160. Epub 2022 May 27 doi: 10.1148/rg.210226. PMID: 35622491
Small-Cell Malignancies of Thyroid: Challenge Solved?
Canberk S, Thodou E, Bongiovanni M
Acta Cytol 2022;66(4):307-318. Epub 2022 Jan 11 doi: 10.1159/000520876. PMID: 35016187
Extraosseous Ewing sarcoma in children and adolescents: A retrospective series from a referral pediatric oncology center.
Livellara V, Bergamaschi L, Puma N, Chiaravalli S, Podda M, Casanova M, Gasparini P, Pecori E, Alessandro O, Nigro O, Sironi G, Gattuso G, Terenziani M, Spreafico F, Meazza C, Biassoni V, Schiavello E, Massimino M, Luksch R, Ferrari A
Pediatr Blood Cancer 2022 May;69(5):e29512. Epub 2021 Dec 28 doi: 10.1002/pbc.29512. PMID: 34962687
Extraskeletal Ewing's sarcoma.
Ahmad R, Mayol BR, Davis M, Rougraff BT
Cancer 1999 Feb 1;85(3):725-31. PMID: 10091746

Diagnosis

Extraskeletal Ewing Sarcoma from Head to Toe: Multimodality Imaging Review.
Wright A, Desai M, Bolan CW, Badawy M, Guccione J, Rao Korivi B, Pickhardt PJ, Mellnick VM, Lubner MG, Chen L, Elsayes KM
Radiographics 2022 Jul-Aug;42(4):1145-1160. Epub 2022 May 27 doi: 10.1148/rg.210226. PMID: 35622491
Small-Cell Malignancies of Thyroid: Challenge Solved?
Canberk S, Thodou E, Bongiovanni M
Acta Cytol 2022;66(4):307-318. Epub 2022 Jan 11 doi: 10.1159/000520876. PMID: 35016187
Extraskeletal, intradural, non-metastatic Ewing's sarcoma. Case report.
Ottóffy G, Komáromy H
Ideggyogy Sz 2020 Jul 30;73(7-08):286-288. doi: 10.18071/isz.73.0268. PMID: 32750246
Extraskeletal Ewing's sarcoma: a report of 18 cases and literature review.
Xie CF, Liu MZ, Xi M
Chin J Cancer 2010 Apr;29(4):420-4. doi: 10.5732/cjc.009.10402. PMID: 20346219
Extraskeletal Ewing's sarcoma.
Ahmad R, Mayol BR, Davis M, Rougraff BT
Cancer 1999 Feb 1;85(3):725-31. PMID: 10091746

Therapy

Treatment outcomes of extraskeletal Ewing sarcoma.
Houdek MT, Heidenreich MJ, Ahmed SK, Allen-Rhoades W, Siontis BL, Robinson SI, Petersen IA, Rose PS
J Surg Oncol 2023 Jul;128(1):105-110. Epub 2023 Mar 31 doi: 10.1002/jso.27250. PMID: 36999583
Extraosseous Ewing sarcoma in children and adolescents: A retrospective series from a referral pediatric oncology center.
Livellara V, Bergamaschi L, Puma N, Chiaravalli S, Podda M, Casanova M, Gasparini P, Pecori E, Alessandro O, Nigro O, Sironi G, Gattuso G, Terenziani M, Spreafico F, Meazza C, Biassoni V, Schiavello E, Massimino M, Luksch R, Ferrari A
Pediatr Blood Cancer 2022 May;69(5):e29512. Epub 2021 Dec 28 doi: 10.1002/pbc.29512. PMID: 34962687
Primary metastasized extraskeletal Ewing sarcoma of the vulva: report of a case and review of the literature.
Kelling K, Noack F, Altgassen C, Kujath P, Bohlmann MK, Hoellen F
Arch Gynecol Obstet 2012 Mar;285(3):785-9. Epub 2011 Jul 30 doi: 10.1007/s00404-011-2011-x. PMID: 21805144
Extraskeletal Ewing's sarcoma: a report of 18 cases and literature review.
Xie CF, Liu MZ, Xi M
Chin J Cancer 2010 Apr;29(4):420-4. doi: 10.5732/cjc.009.10402. PMID: 20346219
Extraskeletal Ewing's sarcoma.
Ahmad R, Mayol BR, Davis M, Rougraff BT
Cancer 1999 Feb 1;85(3):725-31. PMID: 10091746

Prognosis

Extraskeletal Ewing Sarcoma from Head to Toe: Multimodality Imaging Review.
Wright A, Desai M, Bolan CW, Badawy M, Guccione J, Rao Korivi B, Pickhardt PJ, Mellnick VM, Lubner MG, Chen L, Elsayes KM
Radiographics 2022 Jul-Aug;42(4):1145-1160. Epub 2022 May 27 doi: 10.1148/rg.210226. PMID: 35622491
Extraosseous Ewing sarcoma in children and adolescents: A retrospective series from a referral pediatric oncology center.
Livellara V, Bergamaschi L, Puma N, Chiaravalli S, Podda M, Casanova M, Gasparini P, Pecori E, Alessandro O, Nigro O, Sironi G, Gattuso G, Terenziani M, Spreafico F, Meazza C, Biassoni V, Schiavello E, Massimino M, Luksch R, Ferrari A
Pediatr Blood Cancer 2022 May;69(5):e29512. Epub 2021 Dec 28 doi: 10.1002/pbc.29512. PMID: 34962687
Extraskeletal Ewing's sarcoma family of tumors in adults: prognostic factors and clinical outcome.
Tural D, Molinas Mandel N, Dervisoglu S, Oner Dincbas F, Koca S, Colpan Oksuz D, Kantarci F, Turna H, Selcukbiricik F, Hiz M
Jpn J Clin Oncol 2012 May;42(5):420-6. Epub 2012 Mar 12 doi: 10.1093/jjco/hys027. PMID: 22416252
Extraskeletal Ewing's sarcoma: a report of 18 cases and literature review.
Xie CF, Liu MZ, Xi M
Chin J Cancer 2010 Apr;29(4):420-4. doi: 10.5732/cjc.009.10402. PMID: 20346219
Extraskeletal Ewing's sarcoma.
Ahmad R, Mayol BR, Davis M, Rougraff BT
Cancer 1999 Feb 1;85(3):725-31. PMID: 10091746

Clinical prediction guides

Extraskeletal, intradural, non-metastatic Ewing's sarcoma. Case report.
Ottóffy G, Komáromy H
Ideggyogy Sz 2020 Jul 30;73(7-08):286-288. doi: 10.18071/isz.73.0268. PMID: 32750246
Advantages in Prognosis of Adult Patients with Ewing Sarcoma: 11-years Experiences and Current Treatment Management.
Krakorova DA, Kubackova K, Dusek L, Tomas T, Janicek P, Tucek S, Prausova J, Kiss I, Zambo I
Pathol Oncol Res 2018 Jul;24(3):623-630. Epub 2017 Aug 12 doi: 10.1007/s12253-017-0291-6. PMID: 28803261
Extraskeletal Ewing's sarcoma family of tumors in adults: prognostic factors and clinical outcome.
Tural D, Molinas Mandel N, Dervisoglu S, Oner Dincbas F, Koca S, Colpan Oksuz D, Kantarci F, Turna H, Selcukbiricik F, Hiz M
Jpn J Clin Oncol 2012 May;42(5):420-6. Epub 2012 Mar 12 doi: 10.1093/jjco/hys027. PMID: 22416252
Clinical features and outcomes in patients with Ewing sarcoma and regional lymph node involvement.
Applebaum MA, Goldsby R, Neuhaus J, DuBois SG
Pediatr Blood Cancer 2012 Oct;59(4):617-20. Epub 2011 Dec 19 doi: 10.1002/pbc.24053. PMID: 22184129Free PMC Article
Whole-body MRI for detecting metastatic bone tumor: diagnostic value of diffusion-weighted images.
Nakanishi K, Kobayashi M, Nakaguchi K, Kyakuno M, Hashimoto N, Onishi H, Maeda N, Nakata S, Kuwabara M, Murakami T, Nakamura H
Magn Reson Med Sci 2007;6(3):147-55. doi: 10.2463/mrms.6.147. PMID: 18037795

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