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Advanced Malignant Peripheral Nerve Sheath Tumor

MedGen UID:
1712867
Concept ID:
C5239068
Neoplastic Process

Definition

A malignant peripheral nerve sheath tumor that has spread extensively to other anatomic sites or is no longer responding to treatment. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVAdvanced Malignant Peripheral Nerve Sheath Tumor

Professional guidelines

PubMed

Al-Ezzi E, Gounder M, Watson G, Mazzocca A, D'Angelo SP, Bravetti J, Wang H, Abdul Razak A, Vincenzi B
Oncologist 2021 Apr;26(4):e710-e714. Epub 2021 Feb 17 doi: 10.1002/onco.13692. PMID: 33512749Free PMC Article

Recent clinical studies

Etiology

Brown R
Curr Oncol Rep 2023 Dec;25(12):1409-1417. Epub 2023 Oct 31 doi: 10.1007/s11912-023-01451-z. PMID: 37906356
Lemberg KM, Wang J, Pratilas CA
Genes (Basel) 2020 Jun 24;11(6) doi: 10.3390/genes11060691. PMID: 32599735Free PMC Article
Abreu E, Aubert S, Wavreille G, Gheno R, Canella C, Cotten A
Eur J Radiol 2013 Jan;82(1):38-50. Epub 2011 May 10 doi: 10.1016/j.ejrad.2011.04.036. PMID: 21561733
Rodriguez FJ, Folpe AL, Giannini C, Perry A
Acta Neuropathol 2012 Mar;123(3):295-319. Epub 2012 Feb 12 doi: 10.1007/s00401-012-0954-z. PMID: 22327363Free PMC Article
Mrugala MM, Batchelor TT, Plotkin SR
Curr Opin Neurol 2005 Oct;18(5):604-10. doi: 10.1097/01.wco.0000179507.51647.02. PMID: 16155448

Diagnosis

Lefebvre G, Le Corroller T
Skeletal Radiol 2023 Mar;52(3):405-419. Epub 2022 Jun 17 doi: 10.1007/s00256-022-04087-5. PMID: 35713690
Hassan A, Pestana RC, Parkes A
Curr Treat Options Oncol 2021 Feb 27;22(4):33. doi: 10.1007/s11864-021-00830-7. PMID: 33641042
Farid M, Demicco EG, Garcia R, Ahn L, Merola PR, Cioffi A, Maki RG
Oncologist 2014 Feb;19(2):193-201. Epub 2014 Jan 27 doi: 10.1634/theoncologist.2013-0328. PMID: 24470531Free PMC Article
Ferner RE, Gutmann DH
Handb Clin Neurol 2013;115:939-55. doi: 10.1016/B978-0-444-52902-2.00053-9. PMID: 23931823
Korf BR
Am J Med Genet 1999 Mar 26;89(1):31-7. doi: 10.1002/(sici)1096-8628(19990326)89:1<31::aid-ajmg7>3.0.co;2-w. PMID: 10469434

Therapy

Brown R
Curr Oncol Rep 2023 Dec;25(12):1409-1417. Epub 2023 Oct 31 doi: 10.1007/s11912-023-01451-z. PMID: 37906356
Fernández-Rodríguez J, Creus-Bachiller E, Zhang X, Martínez-Iniesta M, Ortega-Bertran S, Guha R, Thomas CJ, Wallace MR, Romagosa C, Salazar-Huayna L, Reilly KM, Blakely JO, Serra-Musach J, Pujana MA, Serra E, Villanueva A, Ferrer M, Lázaro C
Mol Cancer Ther 2022 Jul 5;21(7):1246-1258. doi: 10.1158/1535-7163.MCT-21-0947. PMID: 35511749Free PMC Article
Galvin R, Watson AL, Largaespada DA, Ratner N, Osum S, Moertel CL
Curr Oncol Rep 2021 Mar 15;23(4):45. doi: 10.1007/s11912-021-01032-y. PMID: 33721151Free PMC Article
Butler E, Schwettmann B, Geboers S, Hao G, Kim J, Nham K, Sun X, Laetsch TW, Xu L, Williams NS, Skapek SX
Pediatr Blood Cancer 2020 Dec;67(12):e28639. Epub 2020 Sep 25 doi: 10.1002/pbc.28639. PMID: 32975370
Karpinsky G, Krawczyk MA, Izycka-Swieszewska E, Fatyga A, Budka A, Balwierz W, Sobol G, Zalewska-Szewczyk B, Rychlowska-Pruszynska M, Klepacka T, Dembowska-Baginska B, Kazanowska B, Gabrych A, Bien E
J Cancer Res Clin Oncol 2018 Mar;144(3):519-529. Epub 2018 Jan 13 doi: 10.1007/s00432-018-2580-1. PMID: 29332262Free PMC Article

Prognosis

Brown R
Curr Oncol Rep 2023 Dec;25(12):1409-1417. Epub 2023 Oct 31 doi: 10.1007/s11912-023-01451-z. PMID: 37906356
Hassan A, Pestana RC, Parkes A
Curr Treat Options Oncol 2021 Feb 27;22(4):33. doi: 10.1007/s11864-021-00830-7. PMID: 33641042
Abdel Razek AAK, Gamaleldin OA, Elsebaie NA
J Comput Assist Tomogr 2020 Nov/Dec;44(6):928-940. doi: 10.1097/RCT.0000000000001109. PMID: 33196600
Assadi M, Velez E, Najafi MH, Matcuk G, Gholamrezanezhad A
PET Clin 2019 Jan;14(1):81-89. Epub 2018 Oct 24 doi: 10.1016/j.cpet.2018.08.013. PMID: 30420224
Farid M, Demicco EG, Garcia R, Ahn L, Merola PR, Cioffi A, Maki RG
Oncologist 2014 Feb;19(2):193-201. Epub 2014 Jan 27 doi: 10.1634/theoncologist.2013-0328. PMID: 24470531Free PMC Article

Clinical prediction guides

Fernández-Rodríguez J, Creus-Bachiller E, Zhang X, Martínez-Iniesta M, Ortega-Bertran S, Guha R, Thomas CJ, Wallace MR, Romagosa C, Salazar-Huayna L, Reilly KM, Blakely JO, Serra-Musach J, Pujana MA, Serra E, Villanueva A, Ferrer M, Lázaro C
Mol Cancer Ther 2022 Jul 5;21(7):1246-1258. doi: 10.1158/1535-7163.MCT-21-0947. PMID: 35511749Free PMC Article
Schaefer IM, Hornick JL
Semin Diagn Pathol 2021 May;38(3):222-231. Epub 2020 Jun 5 doi: 10.1053/j.semdp.2020.05.005. PMID: 32646614Free PMC Article
Abdel Razek AAK, Gamaleldin OA, Elsebaie NA
J Comput Assist Tomogr 2020 Nov/Dec;44(6):928-940. doi: 10.1097/RCT.0000000000001109. PMID: 33196600
Abreu E, Aubert S, Wavreille G, Gheno R, Canella C, Cotten A
Eur J Radiol 2013 Jan;82(1):38-50. Epub 2011 May 10 doi: 10.1016/j.ejrad.2011.04.036. PMID: 21561733
Rodriguez FJ, Folpe AL, Giannini C, Perry A
Acta Neuropathol 2012 Mar;123(3):295-319. Epub 2012 Feb 12 doi: 10.1007/s00401-012-0954-z. PMID: 22327363Free PMC Article

Recent systematic reviews

Drews MA, Milosevic A, Hamacher R, Grüneisen JS, Haubold J, Opitz MK, Bauer S, Umutlu L, Forsting M, Schaarschmidt BM
Br J Radiol 2024 Feb 2;97(1154):430-438. doi: 10.1093/bjr/tqad035. PMID: 38308031

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