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Advanced Undifferentiated Pleomorphic Sarcoma

MedGen UID:
1715501
Concept ID:
C5237456
Neoplastic Process

Definition

An undifferentiated pleomorphic sarcoma that has spread extensively to other anatomic sites or is no longer responding to treatment. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVAdvanced Undifferentiated Pleomorphic Sarcoma

Professional guidelines

PubMed

Crago AM, Cardona K, Koseła-Paterczyk H, Rutkowski P
Surg Oncol Clin N Am 2022 Jul;31(3):419-430. doi: 10.1016/j.soc.2022.03.006. PMID: 35715142
Thway K, Fisher C
Semin Diagn Pathol 2021 Nov;38(6):170-186. Epub 2021 Sep 29 doi: 10.1053/j.semdp.2021.09.005. PMID: 34602314
Widemann BC, Italiano A
J Clin Oncol 2018 Jan 10;36(2):160-167. Epub 2017 Dec 8 doi: 10.1200/JCO.2017.75.3467. PMID: 29220302Free PMC Article

Recent clinical studies

Etiology

Somaiah N, Conley AP, Parra ER, Lin H, Amini B, Solis Soto L, Salazar R, Barreto C, Chen H, Gite S, Haymaker C, Nassif EF, Bernatchez C, Mitra A, Livingston JA, Ravi V, Araujo DM, Benjamin R, Patel S, Zarzour MA, Sabir S, Lazar AJ, Wang WL, Daw NC, Zhou X, Roland CL, Cooper ZA, Rodriguez-Canales J, Futreal A, Soria JC, Wistuba II, Hwu P
Lancet Oncol 2022 Sep;23(9):1156-1166. Epub 2022 Aug 4 doi: 10.1016/S1470-2045(22)00392-8. PMID: 35934010
Crago AM, Cardona K, Koseła-Paterczyk H, Rutkowski P
Surg Oncol Clin N Am 2022 Jul;31(3):419-430. doi: 10.1016/j.soc.2022.03.006. PMID: 35715142
Tang F, Tie Y, Wei YQ, Tu CQ, Wei XW
Biochim Biophys Acta Rev Cancer 2021 Dec;1876(2):188606. Epub 2021 Aug 8 doi: 10.1016/j.bbcan.2021.188606. PMID: 34371128
Kokkali S, Stravodimou A, Duran-Moreno J, Koufopoulos N, Voutsadakis IA, Digklia A
Expert Rev Anticancer Ther 2021 Jun;21(6):591-604. Epub 2021 Mar 12 doi: 10.1080/14737140.2021.1880327. PMID: 33554686
Tawbi HA, Burgess M, Bolejack V, Van Tine BA, Schuetze SM, Hu J, D'Angelo S, Attia S, Riedel RF, Priebat DA, Movva S, Davis LE, Okuno SH, Reed DR, Crowley J, Butterfield LH, Salazar R, Rodriguez-Canales J, Lazar AJ, Wistuba II, Baker LH, Maki RG, Reinke D, Patel S
Lancet Oncol 2017 Nov;18(11):1493-1501. Epub 2017 Oct 4 doi: 10.1016/S1470-2045(17)30624-1. PMID: 28988646Free PMC Article

Diagnosis

Crago AM, Cardona K, Koseła-Paterczyk H, Rutkowski P
Surg Oncol Clin N Am 2022 Jul;31(3):419-430. doi: 10.1016/j.soc.2022.03.006. PMID: 35715142
Thway K, Fisher C
Semin Diagn Pathol 2021 Nov;38(6):170-186. Epub 2021 Sep 29 doi: 10.1053/j.semdp.2021.09.005. PMID: 34602314
Karakas C, Christensen P, Baek D, Jung M, Ro JY
Ann Diagn Pathol 2019 Apr;39:118-124. Epub 2018 Dec 18 doi: 10.1016/j.anndiagpath.2018.12.005. PMID: 30661742
Ray-Coquard I, Serre D, Reichardt P, Martín-Broto J, Bauer S
Future Oncol 2018 May;14(10s):25-49. doi: 10.2217/fon-2018-0076. PMID: 29768052
Widemann BC, Italiano A
J Clin Oncol 2018 Jan 10;36(2):160-167. Epub 2017 Dec 8 doi: 10.1200/JCO.2017.75.3467. PMID: 29220302Free PMC Article

Therapy

Somaiah N, Conley AP, Parra ER, Lin H, Amini B, Solis Soto L, Salazar R, Barreto C, Chen H, Gite S, Haymaker C, Nassif EF, Bernatchez C, Mitra A, Livingston JA, Ravi V, Araujo DM, Benjamin R, Patel S, Zarzour MA, Sabir S, Lazar AJ, Wang WL, Daw NC, Zhou X, Roland CL, Cooper ZA, Rodriguez-Canales J, Futreal A, Soria JC, Wistuba II, Hwu P
Lancet Oncol 2022 Sep;23(9):1156-1166. Epub 2022 Aug 4 doi: 10.1016/S1470-2045(22)00392-8. PMID: 35934010
Demetri GD, Luke JJ, Hollebecque A, Powderly JD 2nd, Spira AI, Subbiah V, Naumovski L, Chen C, Fang H, Lai DW, Yue H, Polepally AR, Purcell JW, Robinson R, Sharma P, Allison JP, Tolcher A, Villalobos VM
Clin Cancer Res 2021 Jul 1;27(13):3556-3566. Epub 2021 Apr 5 doi: 10.1158/1078-0432.CCR-20-4513. PMID: 33820780
Karakas C, Christensen P, Baek D, Jung M, Ro JY
Ann Diagn Pathol 2019 Apr;39:118-124. Epub 2018 Dec 18 doi: 10.1016/j.anndiagpath.2018.12.005. PMID: 30661742
Ray-Coquard I, Serre D, Reichardt P, Martín-Broto J, Bauer S
Future Oncol 2018 May;14(10s):25-49. doi: 10.2217/fon-2018-0076. PMID: 29768052
Tawbi HA, Burgess M, Bolejack V, Van Tine BA, Schuetze SM, Hu J, D'Angelo S, Attia S, Riedel RF, Priebat DA, Movva S, Davis LE, Okuno SH, Reed DR, Crowley J, Butterfield LH, Salazar R, Rodriguez-Canales J, Lazar AJ, Wistuba II, Baker LH, Maki RG, Reinke D, Patel S
Lancet Oncol 2017 Nov;18(11):1493-1501. Epub 2017 Oct 4 doi: 10.1016/S1470-2045(17)30624-1. PMID: 28988646Free PMC Article

Prognosis

Thway K, Fisher C
Semin Diagn Pathol 2021 Nov;38(6):170-186. Epub 2021 Sep 29 doi: 10.1053/j.semdp.2021.09.005. PMID: 34602314
You Y, Shi R, Dai M, Du Z, Tian Z, Xu G, Wang L, Wang Y, Xiao M
Histol Histopathol 2021 Aug;36(8):889-898. Epub 2021 Jul 20 doi: 10.14670/HH-18-359. PMID: 34282850
Zhu MMT, Shenasa E, Nielsen TO
Cancer Treat Rev 2020 Dec;91:102115. Epub 2020 Oct 20 doi: 10.1016/j.ctrv.2020.102115. PMID: 33130422
Ray-Coquard I, Serre D, Reichardt P, Martín-Broto J, Bauer S
Future Oncol 2018 May;14(10s):25-49. doi: 10.2217/fon-2018-0076. PMID: 29768052
Tawbi HA, Burgess M, Bolejack V, Van Tine BA, Schuetze SM, Hu J, D'Angelo S, Attia S, Riedel RF, Priebat DA, Movva S, Davis LE, Okuno SH, Reed DR, Crowley J, Butterfield LH, Salazar R, Rodriguez-Canales J, Lazar AJ, Wistuba II, Baker LH, Maki RG, Reinke D, Patel S
Lancet Oncol 2017 Nov;18(11):1493-1501. Epub 2017 Oct 4 doi: 10.1016/S1470-2045(17)30624-1. PMID: 28988646Free PMC Article

Clinical prediction guides

Crago AM, Cardona K, Koseła-Paterczyk H, Rutkowski P
Surg Oncol Clin N Am 2022 Jul;31(3):419-430. doi: 10.1016/j.soc.2022.03.006. PMID: 35715142
García-Ortega DY, Melendez-Fernandez AP, Alvarez-Cano A, Clara-Altamirano MA, Caro-Sanchez C, Alamilla-Garcia G, Luna-Ortiz K
Surg Oncol 2022 Jun;42:101746. Epub 2022 Mar 29 doi: 10.1016/j.suronc.2022.101746. PMID: 35378375
Demetri GD, Luke JJ, Hollebecque A, Powderly JD 2nd, Spira AI, Subbiah V, Naumovski L, Chen C, Fang H, Lai DW, Yue H, Polepally AR, Purcell JW, Robinson R, Sharma P, Allison JP, Tolcher A, Villalobos VM
Clin Cancer Res 2021 Jul 1;27(13):3556-3566. Epub 2021 Apr 5 doi: 10.1158/1078-0432.CCR-20-4513. PMID: 33820780
Rosko AJ, Birkeland AC, Chinn SB, Shuman AG, Prince ME, Patel RM, McHugh JB, Spector ME
Otolaryngol Head Neck Surg 2017 Aug;157(2):252-259. Epub 2017 Apr 11 doi: 10.1177/0194599817700389. PMID: 28397585
Becerikli M, Wieczorek S, Stricker I, Nambiar S, Rittig A, Epplen JT, Tannapfel A, Lehnhardt M, Steinstraesser L, Jacobsen F
Anticancer Res 2014 Dec;34(12):7119-27. PMID: 25503139

Recent systematic reviews

Saerens M, Brusselaers N, Rottey S, Decruyenaere A, Creytens D, Lapeire L
Eur J Cancer 2021 Jul;152:165-182. Epub 2021 Jun 6 doi: 10.1016/j.ejca.2021.04.034. PMID: 34107450
Neuwirth MG, Song Y, Sinnamon AJ, Fraker DL, Zager JS, Karakousis GC
Ann Surg Oncol 2017 Dec;24(13):3803-3810. Epub 2017 Oct 11 doi: 10.1245/s10434-017-6109-7. PMID: 29022281

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