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Sinonasal Undifferentiated Pleomorphic Sarcoma

MedGen UID:
1751735
•Concept ID:
C5420046
•
Neoplastic Process

Definition

An undifferentiated pleomorphic sarcoma that arises from the nasal cavity and paranasal sinuses. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVSinonasal Undifferentiated Pleomorphic Sarcoma

Professional guidelines

PubMed

Management of adult soft tissue sarcomas of the head and neck.
de Bree R, van der Waal I, de Bree E, Leemans CR
Oral Oncol 2010 Nov;46(11):786-90. Epub 2010 Oct 13 doi: 10.1016/j.oraloncology.2010.09.001. PMID: 20947413

Recent clinical studies

Etiology

Sinonasal/basicranial myxofibrosarcoma: a report of 6 surgical cases combined with a literature review.
Li H, Wang H, Wang D
Braz J Otorhinolaryngol 2022 Nov-Dec;88 Suppl 5(Suppl 5):S171-S178. Epub 2022 Feb 15 doi: 10.1016/j.bjorl.2022.02.001. PMID: 35256287Free PMC Article
Management of adult soft tissue sarcomas of the head and neck.
de Bree R, van der Waal I, de Bree E, Leemans CR
Oral Oncol 2010 Nov;46(11):786-90. Epub 2010 Oct 13 doi: 10.1016/j.oraloncology.2010.09.001. PMID: 20947413
Primary mucosal melanoma of the head and neck: a proposal for microstaging localized, Stage I (lymph node-negative) tumors.
Prasad ML, Patel SG, Huvos AG, Shah JP, Busam KJ
Cancer 2004 Apr 15;100(8):1657-64. doi: 10.1002/cncr.20201. PMID: 15073854

Diagnosis

PRAME immunohistochemistry in soft tissue tumors and mimics: a study of 350 cases highlighting its imperfect specificity but potentially useful diagnostic applications.
Cammareri C, Beltzung F, Michal M, Vanhersecke L, Coindre JM, Velasco V, Le Loarer F, Vergier B, Perret R
Virchows Arch 2023 Aug;483(2):145-156. Epub 2023 Jul 21 doi: 10.1007/s00428-023-03606-6. PMID: 37477762
Sinonasal/basicranial myxofibrosarcoma: a report of 6 surgical cases combined with a literature review.
Li H, Wang H, Wang D
Braz J Otorhinolaryngol 2022 Nov-Dec;88 Suppl 5(Suppl 5):S171-S178. Epub 2022 Feb 15 doi: 10.1016/j.bjorl.2022.02.001. PMID: 35256287Free PMC Article
Management of adult soft tissue sarcomas of the head and neck.
de Bree R, van der Waal I, de Bree E, Leemans CR
Oral Oncol 2010 Nov;46(11):786-90. Epub 2010 Oct 13 doi: 10.1016/j.oraloncology.2010.09.001. PMID: 20947413
Malignant fibrous histiocytoma of the sinonasal tract.
Wang CP, Chang YL, Ting LL, Yang TL, Ko JY, Lou PJ
Head Neck 2009 Jan;31(1):85-93. doi: 10.1002/hed.20936. PMID: 18853446
Fibrosarcoma of the head and neck.
Frankenthaler R, Ayala AG, Hartwick RW, Goepfert H
Laryngoscope 1990 Aug;100(8):799-802. doi: 10.1288/00005537-199008000-00001. PMID: 2166190

Therapy

Sinonasal/basicranial myxofibrosarcoma: a report of 6 surgical cases combined with a literature review.
Li H, Wang H, Wang D
Braz J Otorhinolaryngol 2022 Nov-Dec;88 Suppl 5(Suppl 5):S171-S178. Epub 2022 Feb 15 doi: 10.1016/j.bjorl.2022.02.001. PMID: 35256287Free PMC Article

Prognosis

Sinonasal/basicranial myxofibrosarcoma: a report of 6 surgical cases combined with a literature review.
Li H, Wang H, Wang D
Braz J Otorhinolaryngol 2022 Nov-Dec;88 Suppl 5(Suppl 5):S171-S178. Epub 2022 Feb 15 doi: 10.1016/j.bjorl.2022.02.001. PMID: 35256287Free PMC Article
Management of adult soft tissue sarcomas of the head and neck.
de Bree R, van der Waal I, de Bree E, Leemans CR
Oral Oncol 2010 Nov;46(11):786-90. Epub 2010 Oct 13 doi: 10.1016/j.oraloncology.2010.09.001. PMID: 20947413
Malignant fibrous histiocytoma of the sinonasal tract.
Wang CP, Chang YL, Ting LL, Yang TL, Ko JY, Lou PJ
Head Neck 2009 Jan;31(1):85-93. doi: 10.1002/hed.20936. PMID: 18853446
Primary mucosal melanoma of the head and neck: a proposal for microstaging localized, Stage I (lymph node-negative) tumors.
Prasad ML, Patel SG, Huvos AG, Shah JP, Busam KJ
Cancer 2004 Apr 15;100(8):1657-64. doi: 10.1002/cncr.20201. PMID: 15073854
Fibrosarcoma of the head and neck.
Frankenthaler R, Ayala AG, Hartwick RW, Goepfert H
Laryngoscope 1990 Aug;100(8):799-802. doi: 10.1288/00005537-199008000-00001. PMID: 2166190

Clinical prediction guides

Primary mucosal melanoma of the head and neck: a proposal for microstaging localized, Stage I (lymph node-negative) tumors.
Prasad ML, Patel SG, Huvos AG, Shah JP, Busam KJ
Cancer 2004 Apr 15;100(8):1657-64. doi: 10.1002/cncr.20201. PMID: 15073854

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