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Digestive System Rhabdomyosarcoma

MedGen UID:
1752521
Concept ID:
C5419974
Neoplastic Process

Definition

A rhabdomyosarcoma arising from an anatomic site in the digestive system. [from NCI]

Professional guidelines

PubMed

Agaimy A, Stoehr R, Hornung A, Popp J, Erdmann M, Heinzerling L, Hartmann A
Am J Surg Pathol 2021 Feb 1;45(2):240-254. doi: 10.1097/PAS.0000000000001645. PMID: 33428337
Urla C, Warmann SW, Sparber-Sauer M, Schuck A, Leuschner I, Klingebiel T, Blumenstock G, Seitz G, Koscielniak E, Fuchs J
BMC Cancer 2019 Oct 14;19(1):945. doi: 10.1186/s12885-019-6172-5. PMID: 31610788Free PMC Article
Geoffray A, Couanet D, Montagne JP, Leclère J, Flamant F
Pediatr Radiol 1987;17(2):127-31. doi: 10.1007/BF02388089. PMID: 3550663

Recent clinical studies

Etiology

Thway K, Fisher C
Surg Pathol Clin 2023 Dec;16(4):765-778. Epub 2023 Jul 11 doi: 10.1016/j.path.2023.05.012. PMID: 37863565
Çebi MN, Yılmaz G, Çelikdemir G, Özcan R, Ocak S, Celkan TT, Çomunoğlu N
Turk J Pediatr 2022;64(2):385-388. doi: 10.24953/turkjped.2021.264. PMID: 35611429
Guo Y, Hu B, Huang D, Wang X, Li J, Zhang D, Li X, Chen G, Ren D
BMC Surg 2021 Jan 30;21(1):66. doi: 10.1186/s12893-021-01073-x. PMID: 33516222Free PMC Article
Agaimy A, Stoehr R, Hornung A, Popp J, Erdmann M, Heinzerling L, Hartmann A
Am J Surg Pathol 2021 Feb 1;45(2):240-254. doi: 10.1097/PAS.0000000000001645. PMID: 33428337
Gökdemir G, Ekmen S, Gungor S, Singer R
Pediatr Dermatol 2013 Jan-Feb;30(1):97-9. Epub 2012 Feb 22 doi: 10.1111/j.1525-1470.2011.01684.x. PMID: 22352996

Diagnosis

Simmons CL, Harper LK, Patel MC, Katabathina VS, Southard RN, Goncalves L, Tran E, Biyyam DR
Radiographics 2024 Mar;44(3):e230109. doi: 10.1148/rg.230109. PMID: 38358937
Nakamura N, Suzuki R, Takahashi Y, Uwamori A, Masuda M, Fukui T, Noda Y, Tsuta K, Naganuma M
Intern Med 2023 Dec 1;62(23):3483-3488. Epub 2023 Apr 21 doi: 10.2169/internalmedicine.1645-23. PMID: 37081684Free PMC Article
Nunes MM, da Costa AAS, Tavares TS, Aguiar MCF, Martins CC, Caldeira PC
J Oral Pathol Med 2023 Jul;52(6):468-475. Epub 2023 Feb 8 doi: 10.1111/jop.13411. PMID: 36715564
Askan G, Basturk O
Turk Patoloji Derg 2022;38(1):46-53. doi: 10.5146/tjpath.2022.01567. PMID: 35001360Free PMC Article
Agaimy A, Stoehr R, Hornung A, Popp J, Erdmann M, Heinzerling L, Hartmann A
Am J Surg Pathol 2021 Feb 1;45(2):240-254. doi: 10.1097/PAS.0000000000001645. PMID: 33428337

Therapy

Guérin F, Martelli H, Rogers T, Zanetti I, van Scheltinga ST, De Corti F, Burrieza GG, Minard-Colin V, Orbach D, van Noesel MM, Karanian M, Fajardo RD, Merks JHM, Ferrari A, Bisogno G
Pediatr Blood Cancer 2023 Jul;70(7):e30374. Epub 2023 Apr 21 doi: 10.1002/pbc.30374. PMID: 37083216
de Paula DS, Nóbrega Malta CE, de Brito WH, Mota Lemos JV, Cetira Fillho EL, Gurgel Costa FW, Nunes Alves APN, de Barros Silva PG
Int J Paediatr Dent 2021 Jul;31(4):504-519. Epub 2021 Mar 15 doi: 10.1111/ipd.12765. PMID: 33289182
Manzanares A, Restrepo-Perdomo CA, Botteri G, Castillo-Ecija H, Pascual-Pasto G, Cano F, Garcia-Alvarez L, Monterrubio C, Ruiz B, Vazquez-Carrera M, Suñol M, Mora J, Tornero JA, Sosnik A, Carcaboso AM
Adv Healthc Mater 2018 Aug;7(15):e1800255. Epub 2018 Jun 11 doi: 10.1002/adhm.201800255. PMID: 29892999
Gökdemir G, Ekmen S, Gungor S, Singer R
Pediatr Dermatol 2013 Jan-Feb;30(1):97-9. Epub 2012 Feb 22 doi: 10.1111/j.1525-1470.2011.01684.x. PMID: 22352996
Schneider U, Lomax A, Timmermann B
Radiother Oncol 2008 Nov;89(2):135-40. Epub 2008 Aug 15 doi: 10.1016/j.radonc.2008.07.017. PMID: 18707783

Prognosis

Nunes MM, da Costa AAS, Tavares TS, Aguiar MCF, Martins CC, Caldeira PC
J Oral Pathol Med 2023 Jul;52(6):468-475. Epub 2023 Feb 8 doi: 10.1111/jop.13411. PMID: 36715564
Guo Y, Hu B, Huang D, Wang X, Li J, Zhang D, Li X, Chen G, Ren D
BMC Surg 2021 Jan 30;21(1):66. doi: 10.1186/s12893-021-01073-x. PMID: 33516222Free PMC Article
Yao W, Schweitzer N, Biswal N, Polf J, Farr J, Vujaskovic Z
Acta Oncol 2020 Oct;59(10):1186-1192. Epub 2020 Jun 5 doi: 10.1080/0284186X.2020.1769859. PMID: 32500780
Liu LI, Ahn E, Studeman K, Campbell K, Lai J
Anticancer Res 2020 Apr;40(4):2225-2229. doi: 10.21873/anticanres.14184. PMID: 32234918
Gökdemir G, Ekmen S, Gungor S, Singer R
Pediatr Dermatol 2013 Jan-Feb;30(1):97-9. Epub 2012 Feb 22 doi: 10.1111/j.1525-1470.2011.01684.x. PMID: 22352996

Clinical prediction guides

de Paula DS, Nóbrega Malta CE, de Brito WH, Mota Lemos JV, Cetira Fillho EL, Gurgel Costa FW, Nunes Alves APN, de Barros Silva PG
Int J Paediatr Dent 2021 Jul;31(4):504-519. Epub 2021 Mar 15 doi: 10.1111/ipd.12765. PMID: 33289182
Mattos VD, Ferman S, Magalhães DMA, Antunes HS, Lourenço SQC
Oral Surg Oral Med Oral Pathol Oral Radiol 2019 Apr;127(4):272-281. Epub 2018 Dec 21 doi: 10.1016/j.oooo.2018.12.012. PMID: 30685390
Manzanares A, Restrepo-Perdomo CA, Botteri G, Castillo-Ecija H, Pascual-Pasto G, Cano F, Garcia-Alvarez L, Monterrubio C, Ruiz B, Vazquez-Carrera M, Suñol M, Mora J, Tornero JA, Sosnik A, Carcaboso AM
Adv Healthc Mater 2018 Aug;7(15):e1800255. Epub 2018 Jun 11 doi: 10.1002/adhm.201800255. PMID: 29892999
Mamlouk MD, Rosbe KW, Glastonbury CM
Clin Radiol 2015 Mar;70(3):270-7. Epub 2014 Dec 13 doi: 10.1016/j.crad.2014.11.009. PMID: 25515793
Fuchs J, Dantonello TM, Blumenstock G, Kosztyla D, Klingebiel T, Leuschner I, Schuck A, Niggli FK, Koscielniak E, Seitz G
Ann Surg 2014 Jun;259(6):1166-72. doi: 10.1097/SLA.0b013e3182a6f320. PMID: 24045440

Recent systematic reviews

de Paula DS, Nóbrega Malta CE, de Brito WH, Mota Lemos JV, Cetira Fillho EL, Gurgel Costa FW, Nunes Alves APN, de Barros Silva PG
Int J Paediatr Dent 2021 Jul;31(4):504-519. Epub 2021 Mar 15 doi: 10.1111/ipd.12765. PMID: 33289182

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