Full Report

Format

Full Report
Summary (Text)
Summary (XML)

Send to:

Choose Destination

File
Clipboard
Collections

Digestive System Rhabdomyosarcoma

MedGen UID:: 1752521
•Concept ID:: C5419974
•: Neoplastic Process

Definition

A rhabdomyosarcoma arising from an anatomic site in the digestive system. [from NCI]

Term Hierarchy

GTR
MeSH

CClinical test, RResearch test, OOMIM, GGeneReviews, VClinVar

CROGVDigestive System Rhabdomyosarcoma

Disease
- Disorder by Site
  - Disorder of gastrointestinal tract
    - Neoplasm of the gastrointestinal tract
      - Digestive System Soft Tissue Neoplasm
        Digestive System Sarcoma
        Digestive System Rhabdomyosarcoma
        Anus rhabdomyosarcoma
        Esophageal Rhabdomyosarcoma
        Extrahepatic bile duct rhabdomyosarcoma
        Embryonal extrahepatic bile duct rhabdomyosarcoma
        Gallbladder rhabdomyosarcoma
        Liver rhabdomyosarcoma
        Rectum rhabdomyosarcoma

Professional guidelines

PubMed

Dedifferentiated and Undifferentiated Melanomas: Report of 35 New Cases With Literature Review and Proposal of Diagnostic Criteria.

Agaimy A, Stoehr R, Hornung A, Popp J, Erdmann M, Heinzerling L, Hartmann A
Am J Surg Pathol 2021 Feb 1;45(2):240-254. doi: 10.1097/PAS.0000000000001645. PMID: 33428337

Treatment and outcome of the patients with rhabdomyosarcoma of the biliary tree: Experience of the Cooperative Weichteilsarkom Studiengruppe (CWS).

Urla C, Warmann SW, Sparber-Sauer M, Schuck A, Leuschner I, Klingebiel T, Blumenstock G, Seitz G, Koscielniak E, Fuchs J
BMC Cancer 2019 Oct 14;19(1):945. doi: 10.1186/s12885-019-6172-5. PMID: 31610788 Free PMC Article

Ultrasonography and computed tomography for diagnosis and follow-up of biliary duct rhabdomyosarcomas in children.

Geoffray A, Couanet D, Montagne JP, Leclère J, Flamant F
Pediatr Radiol 1987;17(2):127-31. doi: 10.1007/BF02388089. PMID: 3550663

See all (8)

Recent clinical studies

Etiology

Primitive neuroectodermal tumor in a child with Currarino syndrome.

Çebi MN, Yılmaz G, Çelikdemir G, Özcan R, Ocak S, Celkan TT, Çomunoğlu N
Turk J Pediatr 2022;64(2):385-388. doi: 10.24953/turkjped.2021.264. PMID: 35611429

Perianal and perineal rhabdomyosarcomas: a retrospective multicenter study of 35 cases.

Guo Y, Hu B, Huang D, Wang X, Li J, Zhang D, Li X, Chen G, Ren D
BMC Surg 2021 Jan 30;21(1):66. doi: 10.1186/s12893-021-01073-x. PMID: 33516222 Free PMC Article

Dedifferentiated and Undifferentiated Melanomas: Report of 35 New Cases With Literature Review and Proposal of Diagnostic Criteria.

Agaimy A, Stoehr R, Hornung A, Popp J, Erdmann M, Heinzerling L, Hartmann A
Am J Surg Pathol 2021 Feb 1;45(2):240-254. doi: 10.1097/PAS.0000000000001645. PMID: 33428337

Treatment and outcome of patients suffering from perineal/perianal rhabdomyosarcoma: results from the CWS trials--retrospective clinical study.

Fuchs J, Dantonello TM, Blumenstock G, Kosztyla D, Klingebiel T, Leuschner I, Schuck A, Niggli FK, Koscielniak E, Seitz G
Ann Surg 2014 Jun;259(6):1166-72. doi: 10.1097/SLA.0b013e3182a6f320. PMID: 24045440

Perianal rhabdomyosarcoma: report of a case in an infant and review of the literature.

Gökdemir G, Ekmen S, Gungor S, Singer R
Pediatr Dermatol 2013 Jan-Feb;30(1):97-9. Epub 2012 Feb 22 doi: 10.1111/j.1525-1470.2011.01684.x. PMID: 22352996

See all (59)

Diagnosis

Rhabdomyosarcoma of the oral cavity in children aged 0-2 years: A scoping review.

Nunes MM, da Costa AAS, Tavares TS, Aguiar MCF, Martins CC, Caldeira PC
J Oral Pathol Med 2023 Jul;52(6):468-475. Epub 2023 Feb 8 doi: 10.1111/jop.13411. PMID: 36715564

Mesenchymal Tumors Involving the Pancreas: A Clinicopathologic Analysis and Review of the Literature.

Askan G, Basturk O
Turk Patoloji Derg 2022;38(1):46-53. doi: 10.5146/tjpath.2022.01567. PMID: 35001360 Free PMC Article

Dedifferentiated and Undifferentiated Melanomas: Report of 35 New Cases With Literature Review and Proposal of Diagnostic Criteria.

Agaimy A, Stoehr R, Hornung A, Popp J, Erdmann M, Heinzerling L, Hartmann A
Am J Surg Pathol 2021 Feb 1;45(2):240-254. doi: 10.1097/PAS.0000000000001645. PMID: 33428337

Pleomorphic rhabdomyosarcoma of the liver with a hepatic cyst in an adult: Case report and literature review.

Yin J, Liu Z, Yang K
Medicine (Baltimore) 2018 Jul;97(29):e11335. doi: 10.1097/MD.0000000000011335. PMID: 30024506 Free PMC Article

Pancreatic rhabdomyosarcoma.

Yasuda I, Adachi S, Kasahara S, Asano T, Shirakami Y, Kato T, Shimokawa K, Moriwaki H
Gastrointest Endosc 2004 Sep;60(3):433-4. doi: 10.1016/s0016-5107(04)01705-5. PMID: 15332041

See all (99)

Therapy

Prevalence of malignant neoplastic oral lesions among children and adolescents: A systematic review and meta-analysis.

de Paula DS, Nóbrega Malta CE, de Brito WH, Mota Lemos JV, Cetira Fillho EL, Gurgel Costa FW, Nunes Alves APN, de Barros Silva PG
Int J Paediatr Dent 2021 Jul;31(4):504-519. Epub 2021 Mar 15 doi: 10.1111/ipd.12765. PMID: 33289182

Tissue Compatibility of SN-38-Loaded Anticancer Nanofiber Matrices.

Manzanares A, Restrepo-Perdomo CA, Botteri G, Castillo-Ecija H, Pascual-Pasto G, Cano F, Garcia-Alvarez L, Monterrubio C, Ruiz B, Vazquez-Carrera M, Suñol M, Mora J, Tornero JA, Sosnik A, Carcaboso AM
Adv Healthc Mater 2018 Aug;7(15):e1800255. Epub 2018 Jun 11 doi: 10.1002/adhm.201800255. PMID: 29892999

Treatment and outcome of patients suffering from perineal/perianal rhabdomyosarcoma: results from the CWS trials--retrospective clinical study.

Perianal rhabdomyosarcoma: report of a case in an infant and review of the literature.

Gökdemir G, Ekmen S, Gungor S, Singer R
Pediatr Dermatol 2013 Jan-Feb;30(1):97-9. Epub 2012 Feb 22 doi: 10.1111/j.1525-1470.2011.01684.x. PMID: 22352996

Second cancers in children treated with modern radiotherapy techniques.

Schneider U, Lomax A, Timmermann B
Radiother Oncol 2008 Nov;89(2):135-40. Epub 2008 Aug 15 doi: 10.1016/j.radonc.2008.07.017. PMID: 18707783

See all (50)

Prognosis

Rhabdomyosarcoma of the oral cavity in children aged 0-2 years: A scoping review.

Nunes MM, da Costa AAS, Tavares TS, Aguiar MCF, Martins CC, Caldeira PC
J Oral Pathol Med 2023 Jul;52(6):468-475. Epub 2023 Feb 8 doi: 10.1111/jop.13411. PMID: 36715564

Perianal and perineal rhabdomyosarcomas: a retrospective multicenter study of 35 cases.

Guo Y, Hu B, Huang D, Wang X, Li J, Zhang D, Li X, Chen G, Ren D
BMC Surg 2021 Jan 30;21(1):66. doi: 10.1186/s12893-021-01073-x. PMID: 33516222 Free PMC Article

Primary Hepatic Carcinosarcoma Composed of Hepatocellular Carcinoma, Cholangiocarcinoma, Osteosarcoma and Rhabdomyosarcoma With Poor Prognosis.

Liu LI, Ahn E, Studeman K, Campbell K, Lai J
Anticancer Res 2020 Apr;40(4):2225-2229. doi: 10.21873/anticanres.14184. PMID: 32234918

Pleomorphic rhabdomyosarcoma of the liver with a hepatic cyst in an adult: Case report and literature review.

Yin J, Liu Z, Yang K
Medicine (Baltimore) 2018 Jul;97(29):e11335. doi: 10.1097/MD.0000000000011335. PMID: 30024506 Free PMC Article

Perianal rhabdomyosarcoma: report of a case in an infant and review of the literature.

Gökdemir G, Ekmen S, Gungor S, Singer R
Pediatr Dermatol 2013 Jan-Feb;30(1):97-9. Epub 2012 Feb 22 doi: 10.1111/j.1525-1470.2011.01684.x. PMID: 22352996

See all (57)

Clinical prediction guides

Prevalence of malignant neoplastic oral lesions among children and adolescents: A systematic review and meta-analysis.

Dental and craniofacial alterations in long-term survivors of childhood head and neck rhabdomyosarcoma.

Mattos VD, Ferman S, Magalhães DMA, Antunes HS, Lourenço SQC
Oral Surg Oral Med Oral Pathol Oral Radiol 2019 Apr;127(4):272-281. Epub 2018 Dec 21 doi: 10.1016/j.oooo.2018.12.012. PMID: 30685390

Tissue Compatibility of SN-38-Loaded Anticancer Nanofiber Matrices.

Paediatric parotid neoplasms: a 10 year retrospective imaging and pathology review of these rare tumours.

Mamlouk MD, Rosbe KW, Glastonbury CM
Clin Radiol 2015 Mar;70(3):270-7. Epub 2014 Dec 13 doi: 10.1016/j.crad.2014.11.009. PMID: 25515793

Treatment and outcome of patients suffering from perineal/perianal rhabdomyosarcoma: results from the CWS trials--retrospective clinical study.

See all (27)