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Retroperitoneal Undifferentiated Pleomorphic Sarcoma

MedGen UID:
1770865
Concept ID:
C5421312
Neoplastic Process

Definition

A rare undifferentiated pleomorphic sarcoma that arises from the retroperitoneum. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVRetroperitoneal Undifferentiated Pleomorphic Sarcoma

Professional guidelines

PubMed

Rutkowski PL, Mullen JT
J Surg Oncol 2018 Jan;117(1):79-86. Epub 2017 Nov 11 doi: 10.1002/jso.24893. PMID: 29127695
Trans-Atlantic RPS Working Group
Ann Surg Oncol 2016 Oct;23(11):3531-3540. Epub 2016 Aug 1 doi: 10.1245/s10434-016-5336-7. PMID: 27480354Free PMC Article
Shiraev T, Pasricha SS, Choong P, Schlicht S, van Rijswijk CS, Dimmick S, Stuckey S, Anderson SE
J Med Imaging Radiat Oncol 2013 Dec;57(6):687-700. Epub 2013 Oct 7 doi: 10.1111/1754-9485.12123. PMID: 24118833

Recent clinical studies

Etiology

Tseng WW, Swallow CJ, Strauss DC, Bonvalot S, Rutkowski P, Ford SJ, Gonzalez RJ, Gladdy RA, Gyorki DE, Fairweather M, Lee KW, Albertsmeier M, van Houdt WJ, Fau M, Nessim C, Grignani G, Cardona K, Quagliuolo V, Grignol V, Farma JM, Pennacchioli E, Fiore M, Hayes A, Tzanis D, Skoczylas J, Almond ML, Mullinax JE, Johnston W, Snow H, Haas RL, Callegaro D, Smith MJ, Bouhadiba T, Desai A, Voss R, Sanfilippo R, Jones RL, Baldini EH, Wagner AJ, Catton CN, Stacchiotti S, Thway K, Roland CL, Raut CP, Gronchi A; Transatlantic Australasian Retroperitoneal Sarcoma Working Group
Ann Surg Oncol 2022 Nov;29(12):7335-7348. Epub 2022 Jun 29 doi: 10.1245/s10434-022-11864-y. PMID: 35767103
Pham V, Henderson-Jackson E, Doepker MP, Caracciolo JT, Gonzalez RJ, Druta M, Ding Y, Bui MM
Cancer Control 2016 Jul;23(3):249-64. doi: 10.1177/107327481602300308. PMID: 27556665
Tuan J, Vitolo V, Vischioni B, Iannalfi A, Fiore MR, Fossati P, Orecchia R
Radiol Med 2014 Oct;119(10):790-802. Epub 2014 Mar 18 doi: 10.1007/s11547-013-0350-3. PMID: 24638910
Eilber FC, Eilber KS, Eilber FR
Curr Treat Options Oncol 2000 Aug;1(3):274-8. doi: 10.1007/s11864-000-0040-y. PMID: 12057171
Weiss SW
Monogr Pathol 1996;38:207-39. PMID: 8744279

Diagnosis

Thway K
Semin Diagn Pathol 2019 Mar;36(2):112-121. Epub 2019 Feb 28 doi: 10.1053/j.semdp.2019.02.006. PMID: 30852045
Pham V, Henderson-Jackson E, Doepker MP, Caracciolo JT, Gonzalez RJ, Druta M, Ding Y, Bui MM
Cancer Control 2016 Jul;23(3):249-64. doi: 10.1177/107327481602300308. PMID: 27556665
Tuan J, Vitolo V, Vischioni B, Iannalfi A, Fiore MR, Fossati P, Orecchia R
Radiol Med 2014 Oct;119(10):790-802. Epub 2014 Mar 18 doi: 10.1007/s11547-013-0350-3. PMID: 24638910
Eilber FC, Eilber KS, Eilber FR
Curr Treat Options Oncol 2000 Aug;1(3):274-8. doi: 10.1007/s11864-000-0040-y. PMID: 12057171
Weiss SW
Monogr Pathol 1996;38:207-39. PMID: 8744279

Therapy

Roland CL, Nassif Haddad EF, Keung EZ, Wang WL, Lazar AJ, Lin H, Chelvanambi M, Parra ER, Wani K, Guadagnolo BA, Bishop AJ, Burton EM, Hunt KK, Torres KE, Feig BW, Scally CP, Lewis VO, Bird JE, Ratan R, Araujo D, Zarzour MA, Patel S, Benjamin R, Conley AP, Livingston JA, Ravi V, Tawbi HA, Lin PP, Moon BS, Satcher RL, Mujtaba B, Witt RG, Traweek RS, Cope B, Lazcano R, Wu CC, Zhou X, Mohammad MM, Chu RA, Zhang J, Damania A, Sahasrabhojane P, Tate T, Callahan K, Nguyen S, Ingram D, Morey R, Crosby S, Mathew G, Duncan S, Lima CF, Blay JY, Fridman WH, Shaw K, Wistuba I, Futreal A, Ajami N, Wargo JA, Somaiah N
Nat Cancer 2024 Apr;5(4):625-641. Epub 2024 Feb 13 doi: 10.1038/s43018-024-00726-z. PMID: 38351182
Keung EZ, Lazar AJ, Torres KE, Wang WL, Cormier JN, Ashleigh Guadagnolo B, Bishop AJ, Lin H, Hunt KK, Bird J, Lewis VO, Patel SR, Wargo JA, Somaiah N, Roland CL
BMC Cancer 2018 Sep 24;18(1):913. doi: 10.1186/s12885-018-4829-0. PMID: 30249211Free PMC Article
Tuan J, Vitolo V, Vischioni B, Iannalfi A, Fiore MR, Fossati P, Orecchia R
Radiol Med 2014 Oct;119(10):790-802. Epub 2014 Mar 18 doi: 10.1007/s11547-013-0350-3. PMID: 24638910
Eilber FC, Eilber KS, Eilber FR
Curr Treat Options Oncol 2000 Aug;1(3):274-8. doi: 10.1007/s11864-000-0040-y. PMID: 12057171
Catton CN, O'Sullivan B, Kotwall C, Cummings B, Hao Y, Fornasier V
Int J Radiat Oncol Biol Phys 1994 Jul 30;29(5):1005-10. doi: 10.1016/0360-3016(94)90395-6. PMID: 8083069

Prognosis

Tseng WW, Swallow CJ, Strauss DC, Bonvalot S, Rutkowski P, Ford SJ, Gonzalez RJ, Gladdy RA, Gyorki DE, Fairweather M, Lee KW, Albertsmeier M, van Houdt WJ, Fau M, Nessim C, Grignani G, Cardona K, Quagliuolo V, Grignol V, Farma JM, Pennacchioli E, Fiore M, Hayes A, Tzanis D, Skoczylas J, Almond ML, Mullinax JE, Johnston W, Snow H, Haas RL, Callegaro D, Smith MJ, Bouhadiba T, Desai A, Voss R, Sanfilippo R, Jones RL, Baldini EH, Wagner AJ, Catton CN, Stacchiotti S, Thway K, Roland CL, Raut CP, Gronchi A; Transatlantic Australasian Retroperitoneal Sarcoma Working Group
Ann Surg Oncol 2022 Nov;29(12):7335-7348. Epub 2022 Jun 29 doi: 10.1245/s10434-022-11864-y. PMID: 35767103
Thway K, Jones RL, Noujaim J, Zaidi S, Miah AB, Fisher C
Adv Anat Pathol 2016 Jan;23(1):30-40. doi: 10.1097/PAP.0000000000000101. PMID: 26645460
Tuan J, Vitolo V, Vischioni B, Iannalfi A, Fiore MR, Fossati P, Orecchia R
Radiol Med 2014 Oct;119(10):790-802. Epub 2014 Mar 18 doi: 10.1007/s11547-013-0350-3. PMID: 24638910
Eilber FC, Eilber KS, Eilber FR
Curr Treat Options Oncol 2000 Aug;1(3):274-8. doi: 10.1007/s11864-000-0040-y. PMID: 12057171
Weiss SW
Monogr Pathol 1996;38:207-39. PMID: 8744279

Clinical prediction guides

Tseng WW, Swallow CJ, Strauss DC, Bonvalot S, Rutkowski P, Ford SJ, Gonzalez RJ, Gladdy RA, Gyorki DE, Fairweather M, Lee KW, Albertsmeier M, van Houdt WJ, Fau M, Nessim C, Grignani G, Cardona K, Quagliuolo V, Grignol V, Farma JM, Pennacchioli E, Fiore M, Hayes A, Tzanis D, Skoczylas J, Almond ML, Mullinax JE, Johnston W, Snow H, Haas RL, Callegaro D, Smith MJ, Bouhadiba T, Desai A, Voss R, Sanfilippo R, Jones RL, Baldini EH, Wagner AJ, Catton CN, Stacchiotti S, Thway K, Roland CL, Raut CP, Gronchi A; Transatlantic Australasian Retroperitoneal Sarcoma Working Group
Ann Surg Oncol 2022 Nov;29(12):7335-7348. Epub 2022 Jun 29 doi: 10.1245/s10434-022-11864-y. PMID: 35767103
Villacis RA, Silveira SM, Barros-Filho MC, Marchi FA, Domingues MA, Scapulatempo-Neto C, Aguiar S Jr, Lopes A, Cunha IW, Rogatto SR
PLoS One 2014;9(7):e102281. Epub 2014 Jul 16 doi: 10.1371/journal.pone.0102281. PMID: 25028927Free PMC Article
Tschoep K, Kohlmann A, Schlemmer M, Haferlach T, Issels RD
Crit Rev Oncol Hematol 2007 Aug;63(2):111-24. Epub 2007 Jun 6 doi: 10.1016/j.critrevonc.2007.04.001. PMID: 17555981
Perez EA, Gutierrez JC, Moffat FL Jr, Franceschi D, Livingstone AS, Spector SA, Levi JU, Sleeman D, Koniaris LG
Ann Surg Oncol 2007 Mar;14(3):1114-22. Epub 2007 Jan 7 doi: 10.1245/s10434-006-9255-x. PMID: 17206483
Catton CN, O'Sullivan B, Kotwall C, Cummings B, Hao Y, Fornasier V
Int J Radiat Oncol Biol Phys 1994 Jul 30;29(5):1005-10. doi: 10.1016/0360-3016(94)90395-6. PMID: 8083069

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