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Secondary Peripheral Chondrosarcoma, Grade 2

MedGen UID:
1791521
Concept ID:
C5555080
Neoplastic Process

Definition

An intermediate-grade chondrosarcoma arising within the cartilaginous cap of a pre-existing osteochondroma. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVSecondary Peripheral Chondrosarcoma, Grade 2

Professional guidelines

PubMed

Deloin X, Dumaine V, Biau D, Karoubi M, Babinet A, Tomeno B, Anract P
Orthop Traumatol Surg Res 2009 Oct;95(6):393-401. Epub 2009 Oct 3 doi: 10.1016/j.otsr.2009.05.004. PMID: 19801212

Recent clinical studies

Etiology

Gnoli M, Gambarotti M, Righi A, Staals EL, Evangelista A, Tremosini M, Brizola E, Mordenti M, Boarini M, Locatelli M, Pedrini E, Sangiorgi L
Orphanet J Rare Dis 2024 Feb 13;19(1):63. doi: 10.1186/s13023-023-03006-8. PMID: 38351015Free PMC Article
Tsuda Y, Evans S, Stevenson JD, Parry M, Fujiwara T, Laitinen M, Outani H, Jeys L
Clin Orthop Relat Res 2019 Nov;477(11):2432-2440. doi: 10.1097/CORR.0000000000000926. PMID: 31453886Free PMC Article
Gambarotti M, Righi A, Picci P, Bertoni F, Manfrini M, Donati DM, Dei Tos AP, Vanel D
Histopathology 2016 Jun;68(7):1073-8. Epub 2015 Nov 25 doi: 10.1111/his.12881. PMID: 26408960
Goud AL, Wuyts W, Bessems J, Bramer J, van der Woude HJ, Ham J
J Bone Joint Surg Am 2015 Jan 7;97(1):24-31. doi: 10.2106/JBJS.N.00121. PMID: 25568391
Deloin X, Dumaine V, Biau D, Karoubi M, Babinet A, Tomeno B, Anract P
Orthop Traumatol Surg Res 2009 Oct;95(6):393-401. Epub 2009 Oct 3 doi: 10.1016/j.otsr.2009.05.004. PMID: 19801212

Diagnosis

Gnoli M, Gambarotti M, Righi A, Staals EL, Evangelista A, Tremosini M, Brizola E, Mordenti M, Boarini M, Locatelli M, Pedrini E, Sangiorgi L
Orphanet J Rare Dis 2024 Feb 13;19(1):63. doi: 10.1186/s13023-023-03006-8. PMID: 38351015Free PMC Article
Abdulfatah E, Rottmann D, Morag Y, Pantanowitz L, Udager AM, Hao W, Lucas DR
Hum Pathol 2023 Jun;136:63-74. Epub 2023 Apr 3 doi: 10.1016/j.humpath.2023.03.011. PMID: 37019410
Gambarotti M, Righi A, Picci P, Bertoni F, Manfrini M, Donati DM, Dei Tos AP, Vanel D
Histopathology 2016 Jun;68(7):1073-8. Epub 2015 Nov 25 doi: 10.1111/his.12881. PMID: 26408960
Hameetman L, Kok P, Eilers PH, Cleton-Jansen AM, Hogendoorn PC, Bovée JV
Virchows Arch 2005 Apr;446(4):430-7. Epub 2005 Mar 3 doi: 10.1007/s00428-005-1208-4. PMID: 15744499
Rozeman LB, Hogendoorn PC, Bovée JV
Expert Rev Mol Diagn 2002 Sep;2(5):461-72. doi: 10.1586/14737159.2.5.461. PMID: 12271817

Therapy

Dickson MA, Mahoney MR, Tap WD, D'Angelo SP, Keohan ML, Van Tine BA, Agulnik M, Horvath LE, Nair JS, Schwartz GK
Ann Oncol 2016 Oct;27(10):1855-60. Epub 2016 Aug 8 doi: 10.1093/annonc/mdw281. PMID: 27502708Free PMC Article

Prognosis

Gnoli M, Gambarotti M, Righi A, Staals EL, Evangelista A, Tremosini M, Brizola E, Mordenti M, Boarini M, Locatelli M, Pedrini E, Sangiorgi L
Orphanet J Rare Dis 2024 Feb 13;19(1):63. doi: 10.1186/s13023-023-03006-8. PMID: 38351015Free PMC Article
Thorkildsen J, Taksdal I, Bjerkehagen B, Haugland HK, Børge Johannesen T, Viset T, Norum OJ, Bruland Ø, Zaikova O
Acta Oncol 2019 Mar;58(3):273-282. Epub 2019 Jan 11 doi: 10.1080/0284186X.2018.1554260. PMID: 30632866
Gambarotti M, Righi A, Picci P, Bertoni F, Manfrini M, Donati DM, Dei Tos AP, Vanel D
Histopathology 2016 Jun;68(7):1073-8. Epub 2015 Nov 25 doi: 10.1111/his.12881. PMID: 26408960
Hameetman L, Kok P, Eilers PH, Cleton-Jansen AM, Hogendoorn PC, Bovée JV
Virchows Arch 2005 Apr;446(4):430-7. Epub 2005 Mar 3 doi: 10.1007/s00428-005-1208-4. PMID: 15744499
Rozeman LB, Hogendoorn PC, Bovée JV
Expert Rev Mol Diagn 2002 Sep;2(5):461-72. doi: 10.1586/14737159.2.5.461. PMID: 12271817

Clinical prediction guides

McLoughlin E, Davies AM, Iqbal A, James SL, Botchu R
Clin Radiol 2020 May;75(5):395.e7-395.e16. Epub 2019 Dec 31 doi: 10.1016/j.crad.2019.11.017. PMID: 31898960
Thorkildsen J, Taksdal I, Bjerkehagen B, Haugland HK, Børge Johannesen T, Viset T, Norum OJ, Bruland Ø, Zaikova O
Acta Oncol 2019 Mar;58(3):273-282. Epub 2019 Jan 11 doi: 10.1080/0284186X.2018.1554260. PMID: 30632866
Franchi A, Baroni G, Sardi I, Giunti L, Capanna R, Campanacci D
Virchows Arch 2012 Mar;460(3):335-42. Epub 2012 Feb 16 doi: 10.1007/s00428-012-1206-2. PMID: 22350005
Hameetman L, Kok P, Eilers PH, Cleton-Jansen AM, Hogendoorn PC, Bovée JV
Virchows Arch 2005 Apr;446(4):430-7. Epub 2005 Mar 3 doi: 10.1007/s00428-005-1208-4. PMID: 15744499
Rozeman LB, Hogendoorn PC, Bovée JV
Expert Rev Mol Diagn 2002 Sep;2(5):461-72. doi: 10.1586/14737159.2.5.461. PMID: 12271817

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