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Major Salivary Gland Acinic Cell Carcinoma

MedGen UID:
233138
Concept ID:
C1334546
Neoplastic Process
Synonyms: Acinic Cell Adenocarcinoma of Major Salivary Gland; Acinic Cell Adenocarcinoma of the Major Salivary Gland; Acinic Cell Carcinoma of Major Salivary Gland; Acinic Cell Carcinoma of the Major Salivary Gland; Major Salivary Gland Acinic Cell Adenocarcinoma

Definition

An adenocarcinoma with serous acinar cell differentiation that arises from the major salivary glands. The vast majority of cases occur in the parotid gland. Patients usually present with a slow growing mass in the parotid area. [from NCI]

Professional guidelines

PubMed

Pang Y, Sun L, Liu H, Ma J
Oral Oncol 2021 Aug;119:105370. Epub 2021 Jun 19 doi: 10.1016/j.oraloncology.2021.105370. PMID: 34157553
Ferrell JK, Mace JC, Clayburgh D
Eur Arch Otorhinolaryngol 2019 Apr;276(4):1135-1146. Epub 2019 Jan 16 doi: 10.1007/s00405-019-05282-2. PMID: 30649610
Nagliati M, Bolner A, Vanoni V, Tomio L, Lay G, Murtas R, Deidda MA, Madeddu A, Delmastro E, Verna R, Gabriele P, Amichetti M
Tumori 2009 Jul-Aug;95(4):442-8. doi: 10.1177/030089160909500406. PMID: 19856654

Recent clinical studies

Etiology

De Luca P, de Campora L, Tassone D, Atturo F, Colangeli R, Petruzzi G, Fermi M, Molinari G, Abeshi A, Cintoli G, Lo Manto A, Togo G, Ricciardiello F, Condorelli P, Raso F, Di Stadio A, Salzano G, Esposito E, D'Ecclesia A, Radici M, Iemma M, Vigili MG, Salzano FA, Magaldi L, Cassano M, Dallan I, Pellini R, Presutti L, Ionna F, de Campora E, Camaioni A
Eur Arch Otorhinolaryngol 2022 Dec;279(12):5821-5829. Epub 2022 Jun 9 doi: 10.1007/s00405-022-07481-w. PMID: 35678874Free PMC Article
Dublin JC, Oliver JR, Tam MM, Persky MJ, Jacobson AS, Liu C, Hu KS, Vaezi AE, Morris LGT, Givi B
Otolaryngol Head Neck Surg 2022 Dec;167(6):941-951. Epub 2022 Mar 8 doi: 10.1177/01945998221083094. PMID: 35259039
Sideris A, Rao A, Maher N, Parker A, Crawford J, Smee R, Jacobson I, Gallagher R
ANZ J Surg 2021 Jun;91(6):1233-1239. Epub 2020 Nov 17 doi: 10.1111/ans.16421. PMID: 33205582
Ayre G, Hyrcza M, Wu J, Berthelet E, Skálová A, Thomson T
Head Neck 2019 May;41(5):1227-1236. Epub 2018 Dec 28 doi: 10.1002/hed.25536. PMID: 30592355
Son E, Panwar A, Mosher CH, Lydiatt D
J Oncol Pract 2018 Feb;14(2):99-108. doi: 10.1200/JOP.2017.026856. PMID: 29436307

Diagnosis

Pang Y, Sun L, Liu H, Ma J
Oral Oncol 2021 Aug;119:105370. Epub 2021 Jun 19 doi: 10.1016/j.oraloncology.2021.105370. PMID: 34157553
Kirschnick LB, Silveira FM, Schuch LF, Fonseca FP, Martins MAT, Lopes MA, Santos-Silva AR, Carrard VC, Dos Santos JN, Vargas PA, Wagner VP, Martins MD
J Oral Pathol Med 2021 Sep;50(8):741-749. Epub 2021 Feb 18 doi: 10.1111/jop.13159. PMID: 33455041
Ayre G, Hyrcza M, Wu J, Berthelet E, Skálová A, Thomson T
Head Neck 2019 May;41(5):1227-1236. Epub 2018 Dec 28 doi: 10.1002/hed.25536. PMID: 30592355
Son E, Panwar A, Mosher CH, Lydiatt D
J Oncol Pract 2018 Feb;14(2):99-108. doi: 10.1200/JOP.2017.026856. PMID: 29436307
Vander Poorten V, Triantafyllou A, Thompson LD, Bishop J, Hauben E, Hunt J, Skalova A, Stenman G, Takes RP, Gnepp DR, Hellquist H, Wenig B, Bell D, Rinaldo A, Ferlito A
Eur Arch Otorhinolaryngol 2016 Nov;273(11):3511-3531. Epub 2015 Dec 19 doi: 10.1007/s00405-015-3855-7. PMID: 26685679

Therapy

Warner BM, Baer AN, Lipson EJ, Allen C, Hinrichs C, Rajan A, Pelayo E, Beach M, Gulley JL, Madan RA, Feliciano J, Grisius M, Long L, Powers A, Kleiner DE, Cappelli L, Alevizos I
Oncologist 2019 Sep;24(9):1259-1269. Epub 2019 Apr 17 doi: 10.1634/theoncologist.2018-0823. PMID: 30996010Free PMC Article
Cheuk DK, Shek TW, Chan GC, Lau YL, Ha SY, Chiang AK
Pediatr Blood Cancer 2008 Mar;50(3):636-9. doi: 10.1002/pbc.21002. PMID: 16865683
Yamamoto T, Staples J, Wataha J, Lewis J, Lockwood P, Schoenlein P, Rao S, Osaki T, Dickinson D, Kamatani T, Schuster G, Hsu S
Anticancer Res 2004 Sep-Oct;24(5A):3065-73. PMID: 15517917

Prognosis

De Luca P, de Campora L, Tassone D, Atturo F, Colangeli R, Petruzzi G, Fermi M, Molinari G, Abeshi A, Cintoli G, Lo Manto A, Togo G, Ricciardiello F, Condorelli P, Raso F, Di Stadio A, Salzano G, Esposito E, D'Ecclesia A, Radici M, Iemma M, Vigili MG, Salzano FA, Magaldi L, Cassano M, Dallan I, Pellini R, Presutti L, Ionna F, de Campora E, Camaioni A
Eur Arch Otorhinolaryngol 2022 Dec;279(12):5821-5829. Epub 2022 Jun 9 doi: 10.1007/s00405-022-07481-w. PMID: 35678874Free PMC Article
Kirschnick LB, Silveira FM, Schuch LF, Fonseca FP, Martins MAT, Lopes MA, Santos-Silva AR, Carrard VC, Dos Santos JN, Vargas PA, Wagner VP, Martins MD
J Oral Pathol Med 2021 Sep;50(8):741-749. Epub 2021 Feb 18 doi: 10.1111/jop.13159. PMID: 33455041
Ayre G, Hyrcza M, Wu J, Berthelet E, Skálová A, Thomson T
Head Neck 2019 May;41(5):1227-1236. Epub 2018 Dec 28 doi: 10.1002/hed.25536. PMID: 30592355
Vander Poorten V, Triantafyllou A, Thompson LD, Bishop J, Hauben E, Hunt J, Skalova A, Stenman G, Takes RP, Gnepp DR, Hellquist H, Wenig B, Bell D, Rinaldo A, Ferlito A
Eur Arch Otorhinolaryngol 2016 Nov;273(11):3511-3531. Epub 2015 Dec 19 doi: 10.1007/s00405-015-3855-7. PMID: 26685679
Yoshida EJ, García J, Eisele DW, Chen AM
Int J Pediatr Otorhinolaryngol 2014 Feb;78(2):174-8. Epub 2013 Nov 19 doi: 10.1016/j.ijporl.2013.11.001. PMID: 24332197

Clinical prediction guides

De Luca P, de Campora L, Tassone D, Atturo F, Colangeli R, Petruzzi G, Fermi M, Molinari G, Abeshi A, Cintoli G, Lo Manto A, Togo G, Ricciardiello F, Condorelli P, Raso F, Di Stadio A, Salzano G, Esposito E, D'Ecclesia A, Radici M, Iemma M, Vigili MG, Salzano FA, Magaldi L, Cassano M, Dallan I, Pellini R, Presutti L, Ionna F, de Campora E, Camaioni A
Eur Arch Otorhinolaryngol 2022 Dec;279(12):5821-5829. Epub 2022 Jun 9 doi: 10.1007/s00405-022-07481-w. PMID: 35678874Free PMC Article
Ding A, Zuo J, Lv H, Zhou L, Ding S, Yu Q, Xiong P
Oral Dis 2022 Oct;28(7):1861-1870. Epub 2021 Nov 26 doi: 10.1111/odi.14080. PMID: 34773340
Shinmura K, Kusafuka K, Kawasaki H, Kato H, Hariyama T, Tsuchiya K, Kawanishi Y, Funai K, Misawa K, Mineta H, Sugimura H
J Pathol 2021 Aug;254(5):519-530. Epub 2021 May 29 doi: 10.1002/path.5688. PMID: 33931860
Fang Q, Wu J, Du W, Zhang X
BMC Cancer 2019 May 21;19(1):475. doi: 10.1186/s12885-019-5711-4. PMID: 31113416Free PMC Article
Yoshida EJ, García J, Eisele DW, Chen AM
Int J Pediatr Otorhinolaryngol 2014 Feb;78(2):174-8. Epub 2013 Nov 19 doi: 10.1016/j.ijporl.2013.11.001. PMID: 24332197

Recent systematic reviews

Kirschnick LB, Silveira FM, Schuch LF, Fonseca FP, Martins MAT, Lopes MA, Santos-Silva AR, Carrard VC, Dos Santos JN, Vargas PA, Wagner VP, Martins MD
J Oral Pathol Med 2021 Sep;50(8):741-749. Epub 2021 Feb 18 doi: 10.1111/jop.13159. PMID: 33455041

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