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Classic congenital mesoblastic nephroma

MedGen UID:
273923
Concept ID:
C1516475
Neoplastic Process
Synonyms: Classic Congenital Mesoblastic Nephroma; classic congenital mesoblastic nephroma; Classic Mesoblastic Nephroma
 
Monarch Initiative: MONDO:0004455

Definition

A congenital mesoblastic nephroma characterized by the presence of interlacing fascicles of fibroblastic cells, low mitotic activity, and collagen formation. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVClassic congenital mesoblastic nephroma

Professional guidelines

PubMed

Chen YX, Huang C, He QM, Wang Z, Huang L, Wang HY, Mei SS, Chai CW, Zhang GL, Zhong W, Li DZ
Prenat Diagn 2021 May;41(6):766-771. Epub 2021 Apr 5 doi: 10.1002/pd.5942. PMID: 33782977

Recent clinical studies

Etiology

Serra G, Cimador M, Giuffrè M, Insinga V, Montante C, Pensabene M, Piro E, Salerno S, Schierz IAM, Corsello G
Ital J Pediatr 2023 Sep 19;49(1):124. doi: 10.1186/s13052-023-01523-7. PMID: 37726782Free PMC Article
Chen YX, Huang C, He QM, Wang Z, Huang L, Wang HY, Mei SS, Chai CW, Zhang GL, Zhong W, Li DZ
Prenat Diagn 2021 May;41(6):766-771. Epub 2021 Apr 5 doi: 10.1002/pd.5942. PMID: 33782977
Li Y, Liu X, Duan CF, Zhuang XH, Ge W, Song XF
Clin Imaging 2021 Apr;72:91-96. Epub 2020 Nov 4 doi: 10.1016/j.clinimag.2020.10.040. PMID: 33217676
Pachl M, Arul GS, Jester I, Bowen C, Hobin D, Morland B
Ann R Coll Surg Engl 2020 Jan;102(1):67-70. Epub 2019 Sep 11 doi: 10.1308/rcsann.2019.0111. PMID: 31508997Free PMC Article
Vokuhl C, Nourkami-Tutdibi N, Furtwängler R, Gessler M, Graf N, Leuschner I
Pediatr Blood Cancer 2018 Apr;65(4) Epub 2017 Dec 29 doi: 10.1002/pbc.26925. PMID: 29286563

Diagnosis

Serra G, Cimador M, Giuffrè M, Insinga V, Montante C, Pensabene M, Piro E, Salerno S, Schierz IAM, Corsello G
Ital J Pediatr 2023 Sep 19;49(1):124. doi: 10.1186/s13052-023-01523-7. PMID: 37726782Free PMC Article
Chen YX, Huang C, He QM, Wang Z, Huang L, Wang HY, Mei SS, Chai CW, Zhang GL, Zhong W, Li DZ
Prenat Diagn 2021 May;41(6):766-771. Epub 2021 Apr 5 doi: 10.1002/pd.5942. PMID: 33782977
Li Y, Liu X, Duan CF, Zhuang XH, Ge W, Song XF
Clin Imaging 2021 Apr;72:91-96. Epub 2020 Nov 4 doi: 10.1016/j.clinimag.2020.10.040. PMID: 33217676
Zhao M, Yin M, Kuick CH, Chen H, Aw SJ, Merchant K, Ng EHQ, Gunaratne S, Loh AHP, Gu W, Tang H, Chang KTE
Histopathology 2020 Oct;77(4):611-621. Epub 2020 Sep 10 doi: 10.1111/his.14194. PMID: 32590884
Chen Y, Zhou L, Liao N, Gao P, Chen L, Li X, Fan M
J Pediatr Urol 2018 Dec;14(6):571.e1-571.e6. Epub 2018 Aug 1 doi: 10.1016/j.jpurol.2018.07.020. PMID: 30145031

Therapy

Bertulli C, Marzollo A, Doria M, Di Cesare S, La Scola C, Mencarelli F, Pasini A, Affinita MC, Vidal E, Magini P, Dimartino P, Masetti R, Greco L, Palomba P, Conti F, Pession A
Int J Mol Sci 2020 Nov 15;21(22) doi: 10.3390/ijms21228604. PMID: 33203071Free PMC Article
Pachl M, Arul GS, Jester I, Bowen C, Hobin D, Morland B
Ann R Coll Surg Engl 2020 Jan;102(1):67-70. Epub 2019 Sep 11 doi: 10.1308/rcsann.2019.0111. PMID: 31508997Free PMC Article
Soyaltın E, Alaygut D, Alparslan C, Özdemir T, Çamlar SA, Mutlubaş F, Kasap-Demir B, Yavaşcan Ö
Turk J Pediatr 2018;60(2):198-200. doi: 10.24953/turkjped.2018.02.014. PMID: 30325129
Vokuhl C, Nourkami-Tutdibi N, Furtwängler R, Gessler M, Graf N, Leuschner I
Pediatr Blood Cancer 2018 Apr;65(4) Epub 2017 Dec 29 doi: 10.1002/pbc.26925. PMID: 29286563
Tuveson DA, Fletcher JA
Curr Opin Oncol 2001 Jul;13(4):249-55. doi: 10.1097/00001622-200107000-00007. PMID: 11429482

Prognosis

Serra G, Cimador M, Giuffrè M, Insinga V, Montante C, Pensabene M, Piro E, Salerno S, Schierz IAM, Corsello G
Ital J Pediatr 2023 Sep 19;49(1):124. doi: 10.1186/s13052-023-01523-7. PMID: 37726782Free PMC Article
Chen YX, Huang C, He QM, Wang Z, Huang L, Wang HY, Mei SS, Chai CW, Zhang GL, Zhong W, Li DZ
Prenat Diagn 2021 May;41(6):766-771. Epub 2021 Apr 5 doi: 10.1002/pd.5942. PMID: 33782977
Chen Y, Zhou L, Liao N, Gao P, Chen L, Li X, Fan M
J Pediatr Urol 2018 Dec;14(6):571.e1-571.e6. Epub 2018 Aug 1 doi: 10.1016/j.jpurol.2018.07.020. PMID: 30145031
Vokuhl C, Nourkami-Tutdibi N, Furtwängler R, Gessler M, Graf N, Leuschner I
Pediatr Blood Cancer 2018 Apr;65(4) Epub 2017 Dec 29 doi: 10.1002/pbc.26925. PMID: 29286563
Daniel J, Ruzic A, Dalland J, Miller V, Hanna M
J Neonatal Perinatal Med 2017;10(1):113-118. doi: 10.3233/NPM-1617. PMID: 28282819

Clinical prediction guides

Serra G, Cimador M, Giuffrè M, Insinga V, Montante C, Pensabene M, Piro E, Salerno S, Schierz IAM, Corsello G
Ital J Pediatr 2023 Sep 19;49(1):124. doi: 10.1186/s13052-023-01523-7. PMID: 37726782Free PMC Article
Surrey LF, Davis JL
Cancer Genet 2022 Jan;260-261:6-13. Epub 2021 Nov 3 doi: 10.1016/j.cancergen.2021.10.007. PMID: 34794069
Li Y, Liu X, Duan CF, Zhuang XH, Ge W, Song XF
Clin Imaging 2021 Apr;72:91-96. Epub 2020 Nov 4 doi: 10.1016/j.clinimag.2020.10.040. PMID: 33217676
Apaydin E, Ozluk Y, Yuksel S, Erginel B, Tugcu D, Celik A, Kilicaslan I
Fetal Pediatr Pathol 2016;35(6):376-384. Epub 2016 Aug 2 doi: 10.1080/15513815.2016.1207731. PMID: 27484189
Chaudry G, Perez-Atayde AR, Ngan BY, Gundogan M, Daneman A
Pediatr Radiol 2009 Oct;39(10):1080-6. Epub 2009 Jul 21 doi: 10.1007/s00247-009-1354-y. PMID: 19629463

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