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Kuster syndrome

MedGen UID:
419150
•Concept ID:
C2931741
•
Disease or Syndrome
Synonyms: Cleft lip and palate, lower lip pits, and limb deficiency defects; Cleft lip palate lip pits limb deficiency
 
Monarch Initiative: MONDO:0023581

Professional guidelines

PubMed

Causes Of Primary Amenorrhea At Tertiary Level Hospital.
Jabeen S, Raees M, Nisar M
J Ayub Med Coll Abbottabad 2019 Jan-Mar;31(1):60-63. PMID: 30868785

Recent clinical studies

Etiology

Causes Of Primary Amenorrhea At Tertiary Level Hospital.
Jabeen S, Raees M, Nisar M
J Ayub Med Coll Abbottabad 2019 Jan-Mar;31(1):60-63. PMID: 30868785
Long-term results of vaginal construction with the use of Frank dilation and a peritoneal graft (Davydov procedure) in patients with Mayer-Rokitansky-Küster syndrome.
Willemsen WN, Kluivers KB
Fertil Steril 2015 Jan;103(1):220-7.e1. Epub 2014 Nov 15 doi: 10.1016/j.fertnstert.2014.10.014. PMID: 25455533
Carcinoma of the neovagina: case report and review of the literature.
Steiner E, Woernle F, Kuhn W, Beckmann K, Schmidt M, Pilch H, Knapstein PG
Gynecol Oncol 2002 Jan;84(1):171-5. doi: 10.1006/gyno.2001.6417. PMID: 11748997
The role of rectosigmoid neocolporrhaphy.
Lenaghan R, Wilson N, Lucas CE, Ledgerwood AM
Surgery 1997 Oct;122(4):856-60. doi: 10.1016/s0039-6060(97)90098-2. PMID: 9347867
Non-grafting method of vaginal construction for patients of vaginal agenesis without functioning uterus (Mayer-Rokitansky-Küster syndrome).
Makinoda S, Nishiya M, Sogame M, Mikuni M, Kojo T, Fujino T, Hareyama H, Fujimoto S
Int Surg 1996 Oct-Dec;81(4):385-9. PMID: 9127801

Diagnosis

Long-term results of vaginal construction with the use of Frank dilation and a peritoneal graft (Davydov procedure) in patients with Mayer-Rokitansky-Küster syndrome.
Willemsen WN, Kluivers KB
Fertil Steril 2015 Jan;103(1):220-7.e1. Epub 2014 Nov 15 doi: 10.1016/j.fertnstert.2014.10.014. PMID: 25455533
Mayer-Rokitansky-Küster-Hauser (MRKH) syndrome: a historical perspective.
Patnaik SS, Brazile B, Dandolu V, Ryan PL, Liao J
Gene 2015 Jan 15;555(1):33-40. Epub 2014 Sep 26 doi: 10.1016/j.gene.2014.09.045. PMID: 25260227
The use of isolated sigmoid colon segment for vaginal replacement in young adults.
Moudouni S, Koutani A, Attya AI, Hachimi M, Lakrissa A
Int Urol Nephrol 2004;36(4):567-71. doi: 10.1007/s11255-004-0861-x. PMID: 15787338
Transrectal scanning: an alternative when transvaginal scanning is not feasible.
Timor-Tritsch IE, Monteagudo A, Rebarber A, Goldstein SR, Tsymbal T
Ultrasound Obstet Gynecol 2003 May;21(5):473-9. doi: 10.1002/uog.110. PMID: 12768560
Vaginal agenesis and congenital adrenal hyperplasia. Psychosocial sequelae of diagnosis and neovagina formation.
Langer M, Grünberger W, Ringler M
Acta Obstet Gynecol Scand 1990;69(4):343-9. doi: 10.3109/00016349009036159. PMID: 2244467

Therapy

Long-term results of vaginal construction with the use of Frank dilation and a peritoneal graft (Davydov procedure) in patients with Mayer-Rokitansky-Küster syndrome.
Willemsen WN, Kluivers KB
Fertil Steril 2015 Jan;103(1):220-7.e1. Epub 2014 Nov 15 doi: 10.1016/j.fertnstert.2014.10.014. PMID: 25455533

Clinical prediction guides

Carcinoma of the neovagina: case report and review of the literature.
Steiner E, Woernle F, Kuhn W, Beckmann K, Schmidt M, Pilch H, Knapstein PG
Gynecol Oncol 2002 Jan;84(1):171-5. doi: 10.1006/gyno.2001.6417. PMID: 11748997
Non-grafting method of vaginal construction for patients of vaginal agenesis without functioning uterus (Mayer-Rokitansky-Küster syndrome).
Makinoda S, Nishiya M, Sogame M, Mikuni M, Kojo T, Fujino T, Hareyama H, Fujimoto S
Int Surg 1996 Oct-Dec;81(4):385-9. PMID: 9127801

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