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Liver neuroendocrine carcinoma

MedGen UID:
474664
•Concept ID:
C3273031
•
Neoplastic Process
Synonyms: Hepatic Neuroendocrine Carcinoma; hepatic neuroendocrine carcinoma; HNEC; liver neuroendocrine cancer; Liver Neuroendocrine Carcinoma; liver neuroendocrine carcinoma; neuroendocrine carcinoma of liver; PHNEC; Primary Hepatic Neuroendocrine Carcinoma; Primary hepatic neuroendocrine carcinoma; primary hepatic neuroendocrine carcinoma; Primary Liver Neuroendocrine Carcinoma; primary liver neuroendocrine carcinoma
SNOMED CT: Primary hepatic neuroendocrine carcinoma (716652006)
Modes of inheritance:
Not genetically inherited
MedGen UID:
988794
•Concept ID:
CN307044
•
Finding
Source: Orphanet
clinical entity without genetic inheritance.
See: This record
Not genetically inherited (Orphanet)
 
Monarch Initiative: MONDO:0015072
Orphanet: ORPHA100085

Definition

A rare hepatic tumor that may manifest with abdominal pain or fullness, as well as diarrhea or weight loss. More than 10% of cases are asymptomatic and in rare cases a carcinoid syndrome may be observed. The age of onset is variable. The etiology is still unknown but it is thought to arise from Kulchitsky cells originating in the neural crest. [from SNOMEDCT_US]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVLiver neuroendocrine carcinoma

Professional guidelines

PubMed

Novel Therapeutics and Treatment Strategies for Medullary Thyroid Cancer.
Walgama E, Busaidy N, Zafereo M
Endocrinol Metab Clin North Am 2022 Jun;51(2):379-389. Epub 2022 May 4 doi: 10.1016/j.ecl.2022.02.001. PMID: 35662447
When should a liver resection be performed in patients with liver metastases from neuroendocrine tumours? A systematic review with practice recommendations.
Lesurtel M, Nagorney DM, Mazzaferro V, Jensen RT, Poston GJ
HPB (Oxford) 2015 Jan;17(1):17-22. Epub 2014 Mar 17 doi: 10.1111/hpb.12225. PMID: 24636662Free PMC Article
Management of patients with metastatic cancer of unknown primary.
Ghosh L, Dahut W, Kakar S, Posadas EM, Torres CG, Cancel-Santiago R, Ghosh BC
Curr Probl Surg 2005 Jan;42(1):12-66. doi: 10.1067/j.cpsurg.2004.10.002. PMID: 15711508

Curated

NCCN Clinical Practice Guidelines in Oncology (NCCN Guidelines®), Neuroendocrine and Adrenal Tumors, 2023

Supplemental Content

Table of contents

    Clinical resources

    Practice guidelines

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    Curated

    • NCCN, 2023
      NCCN Clinical Practice Guidelines in Oncology (NCCN Guidelines®), Neuroendocrine and Adrenal Tumors, 2023

    Reviews

    Related information

    • PMC Articles
      Related information in PubMed Central Links
    • PubMed
      Related literature resources in PubMed

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