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Allergic cutaneous vasculitis

MedGen UID:
57718
Concept ID:
C0151436
Disease or Syndrome
Synonyms: Allergic Cutaneous Angiitides; Allergic Cutaneous Angiitis; Allergic Cutaneous Vasculitides; Allergic Cutaneous Vasculitis; Allergic Vasculitides, Cutaneous; Allergic Vasculitis, Cutaneous; Angiitides, Allergic Cutaneous; Angiitides, Cutaneous Leukocytoclastic; Angiitides, Hypersensitivity; Angiitis, Allergic Cutaneous; Angiitis, Cutaneous Leukocytoclastic; Angiitis, Hypersensitivity; Cutaneous Allergic Vasculitides; Cutaneous Allergic Vasculitis; Cutaneous Angiitides, Allergic; Cutaneous Angiitis, Allergic; Cutaneous Leukocytoclastic Angiitides; Cutaneous Leukocytoclastic Angiitis; Cutaneous Leukocytoclastic Vasculitides; Cutaneous Leukocytoclastic Vasculitis; Cutaneous Vasculitides, Allergic; Cutaneous Vasculitis, Allergic; Hypersensitivity Angiitides; Hypersensitivity Angiitis; Hypersensitivity Vasculitides; Hypersensitivity Vasculitis; Leukocytoclastic Angiitides, Cutaneous; Leukocytoclastic Angiitis, Cutaneous; Leukocytoclastic Vasculitides, Cutaneous; Leukocytoclastic Vasculitis, Cutaneous; Vasculitides, Allergic Cutaneous; Vasculitides, Cutaneous Allergic; Vasculitides, Cutaneous Leukocytoclastic; Vasculitides, Hypersensitivity; Vasculitis, Allergic Cutaneous; Vasculitis, Cutaneous Allergic; Vasculitis, Cutaneous Leukocytoclastic; Vasculitis, Hypersensitivity; Vasculitis, Leukocytoclastic, Cutaneous
SNOMED CT: Hypersensitivity angiitis (60555002); Leukocytoclastic vasculitis (60555002); Allergic vasculitis (60555002); Hypersensitivity vasculitis (60555002); Cutaneous leukocytoclastic angiitis (718217000); Cutaneous hypersensitivity vasculitis (718217000); Cutaneous small vessel vasculitis (718217000); Maladie trisymptome (60555002); Trisymptome (60555002); Leukocytoclastic angiitis (60555002)
 
Monarch Initiative: MONDO:0001290

Definition

A small-vessel vasculitis presenting with palpable purpura and urticarial lesions which predate the purpuric lesions most frequently observed on the legs. Systemic symptoms including fever, cough, haemoptysis, sinusitis, arthralgia, arthritis, myalgia, abdominal pain, diarrhoea, haematochezia, paraesthesia, weakness, and haematuria may be observed. Can be idiopathic (up to 50% of cases) or secondary to infection, medications (such as antituberculosis medication), collagen vascular diseases, or neoplasms. [from SNOMEDCT_US]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVAllergic cutaneous vasculitis

Professional guidelines

PubMed

Marzano AV, Maronese CA, Genovese G, Ferrucci S, Moltrasio C, Asero R, Cugno M
J Allergy Clin Immunol 2022 Apr;149(4):1137-1149. doi: 10.1016/j.jaci.2022.02.007. PMID: 35396080
Fraticelli P, Benfaremo D, Gabrielli A
Intern Emerg Med 2021 Jun;16(4):831-841. Epub 2021 Mar 13 doi: 10.1007/s11739-021-02688-x. PMID: 33713282Free PMC Article
Ting TV
Pediatr Clin North Am 2014 Apr;61(2):321-46. Epub 2014 Jan 21 doi: 10.1016/j.pcl.2013.11.007. PMID: 24636649

Recent clinical studies

Diagnosis

Tosca N, Stratigos JD
Int J Dermatol 1988 Jun;27(5):291-6. doi: 10.1111/j.1365-4362.1988.tb02353.x. PMID: 3292447
Fine RM, Meltzer HD
South Med J 1968 Jul;61(7):680-6. PMID: 5664515

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