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Ocular adnexal lymphoma

MedGen UID:
453939
Concept ID:
C2981712
Neoplastic Process
Synonyms: non-Hodgkin lymphoma of ocular adnexa; OAL; ocular adnexa non-Hodgkin lymphoma; Ocular Adnexal Lymphoma; ocular adnexal lymphoma; Ocular Adnexal Non-Hodgkin Lymphoma; Primary Ocular Adnexal Lymphoma; Primary Ocular Adnexal Non-Hodgkin Lymphoma
 
Monarch Initiative: MONDO:0020646

Definition

A non-Hodgkin lymphoma arising from the conjunctiva, lacrimal gland, lacrimal drainage apparatus, eyelids, or other orbital tissues around the eye. The vast majority of cases are extranodal marginal zone lymphomas of mucosa-associated lymphoid tissue, however, other histologic types of lymphomas can originate from ocular adnexal tissues, including rare cases of NK/T-cell lymphomas of nasal type. [from NCI]

Professional guidelines

PubMed

Yang Y, Jin X, Wang Y, Ma R, He W
Clin Exp Ophthalmol 2023 Mar;51(2):154-161. Epub 2022 Nov 18 doi: 10.1111/ceo.14189. PMID: 36326836
Aronow ME
Int Ophthalmol Clin 2015 Winter;55(1):97-109. doi: 10.1097/IIO.0000000000000049. PMID: 25436496
Ferreri AJ, Assanelli A, Crocchiolo R, Dognini GP, Resti AG, Politi LS, Doglioni C, Cappio FC, Dolcetti R, Ponzoni M
Expert Opin Pharmacother 2007 Jun;8(8):1073-83. doi: 10.1517/14656566.8.8.1073. PMID: 17922636

Recent clinical studies

Etiology

Yang Y, Jin X, Wang Y, Ma R, He W
Clin Exp Ophthalmol 2023 Mar;51(2):154-161. Epub 2022 Nov 18 doi: 10.1111/ceo.14189. PMID: 36326836
Vest SD, Coupland SE, Esmaeli B, Finger PT, Graue GF, Grossniklaus HE, Hindso TG, Holm F, Honavar SG, Khong JJ, Kirkegaard MK, McKelvie PA, Mikkelsen LH, Mulay K, Rasmussen PK, Siersma V, Sjö LD, Sniegowski MC, Thuro BA, Vemuganti GK, Heegaard S
Br J Ophthalmol 2023 Sep;107(9):1231-1238. Epub 2022 May 5 doi: 10.1136/bjophthalmol-2021-320466. PMID: 35512851
Castillejo Becerra CM, Dalvin LA, Jevremovic D, Hodge DO, Tooley AA
Orbit 2022 Feb;41(1):97-104. Epub 2022 Jan 4 doi: 10.1080/01676830.2021.2018715. PMID: 35100932
Hsu CR, Chen YY, Yao M, Wei YH, Hsieh YT, Liao SL
Eye (Lond) 2021 Jul;35(7):1946-1953. Epub 2020 Sep 29 doi: 10.1038/s41433-020-01198-y. PMID: 32994547Free PMC Article
Mulay K, Honavar SG
Semin Diagn Pathol 2016 May;33(3):164-72. Epub 2015 Oct 23 doi: 10.1053/j.semdp.2015.10.004. PMID: 26972223

Diagnosis

Kirkegaard MK
Acta Ophthalmol 2022 Oct;100 Suppl 270:3-37. doi: 10.1111/aos.15248. PMID: 36196757
Hsu CR, Chen YY, Yao M, Wei YH, Hsieh YT, Liao SL
Eye (Lond) 2021 Jul;35(7):1946-1953. Epub 2020 Sep 29 doi: 10.1038/s41433-020-01198-y. PMID: 32994547Free PMC Article
Maheshwari A, Finger PT
Cancer Metastasis Rev 2018 Dec;37(4):677-690. doi: 10.1007/s10555-018-9762-9. PMID: 30203109
Svendsen FH, Heegaard S
Surv Ophthalmol 2017 May-Jun;62(3):312-331. Epub 2016 Nov 26 doi: 10.1016/j.survophthal.2016.11.009. PMID: 27894880
Mulay K, Honavar SG
Semin Diagn Pathol 2016 May;33(3):164-72. Epub 2015 Oct 23 doi: 10.1053/j.semdp.2015.10.004. PMID: 26972223

Therapy

Yang X, Wang R, Yuan X, Yao S, Wang C, Cheng J
Radiat Oncol 2022 Dec 20;17(1):208. doi: 10.1186/s13014-022-02180-6. PMID: 36539787Free PMC Article
Aronow ME
Int Ophthalmol Clin 2015 Winter;55(1):97-109. doi: 10.1097/IIO.0000000000000049. PMID: 25436496
Prat MC, Surapaneni K, Chalian H, DeLaPaz RL, Kazim M
Ophthalmic Plast Reconstr Surg 2013 Nov-Dec;29(6):424-7. doi: 10.1097/IOP.0b013e3182916495. PMID: 24220098
Ferreri AJ, Dolcetti R, Du MQ, Doglioni C, Resti AG, Politi LS, De Conciliis C, Radford J, Bertoni F, Zucca E, Cavalli F, Ponzoni M
Ann Oncol 2008 May;19(5):835-46. Epub 2007 Nov 6 doi: 10.1093/annonc/mdm513. PMID: 17986622
Ferreri AJ, Assanelli A, Crocchiolo R, Dognini GP, Resti AG, Politi LS, Doglioni C, Cappio FC, Dolcetti R, Ponzoni M
Expert Opin Pharmacother 2007 Jun;8(8):1073-83. doi: 10.1517/14656566.8.8.1073. PMID: 17922636

Prognosis

Yang Y, Jin X, Wang Y, Ma R, He W
Clin Exp Ophthalmol 2023 Mar;51(2):154-161. Epub 2022 Nov 18 doi: 10.1111/ceo.14189. PMID: 36326836
Kirkegaard MK
Acta Ophthalmol 2022 Oct;100 Suppl 270:3-37. doi: 10.1111/aos.15248. PMID: 36196757
Hsu CR, Chen YY, Yao M, Wei YH, Hsieh YT, Liao SL
Eye (Lond) 2021 Jul;35(7):1946-1953. Epub 2020 Sep 29 doi: 10.1038/s41433-020-01198-y. PMID: 32994547Free PMC Article
Svendsen FH, Heegaard S
Surv Ophthalmol 2017 May-Jun;62(3):312-331. Epub 2016 Nov 26 doi: 10.1016/j.survophthal.2016.11.009. PMID: 27894880
Mulay K, Honavar SG
Semin Diagn Pathol 2016 May;33(3):164-72. Epub 2015 Oct 23 doi: 10.1053/j.semdp.2015.10.004. PMID: 26972223

Clinical prediction guides

Yang Y, Jin X, Wang Y, Ma R, He W
Clin Exp Ophthalmol 2023 Mar;51(2):154-161. Epub 2022 Nov 18 doi: 10.1111/ceo.14189. PMID: 36326836
Yang X, Wang R, Yuan X, Yao S, Wang C, Cheng J
Radiat Oncol 2022 Dec 20;17(1):208. doi: 10.1186/s13014-022-02180-6. PMID: 36539787Free PMC Article
Kirkegaard MK
Acta Ophthalmol 2022 Oct;100 Suppl 270:3-37. doi: 10.1111/aos.15248. PMID: 36196757
Maheshwari A, Finger PT
Cancer Metastasis Rev 2018 Dec;37(4):677-690. doi: 10.1007/s10555-018-9762-9. PMID: 30203109
Ferreri AJ, Dolcetti R, Du MQ, Doglioni C, Resti AG, Politi LS, De Conciliis C, Radford J, Bertoni F, Zucca E, Cavalli F, Ponzoni M
Ann Oncol 2008 May;19(5):835-46. Epub 2007 Nov 6 doi: 10.1093/annonc/mdm513. PMID: 17986622

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