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Gliosarcoma

MedGen UID:
64638
Concept ID:
C0206726
Neoplastic Process
Synonym: Sarcomatous glioblastoma
SNOMED CT: Gliosarcoma (35262004); Glioblastoma with sarcomatous component (35262004)
Modes of inheritance:
Not genetically inherited
MedGen UID:
988794
Concept ID:
CN307044
Finding
Source: Orphanet
clinical entity without genetic inheritance.
 
Monarch Initiative: MONDO:0016681
Orphanet: ORPHA251576

Definition

A rare histological variant of glioblastoma (WHO grade IV) characterized by a biphasic tissue pattern with alternating areas displaying glial and mesenchymal differentiation (WHO). [from NCI]

Professional guidelines

PubMed

Ma R, Alexe DM, Pereira EA
J Neurosurg Sci 2020 Aug;64(4):341-346. Epub 2017 Nov 20 doi: 10.23736/S0390-5616.17.04077-2. PMID: 29154508
Saadeh F, El Iskandarani S, Najjar M, Assi HI
Clin Neurol Neurosurg 2019 Jul;182:98-103. Epub 2019 May 14 doi: 10.1016/j.clineuro.2019.05.008. PMID: 31112812
McAleer MF, Brown PD
CNS Oncol 2015;4(3):171-8. Epub 2015 Apr 23 doi: 10.2217/cns.14.61. PMID: 25905568Free PMC Article

Recent clinical studies

Etiology

Chen J, Han P, Dahiya S
Indian J Pathol Microbiol 2022 May;65(Supplement):S24-S32. doi: 10.4103/ijpm.ijpm_1109_21. PMID: 35562131
Suwala AK, Felix M, Friedel D, Stichel D, Schrimpf D, Hinz F, Hewer E, Schweizer L, Dohmen H, Pohl U, Staszewski O, Korshunov A, Stein M, Wongsurawat T, Cheunsuacchon P, Sathornsumetee S, Koelsche C, Turner C, Le Rhun E, Mühlebner A, Schucht P, Özduman K, Ono T, Shimizu H, Prinz M, Acker T, Herold-Mende C, Kessler T, Wick W, Capper D, Wesseling P, Sahm F, von Deimling A, Hartmann C, Reuss DE
Acta Neuropathol 2022 Feb;143(2):263-281. Epub 2021 Dec 30 doi: 10.1007/s00401-021-02395-z. PMID: 34967922Free PMC Article
Saadeh F, El Iskandarani S, Najjar M, Assi HI
Clin Neurol Neurosurg 2019 Jul;182:98-103. Epub 2019 May 14 doi: 10.1016/j.clineuro.2019.05.008. PMID: 31112812
Han SJ, Yang I, Tihan T, Chang SM, Parsa AT
J Neurosurg 2010 Jan;112(1):26-32. doi: 10.3171/2009.3.JNS081081. PMID: 19408981
Lach M, Wallace CJ, Krcek J, Curry B
Can Assoc Radiol J 1996 Jun;47(3):209-12. PMID: 8640419

Diagnosis

Chen J, Han P, Dahiya S
Indian J Pathol Microbiol 2022 May;65(Supplement):S24-S32. doi: 10.4103/ijpm.ijpm_1109_21. PMID: 35562131
Suwala AK, Felix M, Friedel D, Stichel D, Schrimpf D, Hinz F, Hewer E, Schweizer L, Dohmen H, Pohl U, Staszewski O, Korshunov A, Stein M, Wongsurawat T, Cheunsuacchon P, Sathornsumetee S, Koelsche C, Turner C, Le Rhun E, Mühlebner A, Schucht P, Özduman K, Ono T, Shimizu H, Prinz M, Acker T, Herold-Mende C, Kessler T, Wick W, Capper D, Wesseling P, Sahm F, von Deimling A, Hartmann C, Reuss DE
Acta Neuropathol 2022 Feb;143(2):263-281. Epub 2021 Dec 30 doi: 10.1007/s00401-021-02395-z. PMID: 34967922Free PMC Article
Kim H, Lim KY, Park JW, Kang J, Won JK, Lee K, Shim Y, Park CK, Kim SK, Choi SH, Kim TM, Yun H, Park SH
Lab Invest 2022 Feb;102(2):160-171. Epub 2021 Nov 30 doi: 10.1038/s41374-021-00694-3. PMID: 34848827Free PMC Article
Hashmi FA, Salim A, Shamim MS, Bari ME
J Pak Med Assoc 2018 Aug;68(8):1273-1275. PMID: 30108403
Miller CR, Perry A
Arch Pathol Lab Med 2007 Mar;131(3):397-406. doi: 10.5858/2007-131-397-G. PMID: 17516742

Therapy

Vuong HG, Dunn IF
J Neurooncol 2022 Aug;159(1):195-200. Epub 2022 Jun 29 doi: 10.1007/s11060-022-04057-w. PMID: 35768633
Kim H, Lim KY, Park JW, Kang J, Won JK, Lee K, Shim Y, Park CK, Kim SK, Choi SH, Kim TM, Yun H, Park SH
Lab Invest 2022 Feb;102(2):160-171. Epub 2021 Nov 30 doi: 10.1038/s41374-021-00694-3. PMID: 34848827Free PMC Article
Shin JY, Yoon JK, Diaz AZ
J Clin Neurosci 2017 Nov;45:77-82. Epub 2017 Jul 26 doi: 10.1016/j.jocn.2017.07.002. PMID: 28756069
McAleer MF, Brown PD
CNS Oncol 2015;4(3):171-8. Epub 2015 Apr 23 doi: 10.2217/cns.14.61. PMID: 25905568Free PMC Article
Lach M, Wallace CJ, Krcek J, Curry B
Can Assoc Radiol J 1996 Jun;47(3):209-12. PMID: 8640419

Prognosis

Björkblom B, Wibom C, Eriksson M, Bergenheim AT, Sjöberg RL, Jonsson P, Brännström T, Antti H, Sandström M, Melin B
Neuro Oncol 2022 Sep 1;24(9):1454-1468. doi: 10.1093/neuonc/noac042. PMID: 35157758Free PMC Article
Suwala AK, Felix M, Friedel D, Stichel D, Schrimpf D, Hinz F, Hewer E, Schweizer L, Dohmen H, Pohl U, Staszewski O, Korshunov A, Stein M, Wongsurawat T, Cheunsuacchon P, Sathornsumetee S, Koelsche C, Turner C, Le Rhun E, Mühlebner A, Schucht P, Özduman K, Ono T, Shimizu H, Prinz M, Acker T, Herold-Mende C, Kessler T, Wick W, Capper D, Wesseling P, Sahm F, von Deimling A, Hartmann C, Reuss DE
Acta Neuropathol 2022 Feb;143(2):263-281. Epub 2021 Dec 30 doi: 10.1007/s00401-021-02395-z. PMID: 34967922Free PMC Article
Saadeh F, El Iskandarani S, Najjar M, Assi HI
Clin Neurol Neurosurg 2019 Jul;182:98-103. Epub 2019 May 14 doi: 10.1016/j.clineuro.2019.05.008. PMID: 31112812
Hashmi FA, Salim A, Shamim MS, Bari ME
J Pak Med Assoc 2018 Aug;68(8):1273-1275. PMID: 30108403
Miller CR, Perry A
Arch Pathol Lab Med 2007 Mar;131(3):397-406. doi: 10.5858/2007-131-397-G. PMID: 17516742

Clinical prediction guides

Björkblom B, Wibom C, Eriksson M, Bergenheim AT, Sjöberg RL, Jonsson P, Brännström T, Antti H, Sandström M, Melin B
Neuro Oncol 2022 Sep 1;24(9):1454-1468. doi: 10.1093/neuonc/noac042. PMID: 35157758Free PMC Article
Pierscianek D, Ahmadipour Y, Michel A, Rauschenbach L, Darkwah Oppong M, Deuschl C, Kebir S, Wrede KH, Glas M, Stuschke M, Sure U, Jabbarli R
Clin Neurol Neurosurg 2021 Jan;200:106348. Epub 2020 Nov 1 doi: 10.1016/j.clineuro.2020.106348. PMID: 33158630
Zhang Y, Ma JP, Weng JC, Wang L, Wu Z, Li D, Zhang JT
Neurosurg Rev 2021 Apr;44(2):1003-1015. Epub 2020 Mar 18 doi: 10.1007/s10143-020-01285-4. PMID: 32189095
Yi X, Cao H, Tang H, Gong G, Hu Z, Liao W, Sun L, Chen BT, Li X
Eur Radiol 2019 Jan;29(1):429-438. Epub 2018 Jun 12 doi: 10.1007/s00330-018-5398-y. PMID: 29948068
Smith DR, Wu CC, Saadatmand HJ, Isaacson SR, Cheng SK, Sisti MB, Bruce JN, Sheth SA, Lassman AB, Iwamoto FM, Wang SH, Canoll P, McKhann GM 2nd, Wang TJC
J Neurooncol 2018 Apr;137(2):303-311. Epub 2017 Dec 20 doi: 10.1007/s11060-017-2718-z. PMID: 29264835Free PMC Article

Recent systematic reviews

Vuong HG, Dunn IF
J Neurooncol 2022 Aug;159(1):195-200. Epub 2022 Jun 29 doi: 10.1007/s11060-022-04057-w. PMID: 35768633
Wang X, Jiang J, Liu M, You C
Acta Neurol Belg 2021 Dec;121(6):1789-1797. Epub 2020 Nov 6 doi: 10.1007/s13760-020-01533-w. PMID: 33156945
Gerges C, Elder T, Penuela M, Rossetti N, Maynard M, Jeong S, Wright CH, Wright J, Zhou X, Burant C, Sajatovic M, Hodges T
Clin Neurol Neurosurg 2020 Aug;195:106054. Epub 2020 Jun 29 doi: 10.1016/j.clineuro.2020.106054. PMID: 32650210
Bunevicius A, Matukevicius A, Deltuva V, Gudinaviciene I, Pranys D, Tamasauskas A
World Neurosurg 2018 May;113:129-134. Epub 2018 Feb 13 doi: 10.1016/j.wneu.2018.02.012. PMID: 29452330
Beyer S, von Bueren AO, Klautke G, Guckenberger M, Kortmann RD, Pietschmann S, Müller K
PLoS One 2016;11(2):e0148312. Epub 2016 Feb 9 doi: 10.1371/journal.pone.0148312. PMID: 26859136Free PMC Article

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