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Vestibulocochlear nerve disorder

MedGen UID:
1724
•Concept ID:
C0001163
•
Disease or Syndrome
Synonym: Vestibulocochlear nerve disease
SNOMED CT: Disorder of acoustic nerve (77949003); Disorder of eighth nerve (77949003); Disorder of the vestibulocochlear nerve (77949003); Disorder of acoustovestibular nerve (77949003)
 
Monarch Initiative: MONDO:0001563

Definition

A non-neoplastic or neoplastic disorder affecting the acoustic nerve. [from NCI]

Professional guidelines

PubMed

Updated diagnostic criteria and nomenclature for neurofibromatosis type 2 and schwannomatosis: An international consensus recommendation.
Plotkin SR, Messiaen L, Legius E, Pancza P, Avery RA, Blakeley JO, Babovic-Vuksanovic D, Ferner R, Fisher MJ, Friedman JM, Giovannini M, Gutmann DH, Hanemann CO, Kalamarides M, Kehrer-Sawatzki H, Korf BR, Mautner VF, MacCollin M, Papi L, Rauen KA, Riccardi V, Schorry E, Smith MJ, Stemmer-Rachamimov A, Stevenson DA, Ullrich NJ, Viskochil D, Wimmer K, Yohay K; International Consensus Group on Neurofibromatosis Diagnostic Criteria (I-NF-DC), Huson SM, Wolkenstein P, Evans DG
Genet Med 2022 Sep;24(9):1967-1977. Epub 2022 Jun 9 doi: 10.1016/j.gim.2022.05.007. PMID: 35674741
EANO guideline on the diagnosis and treatment of vestibular schwannoma.
Goldbrunner R, Weller M, Regis J, Lund-Johansen M, Stavrinou P, Reuss D, Evans DG, Lefranc F, Sallabanda K, Falini A, Axon P, Sterkers O, Fariselli L, Wick W, Tonn JC
Neuro Oncol 2020 Jan 11;22(1):31-45. doi: 10.1093/neuonc/noz153. PMID: 31504802Free PMC Article
Dizziness: Approach to Evaluation and Management.
Muncie HL, Sirmans SM, James E
Am Fam Physician 2017 Feb 1;95(3):154-162. PMID: 28145669

Recent clinical studies

Etiology

Vestibular Schwannoma: What We Know and Where We are Heading.
Gupta VK, Thakker A, Gupta KK
Head Neck Pathol 2020 Dec;14(4):1058-1066. Epub 2020 Mar 30 doi: 10.1007/s12105-020-01155-x. PMID: 32232723Free PMC Article
Efficacy of Vestibular Rehabilitation Following Acute Vestibular Neuritis: A Randomized Controlled Trial.
Tokle G, Mørkved S, Bråthen G, Goplen FK, Salvesen Ø, Arnesen H, Holmeslet B, Nordahl SHG, Wilhelmsen KT
Otol Neurotol 2020 Jan;41(1):78-85. doi: 10.1097/MAO.0000000000002443. PMID: 31789800
Vertigo and Dizziness: Understanding and Managing Fall Risk.
Alyono JC
Otolaryngol Clin North Am 2018 Aug;51(4):725-740. Epub 2018 May 24 doi: 10.1016/j.otc.2018.03.003. PMID: 29803531
Neurofibromatosis Type 2.
Ardern-Holmes S, Fisher G, North K
J Child Neurol 2017 Jan;32(1):9-22. Epub 2016 Sep 29 doi: 10.1177/0883073816666736. PMID: 27655473
Acoustic neuroma.
Consens Statement 1991 Dec 11-13;9(4):1-24. PMID: 1840823

Diagnosis

Cogan's Syndrome: Clinical Presentations and Update on Treatment.
Espinoza GM, Wheeler J, Temprano KK, Keller AP
Curr Allergy Asthma Rep 2020 Jun 16;20(9):46. doi: 10.1007/s11882-020-00945-1. PMID: 32548646
Vestibular Schwannoma: What We Know and Where We are Heading.
Gupta VK, Thakker A, Gupta KK
Head Neck Pathol 2020 Dec;14(4):1058-1066. Epub 2020 Mar 30 doi: 10.1007/s12105-020-01155-x. PMID: 32232723Free PMC Article
EANO guideline on the diagnosis and treatment of vestibular schwannoma.
Goldbrunner R, Weller M, Regis J, Lund-Johansen M, Stavrinou P, Reuss D, Evans DG, Lefranc F, Sallabanda K, Falini A, Axon P, Sterkers O, Fariselli L, Wick W, Tonn JC
Neuro Oncol 2020 Jan 11;22(1):31-45. doi: 10.1093/neuonc/noz153. PMID: 31504802Free PMC Article
Vestibular Neuritis: Recent Advances in Etiology, Diagnostic Evaluation, and Treatment.
Le TN, Westerberg BD, Lea J
Adv Otorhinolaryngol 2019;82:87-92. Epub 2019 Jan 15 doi: 10.1159/000490275. PMID: 30947184
Vertigo and Dizziness: Understanding and Managing Fall Risk.
Alyono JC
Otolaryngol Clin North Am 2018 Aug;51(4):725-740. Epub 2018 May 24 doi: 10.1016/j.otc.2018.03.003. PMID: 29803531

Therapy

A Critical Overview of Targeted Therapies for Vestibular Schwannoma.
Tamura R, Toda M
Int J Mol Sci 2022 May 13;23(10) doi: 10.3390/ijms23105462. PMID: 35628268Free PMC Article
Current Understanding of Neurofibromatosis Type 1, 2, and Schwannomatosis.
Tamura R
Int J Mol Sci 2021 May 29;22(11) doi: 10.3390/ijms22115850. PMID: 34072574Free PMC Article
Vestibular Schwannomas.
Carlson ML, Link MJ
N Engl J Med 2021 Apr 8;384(14):1335-1348. doi: 10.1056/NEJMra2020394. PMID: 33826821
Efficacy of Vestibular Rehabilitation Following Acute Vestibular Neuritis: A Randomized Controlled Trial.
Tokle G, Mørkved S, Bråthen G, Goplen FK, Salvesen Ø, Arnesen H, Holmeslet B, Nordahl SHG, Wilhelmsen KT
Otol Neurotol 2020 Jan;41(1):78-85. doi: 10.1097/MAO.0000000000002443. PMID: 31789800
Vestibular Neuritis: Recent Advances in Etiology, Diagnostic Evaluation, and Treatment.
Le TN, Westerberg BD, Lea J
Adv Otorhinolaryngol 2019;82:87-92. Epub 2019 Jan 15 doi: 10.1159/000490275. PMID: 30947184

Prognosis

Vestibular Schwannomas.
Carlson ML, Link MJ
N Engl J Med 2021 Apr 8;384(14):1335-1348. doi: 10.1056/NEJMra2020394. PMID: 33826821
Long-term clinical outcome in vestibular neuritis.
Bronstein AM, Dieterich M
Curr Opin Neurol 2019 Feb;32(1):174-180. doi: 10.1097/WCO.0000000000000652. PMID: 30566414
Radiation therapy for vestibular schwannomas.
Mulder JJ, Kaanders JH, van Overbeeke JJ, Cremers CW
Curr Opin Otolaryngol Head Neck Surg 2012 Oct;20(5):367-71. doi: 10.1097/MOO.0b013e328357d337. PMID: 22931906
Sound conclusions?
Colebatch JG
Clin Neurophysiol 2010 Feb;121(2):124-6. Epub 2009 Nov 7 doi: 10.1016/j.clinph.2009.09.026. PMID: 19897411
Neurofibromatosis type 2.
Evans DG, Sainio M, Baser ME
J Med Genet 2000 Dec;37(12):897-904. doi: 10.1136/jmg.37.12.897. PMID: 11106352Free PMC Article

Clinical prediction guides

EANO guideline on the diagnosis and treatment of vestibular schwannoma.
Goldbrunner R, Weller M, Regis J, Lund-Johansen M, Stavrinou P, Reuss D, Evans DG, Lefranc F, Sallabanda K, Falini A, Axon P, Sterkers O, Fariselli L, Wick W, Tonn JC
Neuro Oncol 2020 Jan 11;22(1):31-45. doi: 10.1093/neuonc/noz153. PMID: 31504802Free PMC Article
Long-term clinical outcome in vestibular neuritis.
Bronstein AM, Dieterich M
Curr Opin Neurol 2019 Feb;32(1):174-180. doi: 10.1097/WCO.0000000000000652. PMID: 30566414
Use of HINTS in the acute vestibular syndrome. An Overview.
Kattah JC
Stroke Vasc Neurol 2018 Dec;3(4):190-196. Epub 2018 Jun 23 doi: 10.1136/svn-2018-000160. PMID: 30637123Free PMC Article
Hearing preservation: microsurgery.
Kari E, Friedman RA
Curr Opin Otolaryngol Head Neck Surg 2012 Oct;20(5):358-66. doi: 10.1097/MOO.0b013e3283579673. PMID: 22929113
Acoustic neuroma.
Consens Statement 1991 Dec 11-13;9(4):1-24. PMID: 1840823

Recent systematic reviews

Treatment for vestibular schwannoma: Systematic review and single arm meta-analysis.
Thai NLB, Mai NY, Vuong NL, Tin NM, Karam D, Refaey MA, Shahin KM, Soliman AL, Al Khudari R, Thuan TM, Sabbah GM, El-Qushayri AE, Karimzadeh S, Hirayama K, Huy NT
Am J Otolaryngol 2022 Mar-Apr;43(2):103337. Epub 2021 Dec 20 doi: 10.1016/j.amjoto.2021.103337. PMID: 34973662
Comparison of surgical outcomes in cystic and solid vestibular schwannomas: a systematic review and meta-analysis.
Wu X, Song G, Wang X, Li M, Chen G, Guo H, Bao Y, Liang J
Neurosurg Rev 2021 Aug;44(4):1889-1902. Epub 2020 Oct 2 doi: 10.1007/s10143-020-01400-5. PMID: 33009643
American Cancer Society Head and Neck Cancer Survivorship Care Guideline.
Cohen EE, LaMonte SJ, Erb NL, Beckman KL, Sadeghi N, Hutcheson KA, Stubblefield MD, Abbott DM, Fisher PS, Stein KD, Lyman GH, Pratt-Chapman ML
CA Cancer J Clin 2016 May;66(3):203-39. Epub 2016 Mar 22 doi: 10.3322/caac.21343. PMID: 27002678
COGAN'S SYNDROME.
Iliescu DA, Timaru CM, Batras M, De Simone A, Stefan C
Rom J Ophthalmol 2015 Jan-Mar;59(1):6-13. PMID: 27373108Free PMC Article
Indications and contraindications of auditory brainstem implants: systematic review and illustrative cases.
Merkus P, Di Lella F, Di Trapani G, Pasanisi E, Beltrame MA, Zanetti D, Negri M, Sanna M
Eur Arch Otorhinolaryngol 2014 Jan;271(1):3-13. Epub 2013 Feb 13 doi: 10.1007/s00405-013-2378-3. PMID: 23404468

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