U.S. flag

An official website of the United States government

Format

Send to:

Choose Destination

Retrocochlear disease

MedGen UID:
11216
•Concept ID:
C0035352
•
Disease or Syndrome
Synonyms: Disease, Retrocochlear; Diseases, Retrocochlear; Retrocochlear Disease; Retrocochlear Diseases
 
Monarch Initiative: MONDO:0002453

Definition

Pathological processes involving the vestibulocochlear nerve; brainstem; or central nervous system. When hearing loss is due to retrocochlear pathology, it is called retrocochlear hearing loss. [from MONDO]

Professional guidelines

PubMed

Clinical Utility of the Standardized Word Recognition Score.
Zapala DA, Stamper GC, Bogle JM, Jagger SL, Lundy LB
Ear Hear 2024 Jan-Feb 01;45(1):94-105. Epub 2023 Jun 30 doi: 10.1097/AUD.0000000000001404. PMID: 37386698
Oral steroid treatment of sudden sensorineural hearing loss: a ten year retrospective analysis.
Chen CY, Halpin C, Rauch SD
Otol Neurotol 2003 Sep;24(5):728-33. doi: 10.1097/00129492-200309000-00006. PMID: 14501447
A practical approach to the patient with vertigo: an outline of diagnosis and management for the nonspecialist.
Turner JS Jr
South Med J 1975 Feb;68(2):241-5. doi: 10.1097/00007611-197502000-00027. PMID: 1118759

Recent clinical studies

Etiology

Clinical Utility of the Standardized Word Recognition Score.
Zapala DA, Stamper GC, Bogle JM, Jagger SL, Lundy LB
Ear Hear 2024 Jan-Feb 01;45(1):94-105. Epub 2023 Jun 30 doi: 10.1097/AUD.0000000000001404. PMID: 37386698
Outcomes of cochlear implantation in patients with neurofibromatosis type 2.
North HJ, Mawman D, O'Driscoll M, Freeman SR, Rutherford SA, King AT, Hammerbeck-Ward C, Evans DG, Lloyd SK
Cochlear Implants Int 2016 Jul;17(4):172-177. doi: 10.1080/14670100.2016.1197587. PMID: 27691934
Oral steroid treatment of sudden sensorineural hearing loss: a ten year retrospective analysis.
Chen CY, Halpin C, Rauch SD
Otol Neurotol 2003 Sep;24(5):728-33. doi: 10.1097/00129492-200309000-00006. PMID: 14501447
Neural networks applied to retrocochlear diagnosis.
Callan DE, Lasky RE, Fowler CG
J Speech Lang Hear Res 1999 Apr;42(2):287-99. doi: 10.1044/jslhr.4202.287. PMID: 10229447
Correcting for factors affecting ABR wave V latency.
Lightfoot GR
Br J Audiol 1993 Jun;27(3):211-20. doi: 10.3109/03005369309076695. PMID: 8241970

Diagnosis

Pseudo-sudden deafness.
Song JE, Sapthavee A, Cager GR, Saadia-Redleaf MI
Ann Otol Rhinol Laryngol 2012 Feb;121(2):96-9. doi: 10.1177/000348941212100204. PMID: 22397217
Oral steroid treatment of sudden sensorineural hearing loss: a ten year retrospective analysis.
Chen CY, Halpin C, Rauch SD
Otol Neurotol 2003 Sep;24(5):728-33. doi: 10.1097/00129492-200309000-00006. PMID: 14501447
Neural networks applied to retrocochlear diagnosis.
Callan DE, Lasky RE, Fowler CG
J Speech Lang Hear Res 1999 Apr;42(2):287-99. doi: 10.1044/jslhr.4202.287. PMID: 10229447
Correcting for factors affecting ABR wave V latency.
Lightfoot GR
Br J Audiol 1993 Jun;27(3):211-20. doi: 10.3109/03005369309076695. PMID: 8241970
A practical approach to the patient with vertigo: an outline of diagnosis and management for the nonspecialist.
Turner JS Jr
South Med J 1975 Feb;68(2):241-5. doi: 10.1097/00007611-197502000-00027. PMID: 1118759

Therapy

Pseudo-sudden deafness.
Song JE, Sapthavee A, Cager GR, Saadia-Redleaf MI
Ann Otol Rhinol Laryngol 2012 Feb;121(2):96-9. doi: 10.1177/000348941212100204. PMID: 22397217
Intratympanic dexamethasone for sudden sensorineural hearing loss after failure of systemic therapy.
Haynes DS, O'Malley M, Cohen S, Watford K, Labadie RF
Laryngoscope 2007 Jan;117(1):3-15. doi: 10.1097/01.mlg.0000245058.11866.15. PMID: 17202923
Oral steroid treatment of sudden sensorineural hearing loss: a ten year retrospective analysis.
Chen CY, Halpin C, Rauch SD
Otol Neurotol 2003 Sep;24(5):728-33. doi: 10.1097/00129492-200309000-00006. PMID: 14501447
Mass screening for retrocochlear disorders: low-field-strength (0.2-T) versus high-field-strength (1.5-T) MR imaging.
Dubrulle F, Delomez J, Kiaei A, Berger P, Vincent C, Vaneecloo FM, Lemaitre L
AJNR Am J Neuroradiol 2002 Jun-Jul;23(6):918-23. PMID: 12063216Free PMC Article
A practical approach to the patient with vertigo: an outline of diagnosis and management for the nonspecialist.
Turner JS Jr
South Med J 1975 Feb;68(2):241-5. doi: 10.1097/00007611-197502000-00027. PMID: 1118759

Prognosis

Clinical Utility of the Standardized Word Recognition Score.
Zapala DA, Stamper GC, Bogle JM, Jagger SL, Lundy LB
Ear Hear 2024 Jan-Feb 01;45(1):94-105. Epub 2023 Jun 30 doi: 10.1097/AUD.0000000000001404. PMID: 37386698
Intratympanic dexamethasone for sudden sensorineural hearing loss after failure of systemic therapy.
Haynes DS, O'Malley M, Cohen S, Watford K, Labadie RF
Laryngoscope 2007 Jan;117(1):3-15. doi: 10.1097/01.mlg.0000245058.11866.15. PMID: 17202923
Oral steroid treatment of sudden sensorineural hearing loss: a ten year retrospective analysis.
Chen CY, Halpin C, Rauch SD
Otol Neurotol 2003 Sep;24(5):728-33. doi: 10.1097/00129492-200309000-00006. PMID: 14501447
Neural networks applied to retrocochlear diagnosis.
Callan DE, Lasky RE, Fowler CG
J Speech Lang Hear Res 1999 Apr;42(2):287-99. doi: 10.1044/jslhr.4202.287. PMID: 10229447
Management of vestibular schwannomas (acoustic neuromas): the value of neurophysiology for evaluation and prediction of auditory function in 420 cases.
Matthies C, Samii M
Neurosurgery 1997 May;40(5):919-29; discussion 929-30. doi: 10.1097/00006123-199705000-00007. PMID: 9149249

Clinical prediction guides

Outcomes of cochlear implantation in patients with neurofibromatosis type 2.
North HJ, Mawman D, O'Driscoll M, Freeman SR, Rutherford SA, King AT, Hammerbeck-Ward C, Evans DG, Lloyd SK
Cochlear Implants Int 2016 Jul;17(4):172-177. doi: 10.1080/14670100.2016.1197587. PMID: 27691934
Pseudo-sudden deafness.
Song JE, Sapthavee A, Cager GR, Saadia-Redleaf MI
Ann Otol Rhinol Laryngol 2012 Feb;121(2):96-9. doi: 10.1177/000348941212100204. PMID: 22397217
Oral steroid treatment of sudden sensorineural hearing loss: a ten year retrospective analysis.
Chen CY, Halpin C, Rauch SD
Otol Neurotol 2003 Sep;24(5):728-33. doi: 10.1097/00129492-200309000-00006. PMID: 14501447
Neural networks applied to retrocochlear diagnosis.
Callan DE, Lasky RE, Fowler CG
J Speech Lang Hear Res 1999 Apr;42(2):287-99. doi: 10.1044/jslhr.4202.287. PMID: 10229447
Auditory brainstem responses in ears with hearing loss: case studies.
Bauch CD, Rose DE, Harner SG
Scand Audiol 1981;10(4):247-54. doi: 10.3109/01050398109076188. PMID: 7323675

Recent systematic reviews

Hearing rehabilitation outcomes in cochlear implant recipients with vestibular schwannoma in observation or radiotherapy groups: A systematic review.
Borsetto D, Hammond-Kenny A, Tysome JR, Axon PR, Donnelly NP, Vijendren A, Phillips V, Bance ML
Cochlear Implants Int 2020 Jan;21(1):9-17. Epub 2019 Sep 8 doi: 10.1080/14670100.2019.1662161. PMID: 31496442

Supplemental Content

Table of contents

    Clinical resources

    Practice guidelines

    • PubMed
      See practice and clinical guidelines in PubMed. The search results may include broader topics and may not capture all published guidelines. See the FAQ for details.

    Consumer resources

    Reviews

    Recent activity

    Clear Turn Off Turn On

    Your browsing activity is empty.

    Activity recording is turned off.

    Turn recording back on

    See more...