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Atrial arrhythmia

MedGen UID:
39317
Concept ID:
C0085611
Pathologic Function
Synonym: Atrial arrhythmias
SNOMED CT: Atrial arrhythmia (17366009)
 
HPO: HP:0001692

Definition

A type of supraventricular tachycardia in which the atria are the principal site of electrophysiologic disturbance. [from HPO]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVAtrial arrhythmia

Conditions with this feature

Congenital heart block
MedGen UID:
57432
Concept ID:
C0149530
Disease or Syndrome
Congenital heart block (CHB) is a rare disorder of atrioventricular conduction, characterized by absence of conduction of atrial impulses to the ventricles with slower ventricular rhythm (atrioventricular dissociation). CHB can occur in association with immunological evidence of maternal connective disease (autoimmune CHD), fetal structural CHD or can be idiopathic.
Danon disease
MedGen UID:
209235
Concept ID:
C0878677
Disease or Syndrome
Danon disease is a multisystem condition with predominant involvement of the heart, skeletal muscles, and retina, with overlying cognitive dysfunction. Males are typically more severely affected than females. Males usually present with childhood onset concentric hypertrophic cardiomyopathy that is progressive and often requires heart transplantation. Rarely, hypertrophic cardiomyopathy can evolve to resemble dilated cardiomyopathy. Most affected males also have cardiac conduction abnormalities. Skeletal muscle weakness may lead to delayed acquisition of motor milestones. Learning disability and intellectual disability, most often in the mild range, are common. Additionally, affected males can develop retinopathy with subsequent visual impairment. The clinical features in females are broader and more variable. Females are more likely to have dilated cardiomyopathy, with a smaller proportion requiring heart transplantation compared to affected males. Cardiac conduction abnormalities, skeletal muscle weakness, mild cognitive impairment, and pigmentary retinopathy are variably seen in affected females.
Atrial standstill 2
MedGen UID:
816731
Concept ID:
C3810401
Disease or Syndrome
Atrial standstill (AS) is a rare condition characterized by the absence of electrical and mechanical activity in the atria. On surface ECG, AS is distinguished by bradycardia, junctional (usually narrow complex) escape rhythm, and absence of the P wave. Nearly 50% of patients with AS experience syncope. AS can be persistent or transient, and diffuse or partial (summary by Fazelifar et al., 2005).
Atrial conduction disease
MedGen UID:
863722
Concept ID:
C4015285
Disease or Syndrome
A rare genetic cardiac disease characterized by variably expressed atrial tachyarrhythmia (such as atrial flutter, paroxysmal or chronic atrial fibrillation, ectopic atrial tachycardia, or multifocal atrial tachycardia), infra-Hisian conduction system disease, and vulnerability to dilated cardiomyopathy. Age of onset ranges between childhood and adulthood.
Emery-Dreifuss muscular dystrophy 1, X-linked
MedGen UID:
1720295
Concept ID:
C5243475
Disease or Syndrome
Emery-Dreifuss muscular dystrophy inherited in an X-linked recessive pattern and caused by mutations in the EMD gene, encoding emerin.

Professional guidelines

PubMed

Pensa AV, Baman JR, Puckelwartz MJ, Wilcox JE
J Cardiovasc Electrophysiol 2022 Aug;33(8):1944-1953. Epub 2022 Mar 19 doi: 10.1111/jce.15446. PMID: 35262243
Guenancia C, Garnier F, Fichot M, Sagnard A, Laurent G, Lorgis L
Future Cardiol 2020 Mar;16(2):133-142. Epub 2020 Mar 3 doi: 10.2217/fca-2019-0066. PMID: 32125174
Martin CA, Lambiase PD
Heart 2017 Oct;103(19):1543-1552. Epub 2017 Aug 30 doi: 10.1136/heartjnl-2016-310391. PMID: 28855272Free PMC Article

Recent clinical studies

Etiology

Kistler PM, Chieng D, Sugumar H, Ling LH, Segan L, Azzopardi S, Al-Kaisey A, Parameswaran R, Anderson RD, Hawson J, Prabhu S, Voskoboinik A, Wong G, Morton JB, Pathik B, McLellan AJ, Lee G, Wong M, Finch S, Pathak RK, Raja DC, Sterns L, Ginks M, Reid CM, Sanders P, Kalman JM
JAMA 2023 Jan 10;329(2):127-135. doi: 10.1001/jama.2022.23722. PMID: 36625809Free PMC Article
Broberg CS, van Dissel A, Minnier J, Aboulhosn J, Kauling RM, Ginde S, Krieger EV, Rodriguez F 3rd, Gupta T, Shah S, John AS, Cotts T, Kay WA, Kuo M, Dwight C, Woods P, Nicolarsen J, Sarubbi B, Fusco F, Antonova P, Fernandes S, Grewal J, Cramer J, Khairy P, Gallego P, O'Donnell C, Hannah J, Dellborg M, Rodriguez-Monserrate CP, Muhll IV, Pylypchuk S, Magalski A, Han F, Lubert AM, Kay J, Yeung E, Roos-Hesselink J, Baker D, Celermajer DS, Burchill LJ, Wilson WM, Wong J, Kutty S, Opotowsky AR
J Am Coll Cardiol 2022 Sep 6;80(10):951-963. doi: 10.1016/j.jacc.2022.06.020. PMID: 36049802
Marrouche NF, Wazni O, McGann C, Greene T, Dean JM, Dagher L, Kholmovski E, Mansour M, Marchlinski F, Wilber D, Hindricks G, Mahnkopf C, Wells D, Jais P, Sanders P, Brachmann J, Bax JJ, Morrison-de Boer L, Deneke T, Calkins H, Sohns C, Akoum N; DECAAF II Investigators
JAMA 2022 Jun 21;327(23):2296-2305. doi: 10.1001/jama.2022.8831. PMID: 35727277Free PMC Article
Wazni OM, Dandamudi G, Sood N, Hoyt R, Tyler J, Durrani S, Niebauer M, Makati K, Halperin B, Gauri A, Morales G, Shao M, Cerkvenik J, Kaplon RE, Nissen SE; STOP AF First Trial Investigators
N Engl J Med 2021 Jan 28;384(4):316-324. Epub 2020 Nov 16 doi: 10.1056/NEJMoa2029554. PMID: 33197158
Gawałko M, Balsam P, Lodziński P, Grabowski M, Krzowski B, Opolski G, Kosiuk J
Circ J 2020 Apr 24;84(5):685-694. Epub 2020 Feb 26 doi: 10.1253/circj.CJ-19-0705. PMID: 32101812

Diagnosis

Turagam MK, Neuzil P, Schmidt B, Reichlin T, Neven K, Metzner A, Hansen J, Blaauw Y, Maury P, Arentz T, Sommer P, Anic A, Anselme F, Boveda S, Deneke T, Willems S, van der Voort P, Tilz R, Funasako M, Scherr D, Wakili R, Steven D, Kautzner J, Vijgen J, Jais P, Petru J, Chun J, Roten L, Füting A, Lemoine MD, Ruwald M, Mulder BA, Rollin A, Lehrmann H, Fink T, Jurisic Z, Chaumont C, Adeliño R, Nentwich K, Gunawardene M, Ouss A, Heeger CH, Manninger M, Bohnen JE, Sultan A, Peichl P, Koopman P, Derval N, Kueffer T, Rahe G, Reddy VY
Circulation 2023 Jul 4;148(1):35-46. Epub 2023 May 18 doi: 10.1161/CIRCULATIONAHA.123.064959. PMID: 37199171
Bradley EA, Zaidi AN
Cardiol Clin 2020 Aug;38(3):317-324. Epub 2020 Jun 6 doi: 10.1016/j.ccl.2020.04.001. PMID: 32622487
Leonelli F, Bagliani G, Boriani G, Padeletti L
Card Electrophysiol Clin 2017 Sep;9(3):383-409. doi: 10.1016/j.ccep.2017.05.002. PMID: 28838547
Marrakchi S, Kanoun F, Idriss S, Kammoun I, Kachboura S
Herz 2015 Apr;40 Suppl 2:101-9. Epub 2014 Jul 4 doi: 10.1007/s00059-014-4123-0. PMID: 24990773
Sucu M, Davutoglu V, Ozer O
Ann Saudi Med 2009 May-Jun;29(3):201-6. doi: 10.4103/0256-4947.51775. PMID: 19448376Free PMC Article

Therapy

Kistler PM, Chieng D, Sugumar H, Ling LH, Segan L, Azzopardi S, Al-Kaisey A, Parameswaran R, Anderson RD, Hawson J, Prabhu S, Voskoboinik A, Wong G, Morton JB, Pathik B, McLellan AJ, Lee G, Wong M, Finch S, Pathak RK, Raja DC, Sterns L, Ginks M, Reid CM, Sanders P, Kalman JM
JAMA 2023 Jan 10;329(2):127-135. doi: 10.1001/jama.2022.23722. PMID: 36625809Free PMC Article
Marrouche NF, Wazni O, McGann C, Greene T, Dean JM, Dagher L, Kholmovski E, Mansour M, Marchlinski F, Wilber D, Hindricks G, Mahnkopf C, Wells D, Jais P, Sanders P, Brachmann J, Bax JJ, Morrison-de Boer L, Deneke T, Calkins H, Sohns C, Akoum N; DECAAF II Investigators
JAMA 2022 Jun 21;327(23):2296-2305. doi: 10.1001/jama.2022.8831. PMID: 35727277Free PMC Article
Reddy VY, Dukkipati SR, Neuzil P, Anic A, Petru J, Funasako M, Cochet H, Minami K, Breskovic T, Sikiric I, Sediva L, Chovanec M, Koruth J, Jais P
JACC Clin Electrophysiol 2021 May;7(5):614-627. Epub 2021 Apr 28 doi: 10.1016/j.jacep.2021.02.014. PMID: 33933412
Brachmann J, Sohns C, Andresen D, Siebels J, Sehner S, Boersma L, Merkely B, Pokushalov E, Sanders P, Schunkert H, Bänsch D, Dagher L, Zhao Y, Mahnkopf C, Wegscheider K, Marrouche NF
JACC Clin Electrophysiol 2021 May;7(5):594-603. Epub 2021 Feb 24 doi: 10.1016/j.jacep.2020.11.021. PMID: 33640355
Gawałko M, Balsam P, Lodziński P, Grabowski M, Krzowski B, Opolski G, Kosiuk J
Circ J 2020 Apr 24;84(5):685-694. Epub 2020 Feb 26 doi: 10.1253/circj.CJ-19-0705. PMID: 32101812

Prognosis

Kalman JM, Al-Kaisey AM, Parameswaran R, Hawson J, Anderson RD, Lim M, Chieng D, Joseph SA, McLellan A, Morton JB, Sparks PB, Lee G, Sanders P, Kistler PM
Eur Heart J 2023 Jul 14;44(27):2447-2454. doi: 10.1093/eurheartj/ehad247. PMID: 37062010
Broberg CS, van Dissel A, Minnier J, Aboulhosn J, Kauling RM, Ginde S, Krieger EV, Rodriguez F 3rd, Gupta T, Shah S, John AS, Cotts T, Kay WA, Kuo M, Dwight C, Woods P, Nicolarsen J, Sarubbi B, Fusco F, Antonova P, Fernandes S, Grewal J, Cramer J, Khairy P, Gallego P, O'Donnell C, Hannah J, Dellborg M, Rodriguez-Monserrate CP, Muhll IV, Pylypchuk S, Magalski A, Han F, Lubert AM, Kay J, Yeung E, Roos-Hesselink J, Baker D, Celermajer DS, Burchill LJ, Wilson WM, Wong J, Kutty S, Opotowsky AR
J Am Coll Cardiol 2022 Sep 6;80(10):951-963. doi: 10.1016/j.jacc.2022.06.020. PMID: 36049802
Gawałko M, Balsam P, Lodziński P, Grabowski M, Krzowski B, Opolski G, Kosiuk J
Circ J 2020 Apr 24;84(5):685-694. Epub 2020 Feb 26 doi: 10.1253/circj.CJ-19-0705. PMID: 32101812
Hernandez-Betancor I, Izquierdo-Gomez MM, Garcia-Niebla J, Laynez-Cerdena I, Garcia-Gonzalez MJ, Barragan-Acea A, Irribarren-Sarria JL, Jimenez-Rivera JJ, Lacalzada-Almeida J
Curr Cardiol Rev 2017;13(4):263-273. doi: 10.2174/1573403X13666170713122600. PMID: 28707575Free PMC Article
Marrakchi S, Kanoun F, Idriss S, Kammoun I, Kachboura S
Herz 2015 Apr;40 Suppl 2:101-9. Epub 2014 Jul 4 doi: 10.1007/s00059-014-4123-0. PMID: 24990773

Clinical prediction guides

Cheng A, Qiu J, Barbhaiya C, Garber L, Holmes D, Jankelson L, Kushnir A, Knotts R, Bernstein S, Park D, Spinelli M, Chinitz L, Aizer A
J Cardiovasc Electrophysiol 2023 Mar;34(3):575-582. Epub 2022 Dec 16 doi: 10.1111/jce.15774. PMID: 36511474
Broberg CS, van Dissel A, Minnier J, Aboulhosn J, Kauling RM, Ginde S, Krieger EV, Rodriguez F 3rd, Gupta T, Shah S, John AS, Cotts T, Kay WA, Kuo M, Dwight C, Woods P, Nicolarsen J, Sarubbi B, Fusco F, Antonova P, Fernandes S, Grewal J, Cramer J, Khairy P, Gallego P, O'Donnell C, Hannah J, Dellborg M, Rodriguez-Monserrate CP, Muhll IV, Pylypchuk S, Magalski A, Han F, Lubert AM, Kay J, Yeung E, Roos-Hesselink J, Baker D, Celermajer DS, Burchill LJ, Wilson WM, Wong J, Kutty S, Opotowsky AR
J Am Coll Cardiol 2022 Sep 6;80(10):951-963. doi: 10.1016/j.jacc.2022.06.020. PMID: 36049802
Pensa AV, Baman JR, Puckelwartz MJ, Wilcox JE
J Cardiovasc Electrophysiol 2022 Aug;33(8):1944-1953. Epub 2022 Mar 19 doi: 10.1111/jce.15446. PMID: 35262243
Gawałko M, Balsam P, Lodziński P, Grabowski M, Krzowski B, Opolski G, Kosiuk J
Circ J 2020 Apr 24;84(5):685-694. Epub 2020 Feb 26 doi: 10.1253/circj.CJ-19-0705. PMID: 32101812
Hernandez-Betancor I, Izquierdo-Gomez MM, Garcia-Niebla J, Laynez-Cerdena I, Garcia-Gonzalez MJ, Barragan-Acea A, Irribarren-Sarria JL, Jimenez-Rivera JJ, Lacalzada-Almeida J
Curr Cardiol Rev 2017;13(4):263-273. doi: 10.2174/1573403X13666170713122600. PMID: 28707575Free PMC Article

Recent systematic reviews

Ezzeddine FM, Agboola KM, Hassett LC, Killu AM, Del-Carpio Munoz F, DeSimone CV, Kowlgi GN, Deshmukh AJ, Siontis KC
Europace 2023 Aug 2;25(9) doi: 10.1093/europace/euad256. PMID: 37595138Free PMC Article
Ngo L, Lee XW, Elwashahy M, Arumugam P, Yang IA, Denman R, Haqqani H, Ranasinghe I
Eur Heart J Qual Care Clin Outcomes 2023 Aug 7;9(5):447-458. doi: 10.1093/ehjqcco/qcad037. PMID: 37336617Free PMC Article
Giannone ME, Filippini T, Whelton PK, Chiari A, Vitolo M, Boriani G, Vinceti M
J Am Heart Assoc 2022 Jul 19;11(14):e025653. Epub 2022 Jul 15 doi: 10.1161/JAHA.122.025653. PMID: 35861843Free PMC Article
Turagam MK, Musikantow D, Whang W, Koruth JS, Miller MA, Langan MN, Sofi A, Choudry S, Dukkipati SR, Reddy VY
JAMA Cardiol 2021 Jun 1;6(6):697-705. doi: 10.1001/jamacardio.2021.0852. PMID: 33909022Free PMC Article
Gaeta M, Bandera F, Tassinari F, Capasso L, Cargnelutti M, Pelissero G, Malavazos AE, Ricci C
Europace 2017 May 1;19(5):747-752. doi: 10.1093/europace/euw398. PMID: 28087595

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