Small intestine neuroendocrine neoplasm

MedGen UID:: 233453
•Concept ID:: C1336005
•: Neoplastic Process

Synonyms:	NET of the small intestine; Neuroendocrine neoplasm of small intestine; neuroendocrine neoplasm of small intestine; Neuroendocrine neoplasm of the small intestine; neuroendocrine neoplasm of the small intestine; Neuroendocrine tumor of small bowel; neuroendocrine tumor of small bowel; neuroendocrine tumor of the small intestine; Neuroendocrine tumor of the small intestine; neuroendocrine tumour of small bowel; neuroendocrine tumour of the small intestine; Small Intestinal Neuroendocrine Neoplasm; small intestinal neuroendocrine neoplasm; small intestine NET; Small Intestine Neuroendocrine Neoplasm; small intestine neuroendocrine neoplasm; small intestine neuroendocrine tumor; small intestine neuroendocrine tumor, well differentiated, low or intermediate grade; small intestine neuroendocrine tumour
SNOMED CT:	Neuroendocrine neoplasm of small intestine (1186805005)

Monarch Initiative:	MONDO:0018510
Orphanet:	ORPHA423975

Definition

A neoplasm with neuroendocrine differentiation that arises from the small intestine. It includes neuroendocrine tumors (well-differentiated neuroendocrine neoplasms) and neuroendocrine carcinomas (poorly differentiated neuroendocrine neoplasms). [from NCI]

Term Hierarchy

GTR
MeSH

CClinical test, RResearch test, OOMIM, GGeneReviews, VClinVar

CROGVSmall intestine neuroendocrine neoplasm

Disorder of digestive system
- Abnormality of the digestive system
  - Digestive system neoplasm
    - Neoplasm of the gastrointestinal tract
      - Digestive system neuroendocrine neoplasm
        Intestinal neuroendocrine neoplasm
        Small intestine neuroendocrine neoplasm
        Ileal neuroendocrine tumor, well differentiated, low or intermediate grade
        Ileal Neuroendocrine Tumor by AJCC v8 Stage
        Stage I Ileal Neuroendocrine Tumor AJCC v8
        Stage II Ileal Neuroendocrine Tumor AJCC v8
        Stage III Ileal Neuroendocrine Tumor AJCC v8
        Stage IV Ileal Neuroendocrine Tumor AJCC v8
        Ileal neuroendocrine tumor G1
        Ileal Neuroendocrine Tumor G2
        Ileal Neuroendocrine Tumor G3
        Small Intestinal Neuroendocrine Carcinoma
        Metastatic Small Intestinal Neuroendocrine Carcinoma
        Advanced Small Intestinal Neuroendocrine Carcinoma
        Small Intestinal Large Cell Neuroendocrine Carcinoma
        Advanced Small Intestinal Large Cell Neuroendocrine Carcinoma
        Small Intestinal Small Cell Neuroendocrine Carcinoma
        Advanced Small Intestinal Small Cell Neuroendocrine Carcinoma
        Small intestine neuroendocrine tumor, well differentiated, low or intermediate grade
        Duodenal neuroendocrine tumor, well differentiated, low or intermediate grade
        Duodenal gastrin-producing neuroendocrine tumor
        Duodenal Neuroendocrine Tumor by AJCC v8 Stage
        Duodenal Neuroendocrine Tumor G1
        Duodenal Neuroendocrine Tumor G2
        Duodenal Neuroendocrine Tumor G3
        Duodenal somatostatinoma
        Somatostatinoma
        Zollinger-Ellison syndrome
        Jejunal neuroendocrine tumor, well differentiated, low or intermediate grade
        Jejunal Neuroendocrine Tumor by AJCC v8 Stage
        Jejunal neuroendocrine tumor G1
        Jejunal Neuroendocrine Tumor G2
        Jejunal Neuroendocrine Tumor G3
        Jejunal somatostatinoma
        Small Intestinal Composite Gangliocytoma/Neuroma and Neuroendocrine Tumor
        Small Intestinal Enterochromaffin Cell Serotonin-Producing Neuroendocrine Tumor
        Small Intestinal Gastrin-Producing Neuroendocrine Tumor
        Small intestinal L-cell glucagon-like peptide producing tumor
        Small intestinal neuroendocrine tumor G1
        Small Intestinal Neuroendocrine Tumor G2
        Small Intestinal Neuroendocrine Tumor G3
        Small Intestinal Somatostatin-Producing Neuroendocrine Tumor
        Small intestinal vasoactive intestinal peptide producing tumor

Professional guidelines

PubMed

Updates in the diagnosis and management of small-bowel tumors.

Vlachou E, Koffas A, Toumpanakis C, Keuchel M
Best Pract Res Clin Gastroenterol 2023 Jun-Aug;64-65:101860. Epub 2023 Aug 12 doi: 10.1016/j.bpg.2023.101860. PMID: 37652650

Management of Small Bowel Neuroendocrine Tumors.

Scott AT, Howe JR
Surg Oncol Clin N Am 2020 Apr;29(2):223-241. doi: 10.1016/j.soc.2019.11.006. PMID: 32151357

Management of Small Bowel Neuroendocrine Tumors.

Scott AT, Howe JR
J Oncol Pract 2018 Aug;14(8):471-482. doi: 10.1200/JOP.18.00135. PMID: 30096273 Free PMC Article

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