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Primary cutaneous T-cell lymphoma

MedGen UID:
36336
Concept ID:
C0079773
Neoplastic Process
Synonym: Cutaneous T-cell lymphoma
SNOMED CT: Primary cutaneous T-cell lymphoma (400122007); Cutaneous T-cell lymphoma (400122007); CTCL - Cutaneous T-cell lymphoma (400122007); Cutaneous T-cell lymphoma (1162973007); Cutaneous lymphoma (1162973007); Primary cutaneous T-cell lymphoma (1187136005)
 
HPO: HP:0012192
Monarch Initiative: MONDO:0015758
Orphanet: ORPHA171901

Definition

A type of T-cell lymphoma that exhibits malignant infiltration of the skin. [from HPO]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVPrimary cutaneous T-cell lymphoma
Follow this link to review classifications for Primary cutaneous T-cell lymphoma in Orphanet.

Professional guidelines

PubMed

Porkert S, Griss J, Hudelist-Venz M, Steiner I, Valencak J, Weninger W, Brunner PM, Jonak C
J Dtsch Dermatol Ges 2024 Apr;22(4):532-550. Epub 2024 Mar 5 doi: 10.1111/ddg.15331. PMID: 38444271
Hu M, Scheffel J, Elieh-Ali-Komi D, Maurer M, Hawro T, Metz M
Clin Exp Med 2023 Dec;23(8):4177-4197. Epub 2023 Aug 9 doi: 10.1007/s10238-023-01141-x. PMID: 37555911Free PMC Article
Scarisbrick JJ
Future Oncol 2017 Nov;13(27):2405-2411. Epub 2017 Aug 14 doi: 10.2217/fon-2017-0263. PMID: 28805086

Recent clinical studies

Etiology

Saleh JS, Subtil A, Hristov AC
Hum Pathol 2023 Oct;140:75-100. Epub 2023 Oct 4 doi: 10.1016/j.humpath.2023.09.009. PMID: 37802757
van der Weyden C, McCormack C, Lade S, Johnstone RW, Prince HM
Cancer Treat Res 2019;176:195-224. doi: 10.1007/978-3-319-99716-2_10. PMID: 30596220
Stadler R, Stranzenbach R
Exp Dermatol 2018 Oct;27(10):1078-1083. Epub 2018 Jul 25 doi: 10.1111/exd.13701. PMID: 29862563
Klemke CD
J Dtsch Dermatol Ges 2014 Jan;12(1):7-28; quiz 29-30. doi: 10.1111/ddg.12237. PMID: 24393310
Tomasini D, Berti E
G Ital Dermatol Venereol 2013 Aug;148(4):395-411. PMID: 23900161

Diagnosis

Saleh JS, Subtil A, Hristov AC
Hum Pathol 2023 Oct;140:75-100. Epub 2023 Oct 4 doi: 10.1016/j.humpath.2023.09.009. PMID: 37802757
van der Weyden C, McCormack C, Lade S, Johnstone RW, Prince HM
Cancer Treat Res 2019;176:195-224. doi: 10.1007/978-3-319-99716-2_10. PMID: 30596220
Muñoz-González H, Molina-Ruiz AM, Requena L
Actas Dermosifiliogr 2017 Apr;108(3):192-208. Epub 2016 Nov 18 doi: 10.1016/j.ad.2016.08.009. PMID: 27871620
Jawed SI, Myskowski PL, Horwitz S, Moskowitz A, Querfeld C
J Am Acad Dermatol 2014 Feb;70(2):205.e1-16; quiz 221-2. doi: 10.1016/j.jaad.2013.07.049. PMID: 24438969
Klemke CD
J Dtsch Dermatol Ges 2014 Jan;12(1):7-28; quiz 29-30. doi: 10.1111/ddg.12237. PMID: 24393310

Therapy

Scarisbrick JJ
Future Oncol 2017 Nov;13(27):2405-2411. Epub 2017 Aug 14 doi: 10.2217/fon-2017-0263. PMID: 28805086
Lo Sicco K, Latkowski JA
J Drugs Dermatol 2015 Dec;14(12):1381-3. PMID: 26659928
DeSimone JA, Sodha P, Ignatova D, Dummer R, Cozzio A, Guenova E
Curr Opin Oncol 2015 Mar;27(2):128-33. doi: 10.1097/CCO.0000000000000161. PMID: 25594623
Klemke CD
J Dtsch Dermatol Ges 2014 Jan;12(1):7-28; quiz 29-30. doi: 10.1111/ddg.12237. PMID: 24393310
Tomasini D, Berti E
G Ital Dermatol Venereol 2013 Aug;148(4):395-411. PMID: 23900161

Prognosis

Saleh JS, Subtil A, Hristov AC
Hum Pathol 2023 Oct;140:75-100. Epub 2023 Oct 4 doi: 10.1016/j.humpath.2023.09.009. PMID: 37802757
Rindler K, Jonak C, Alkon N, Thaler FM, Kurz H, Shaw LE, Stingl G, Weninger W, Halbritter F, Bauer WM, Farlik M, Brunner PM
Mol Cancer 2021 Sep 28;20(1):124. doi: 10.1186/s12943-021-01419-2. PMID: 34583709Free PMC Article
Muñoz-González H, Molina-Ruiz AM, Requena L
Actas Dermosifiliogr 2017 Apr;108(3):192-208. Epub 2016 Nov 18 doi: 10.1016/j.ad.2016.08.009. PMID: 27871620
Jawed SI, Myskowski PL, Horwitz S, Moskowitz A, Querfeld C
J Am Acad Dermatol 2014 Feb;70(2):205.e1-16; quiz 221-2. doi: 10.1016/j.jaad.2013.07.049. PMID: 24438969
Klemke CD
J Dtsch Dermatol Ges 2014 Jan;12(1):7-28; quiz 29-30. doi: 10.1111/ddg.12237. PMID: 24393310

Clinical prediction guides

Hu M, Scheffel J, Frischbutter S, Steinert C, Reidel U, Spindler M, Przybyłowicz K, Hawro M, Maurer M, Metz M, Hawro T
Clin Exp Med 2024 Jul 28;24(1):171. doi: 10.1007/s10238-024-01407-y. PMID: 39068637Free PMC Article
Porkert S, Griss J, Hudelist-Venz M, Steiner I, Valencak J, Weninger W, Brunner PM, Jonak C
J Dtsch Dermatol Ges 2024 Apr;22(4):532-550. Epub 2024 Mar 5 doi: 10.1111/ddg.15331. PMID: 38444271
Manta AI, Wilson-Pogmore AA, Sullivan TJ
Ophthalmic Plast Reconstr Surg 2023 May-Jun 01;39(3):266-274. Epub 2023 Jan 24 doi: 10.1097/IOP.0000000000002309. PMID: 36727764
Rindler K, Jonak C, Alkon N, Thaler FM, Kurz H, Shaw LE, Stingl G, Weninger W, Halbritter F, Bauer WM, Farlik M, Brunner PM
Mol Cancer 2021 Sep 28;20(1):124. doi: 10.1186/s12943-021-01419-2. PMID: 34583709Free PMC Article
Ruiz R, Morante Z, Mantilla R, Mas L, Casanova L, Gomez HL
An Bras Dermatol 2017 Sep-Oct;92(5):649-654. doi: 10.1590/abd1806-4841.20176825. PMID: 29166501Free PMC Article

Recent systematic reviews

Beynon T, Radcliffe E, Child F, Orlowska D, Whittaker S, Lawson S, Selman L, Harding R
Br J Dermatol 2014 Mar;170(3):599-608. doi: 10.1111/bjd.12644. PMID: 24116897
Schlaak M, Pickenhain J, Theurich S, Skoetz N, von Bergwelt-Baildon M, Kurschat P
Cochrane Database Syst Rev 2013 Aug 29;2013(8):CD008908. doi: 10.1002/14651858.CD008908.pub3. PMID: 23986525Free PMC Article
Schlaak M, Theurich S, Pickenhain J, Skoetz N, Kurschat P, von Bergwelt-Baildon M
Crit Rev Oncol Hematol 2013 Jan;85(1):21-31. Epub 2012 Jul 18 doi: 10.1016/j.critrevonc.2012.06.002. PMID: 22819279
Schlaak M, Pickenhain J, Theurich S, Skoetz N, von Bergwelt-Baildon M, Kurschat P
Cochrane Database Syst Rev 2012 Jan 18;1:CD008908. doi: 10.1002/14651858.CD008908.pub2. PMID: 22258991

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