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Abnormal cardiac ventricle morphology

MedGen UID:
871266
•Concept ID:
C4025752
•
Anatomical Abnormality
Synonym: Abnormality of cardiac ventricle
 
HPO: HP:0001713

Definition

An abnormality of a cardiac ventricle. [from HPO]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVAbnormal cardiac ventricle morphology

Professional guidelines

PubMed

Prenatal Diagnosis and Management of Single-Ventricle Heart Disease.
Freud LR, Seed M
Can J Cardiol 2022 Jul;38(7):897-908. Epub 2022 Apr 13 doi: 10.1016/j.cjca.2022.04.003. PMID: 35429589
Molecular Approaches in Single Ventricle Management.
Toubat O, Kumar SR
Semin Thorac Cardiovasc Surg Pediatr Card Surg Annu 2020;23:77-85. doi: 10.1053/j.pcsu.2020.03.003. PMID: 32354551Free PMC Article
Prenatal diagnosis of congenital heart disease: A review of current knowledge.
Bravo-Valenzuela NJ, Peixoto AB, Araujo Júnior E
Indian Heart J 2018 Jan-Feb;70(1):150-164. Epub 2017 Dec 16 doi: 10.1016/j.ihj.2017.12.005. PMID: 29455772Free PMC Article

Recent clinical studies

Etiology

Surgical Strategies in Single Ventricle Management of Neonates and Infants.
Haller C, Barron DJ
Can J Cardiol 2022 Jul;38(7):909-920. Epub 2022 May 2 doi: 10.1016/j.cjca.2022.04.021. PMID: 35513174
Being born with a single cardiac ventricle: What do we tell prospective parents.
d'Udekem Y, Hutchinson D
Prenat Diagn 2022 Apr;42(4):411-418. Epub 2022 Apr 7 doi: 10.1002/pd.6121. PMID: 35278231
Right ventricular pseudoaneurysm.
Sakaguchi T, Akagi S, Totsugawa T, Tamura K, Hiraoka A
Eur Heart J Cardiovasc Imaging 2018 Jul 1;19(7):823. doi: 10.1093/ehjci/jey033. PMID: 29481582
Origins and consequences of congenital heart defects affecting the right ventricle.
Woudstra OI, Ahuja S, Bokma JP, Bouma BJ, Mulder BJM, Christoffels VM
Cardiovasc Res 2017 Oct 1;113(12):1509-1520. doi: 10.1093/cvr/cvx155. PMID: 28957538
Cell Therapy Trials in Congenital Heart Disease.
Oh H
Circ Res 2017 Apr 14;120(8):1353-1366. doi: 10.1161/CIRCRESAHA.117.309697. PMID: 28408455

Diagnosis

Surgical Strategies in Single Ventricle Management of Neonates and Infants.
Haller C, Barron DJ
Can J Cardiol 2022 Jul;38(7):909-920. Epub 2022 May 2 doi: 10.1016/j.cjca.2022.04.021. PMID: 35513174
Molecular Approaches in Single Ventricle Management.
Toubat O, Kumar SR
Semin Thorac Cardiovasc Surg Pediatr Card Surg Annu 2020;23:77-85. doi: 10.1053/j.pcsu.2020.03.003. PMID: 32354551Free PMC Article
Cardiac imaging in Ebstein anomaly.
Qureshi MY, O'Leary PW, Connolly HM
Trends Cardiovasc Med 2018 Aug;28(6):403-409. Epub 2018 Jan 12 doi: 10.1016/j.tcm.2018.01.002. PMID: 29409687
Quadrichambered ventricles.
Akdemir R, Balci MM, Ozer C, Karcaaltincaba M, Acikel S
Cardiol J 2010;17(3):303-5. PMID: 20535723
Aorto-ventricular tunnel.
McKay R
Orphanet J Rare Dis 2007 Oct 8;2:41. doi: 10.1186/1750-1172-2-41. PMID: 17922908Free PMC Article

Therapy

The Secrets of the Frogs Heart.
Corno AF, Zhou Z, Uppu SC, Huang S, Marino B, Milewicz DM, Salazar JD
Pediatr Cardiol 2022 Oct;43(7):1471-1480. Epub 2022 Mar 15 doi: 10.1007/s00246-022-02870-8. PMID: 35290490
Heart failure in single right ventricle congenital heart disease: physiological and molecular considerations.
Garcia AM, Beatty JT, Nakano SJ
Am J Physiol Heart Circ Physiol 2020 Apr 1;318(4):H947-H965. Epub 2020 Feb 28 doi: 10.1152/ajpheart.00518.2019. PMID: 32108525Free PMC Article
The Bioengineered Cardiac Left Ventricle.
Patel NM, Birla RK
ASAIO J 2018 Jan/Feb;64(1):56-62. doi: 10.1097/MAT.0000000000000642. PMID: 28863042
Cell Therapy Trials in Congenital Heart Disease.
Oh H
Circ Res 2017 Apr 14;120(8):1353-1366. doi: 10.1161/CIRCRESAHA.117.309697. PMID: 28408455
Current Therapy for Hypoplastic Left Heart Syndrome and Related Single Ventricle Lesions.
Ohye RG, Schranz D, D'Udekem Y
Circulation 2016 Oct 25;134(17):1265-1279. doi: 10.1161/CIRCULATIONAHA.116.022816. PMID: 27777296Free PMC Article

Prognosis

Molecular Approaches in Single Ventricle Management.
Toubat O, Kumar SR
Semin Thorac Cardiovasc Surg Pediatr Card Surg Annu 2020;23:77-85. doi: 10.1053/j.pcsu.2020.03.003. PMID: 32354551Free PMC Article
Cardiac imaging in Ebstein anomaly.
Qureshi MY, O'Leary PW, Connolly HM
Trends Cardiovasc Med 2018 Aug;28(6):403-409. Epub 2018 Jan 12 doi: 10.1016/j.tcm.2018.01.002. PMID: 29409687
Current Therapy for Hypoplastic Left Heart Syndrome and Related Single Ventricle Lesions.
Ohye RG, Schranz D, D'Udekem Y
Circulation 2016 Oct 25;134(17):1265-1279. doi: 10.1161/CIRCULATIONAHA.116.022816. PMID: 27777296Free PMC Article
Cat eye syndrome.
Sharma D, Murki S, Pratap T, Vasikarla M
BMJ Case Rep 2014 May 19;2014 doi: 10.1136/bcr-2014-203923. PMID: 24842361Free PMC Article
Complex atrioventricular canal.
Mitchell ME, Litwin SB, Tweddell JS
Semin Thorac Cardiovasc Surg Pediatr Card Surg Annu 2007:32-41. doi: 10.1053/j.pcsu.2007.01.002. PMID: 17433989

Clinical prediction guides

Dominant Ventricular Morphology and Early Postoperative Course After the Fontan Procedure.
Pollak U, Abarbanel I, Salem Y, Serraf AE, Mishaly D
World J Pediatr Congenit Heart Surg 2022 May;13(3):346-352. doi: 10.1177/21501351221081246. PMID: 35446208Free PMC Article
Coronary-Cameral Fistula.
Boyle S, Jesuthasan LSB, Jenkins C, Challa P, Ranjan S, Dahiya A
Circ Cardiovasc Imaging 2019 May;12(5):e008691. doi: 10.1161/CIRCIMAGING.118.008691. PMID: 31088151
Cardiac imaging in Ebstein anomaly.
Qureshi MY, O'Leary PW, Connolly HM
Trends Cardiovasc Med 2018 Aug;28(6):403-409. Epub 2018 Jan 12 doi: 10.1016/j.tcm.2018.01.002. PMID: 29409687
Double-chambered right ventricle: a review.
Loukas M, Housman B, Blaak C, Kralovic S, Tubbs RS, Anderson RH
Cardiovasc Pathol 2013 Nov-Dec;22(6):417-23. Epub 2013 May 20 doi: 10.1016/j.carpath.2013.03.004. PMID: 23701985
Aorto-ventricular tunnel.
McKay R
Orphanet J Rare Dis 2007 Oct 8;2:41. doi: 10.1186/1750-1172-2-41. PMID: 17922908Free PMC Article

Recent systematic reviews

Electrocardiographic Predictors of Atrial Fibrillation.
Chousou PA, Chattopadhyay R, Tsampasian V, Vassiliou VS, Pugh PJ
Med Sci (Basel) 2023 Apr 7;11(2) doi: 10.3390/medsci11020030. PMID: 37092499Free PMC Article
Double-chambered Right Ventricle in Children.
Yuan SM
J Coll Physicians Surg Pak 2019 Dec;29(12):1193-1198. doi: 10.29271/jcpsp.2019.12.1193. PMID: 31839094
How often an isolated cardiac disproportion predicts a coarctation of the aorta? Single center experience and systematic review of the literature.
Ghi T, Dall'Asta A, Cavalli C, Galli L, Weiss A, Pedrazzi G, Kaihura CT, Volpe N, Agnetti A, Frusca T
J Matern Fetal Neonatal Med 2018 May;31(10):1350-1357. Epub 2017 Apr 20 doi: 10.1080/14767058.2017.1314459. PMID: 28366040
Comparison of extracardiac conduit and lateral tunnel for functional single-ventricle patients: A meta-analysis.
Lin Z, Ge H, Xue J, Wu G, Du J, Hu X, Zhao Q
Congenit Heart Dis 2017 Dec;12(6):711-720. Epub 2017 Aug 28 doi: 10.1111/chd.12503. PMID: 28845580
Complex Ebstein's malformation: defining preoperative cardiac anatomy and function.
Negoi RI, Ispas AT, Ghiorghiu I, Filipoiu F, Negoi I, Hostiuc M, Hostiuc S, Ginghina C
J Card Surg 2013 Jan;28(1):70-81. doi: 10.1111/jocs.12032. PMID: 23330581

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