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Plasma cell neoplasm

MedGen UID:
368758
Concept ID:
C1959632
Neoplastic Process
Synonyms: Neoplasm, Plasma Cell; Neoplasms, Plasma Cell; Plasma Cell Neoplasm; Plasma Cell Neoplasms
SNOMED CT: Plasma cell neoplasm (415111003); Plasma cell neoplasm (127580003); Plasma cell neoplasm (morphology) (127580003)
 
Monarch Initiative: MONDO:0004959
Orphanet: ORPHA98282

Definition

A clonal proliferation of immunoglobulin-secreting plasma cells. This category includes plasma cell myeloma, plasma cell leukemia, plasmacytoma, monoclonal immunoglobulin deposition disease, and monoclonal gammopathy of undetermined significance. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVPlasma cell neoplasm

Professional guidelines

PubMed

Dispenzieri A
Am J Hematol 2023 Dec;98(12):1934-1950. Epub 2023 Sep 21 doi: 10.1002/ajh.27081. PMID: 37732822
Dispenzieri A
Am J Hematol 2021 Jul 1;96(7):872-888. Epub 2021 May 31 doi: 10.1002/ajh.26240. PMID: 34000085
Dispenzieri A
Am J Hematol 2019 Jul;94(7):812-827. Epub 2019 May 23 doi: 10.1002/ajh.25495. PMID: 31012139

Recent clinical studies

Etiology

Shah UA, Parikh R, Castro F, Bellone M, Lesokhin AM
Leukemia 2023 May;37(5):964-980. Epub 2023 Mar 30 doi: 10.1038/s41375-023-01874-4. PMID: 36997677Free PMC Article
Dispenzieri A
Am J Hematol 2021 Jul 1;96(7):872-888. Epub 2021 May 31 doi: 10.1002/ajh.26240. PMID: 34000085
Liu MC, Oxnard GR, Klein EA, Swanton C, Seiden MV; CCGA Consortium
Ann Oncol 2020 Jun;31(6):745-759. Epub 2020 Mar 30 doi: 10.1016/j.annonc.2020.02.011. PMID: 33506766Free PMC Article
Castaneda O, Baz R
Acta Med Acad 2019 Apr;48(1):57-67. doi: 10.5644/ama2006-124.242. PMID: 31264433
Dispenzieri A
Am J Hematol 2019 Jul;94(7):812-827. Epub 2019 May 23 doi: 10.1002/ajh.25495. PMID: 31012139

Diagnosis

Shah UA, Parikh R, Castro F, Bellone M, Lesokhin AM
Leukemia 2023 May;37(5):964-980. Epub 2023 Mar 30 doi: 10.1038/s41375-023-01874-4. PMID: 36997677Free PMC Article
Dispenzieri A
Am J Hematol 2021 Jul 1;96(7):872-888. Epub 2021 May 31 doi: 10.1002/ajh.26240. PMID: 34000085
Liu MC, Oxnard GR, Klein EA, Swanton C, Seiden MV; CCGA Consortium
Ann Oncol 2020 Jun;31(6):745-759. Epub 2020 Mar 30 doi: 10.1016/j.annonc.2020.02.011. PMID: 33506766Free PMC Article
Castaneda O, Baz R
Acta Med Acad 2019 Apr;48(1):57-67. doi: 10.5644/ama2006-124.242. PMID: 31264433
Dispenzieri A
Am J Hematol 2019 Jul;94(7):812-827. Epub 2019 May 23 doi: 10.1002/ajh.25495. PMID: 31012139

Therapy

Mahadevia H, Ponvilawan B, Sharma P, Al-Obaidi A, Qasim H, Koyi J, Anwer F, Raza S
Crit Rev Oncol Hematol 2023 Mar;183:103917. Epub 2023 Jan 22 doi: 10.1016/j.critrevonc.2023.103917. PMID: 36696931
Frigault MJ, Bishop MR, Rosenblatt J, O'Donnell EK, Raje N, Cook D, Yee AJ, Logan E, Avigan DE, Jakubowiak A, Shaw K, Daley H, Nikiforow S, Griffin F, Cornwell C, Shen A, Heery C, Maus MV
Blood Adv 2023 Mar 14;7(5):768-777. doi: 10.1182/bloodadvances.2022007210. PMID: 35468618Free PMC Article
Dispenzieri A
Am J Hematol 2019 Jul;94(7):812-827. Epub 2019 May 23 doi: 10.1002/ajh.25495. PMID: 31012139
Cowan AJ, Allen C, Barac A, Basaleem H, Bensenor I, Curado MP, Foreman K, Gupta R, Harvey J, Hosgood HD, Jakovljevic M, Khader Y, Linn S, Lad D, Mantovani L, Nong VM, Mokdad A, Naghavi M, Postma M, Roshandel G, Shackelford K, Sisay M, Nguyen CT, Tran TT, Xuan BT, Ukwaja KN, Vollset SE, Weiderpass E, Libby EN, Fitzmaurice C
JAMA Oncol 2018 Sep 1;4(9):1221-1227. doi: 10.1001/jamaoncol.2018.2128. PMID: 29800065Free PMC Article
Diamond E, Lahoud OB, Landau H
Leuk Lymphoma 2018 Jun;59(6):1300-1311. Epub 2017 Aug 28 doi: 10.1080/10428194.2017.1365859. PMID: 28847191Free PMC Article

Prognosis

Clarke SE, Fuller KA, Erber WN
Blood Rev 2024 Mar;64:101168. Epub 2024 Jan 4 doi: 10.1016/j.blre.2024.101168. PMID: 38212176
Alejo E, Puertas B, Mateos MV
Med Clin (Barc) 2023 Sep 8;161(5):217-224. Epub 2023 Jun 15 doi: 10.1016/j.medcli.2023.05.006. PMID: 37330390
Liu MC, Oxnard GR, Klein EA, Swanton C, Seiden MV; CCGA Consortium
Ann Oncol 2020 Jun;31(6):745-759. Epub 2020 Mar 30 doi: 10.1016/j.annonc.2020.02.011. PMID: 33506766Free PMC Article
Castaneda O, Baz R
Acta Med Acad 2019 Apr;48(1):57-67. doi: 10.5644/ama2006-124.242. PMID: 31264433
Cowan AJ, Allen C, Barac A, Basaleem H, Bensenor I, Curado MP, Foreman K, Gupta R, Harvey J, Hosgood HD, Jakovljevic M, Khader Y, Linn S, Lad D, Mantovani L, Nong VM, Mokdad A, Naghavi M, Postma M, Roshandel G, Shackelford K, Sisay M, Nguyen CT, Tran TT, Xuan BT, Ukwaja KN, Vollset SE, Weiderpass E, Libby EN, Fitzmaurice C
JAMA Oncol 2018 Sep 1;4(9):1221-1227. doi: 10.1001/jamaoncol.2018.2128. PMID: 29800065Free PMC Article

Clinical prediction guides

Frigault MJ, Bishop MR, Rosenblatt J, O'Donnell EK, Raje N, Cook D, Yee AJ, Logan E, Avigan DE, Jakubowiak A, Shaw K, Daley H, Nikiforow S, Griffin F, Cornwell C, Shen A, Heery C, Maus MV
Blood Adv 2023 Mar 14;7(5):768-777. doi: 10.1182/bloodadvances.2022007210. PMID: 35468618Free PMC Article
Liu MC, Oxnard GR, Klein EA, Swanton C, Seiden MV; CCGA Consortium
Ann Oncol 2020 Jun;31(6):745-759. Epub 2020 Mar 30 doi: 10.1016/j.annonc.2020.02.011. PMID: 33506766Free PMC Article
Castaneda O, Baz R
Acta Med Acad 2019 Apr;48(1):57-67. doi: 10.5644/ama2006-124.242. PMID: 31264433
Altindag SD, Cakir E, Ekinci N, Avci A, Dilek FH
Ann Diagn Pathol 2019 Jun;40:66-71. Epub 2019 Apr 3 doi: 10.1016/j.anndiagpath.2019.04.003. PMID: 31031217
Bain BJ, Ahmad S
Br J Haematol 2015 Nov;171(3):400-10. Epub 2015 Jul 27 doi: 10.1111/bjh.13600. PMID: 26218186

Recent systematic reviews

Venkatesulu B, Mallick S, Giridhar P, Upadhyay AD, Rath GK
Eur Arch Otorhinolaryngol 2018 Feb;275(2):595-606. Epub 2017 Dec 9 doi: 10.1007/s00405-017-4817-z. PMID: 29224044

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