U.S. flag

An official website of the United States government

Format

Send to:

Choose Destination

Low grade glioma

MedGen UID:
744283
Concept ID:
C1997217
Neoplastic Process
Synonym: Low-grade glioma
SNOMED CT: Low grade glioma (428954009); Low-grade glioma (428954009)
 
Monarch Initiative: MONDO:0021637

Definition

A grade I or grade II glioma arising from the central nervous system. This category includes pilocytic astrocytoma, diffuse astrocytoma, subependymal giant cell astrocytoma, ependymoma, oligodendroglioma, oligoastrocytoma, and angiocentric glioma. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVLow grade glioma

Professional guidelines

PubMed

Pollack IF, Agnihotri S, Broniscer A
J Neurosurg Pediatr 2019 Mar 1;23(3):261-273. doi: 10.3171/2018.10.PEDS18377. PMID: 30835699Free PMC Article
de Blank P, Bandopadhayay P, Haas-Kogan D, Fouladi M, Fangusaro J
Curr Opin Pediatr 2019 Feb;31(1):21-27. doi: 10.1097/MOP.0000000000000717. PMID: 30531227Free PMC Article
Wang TJC, Mehta MP
Neurosurg Clin N Am 2019 Jan;30(1):111-118. Epub 2018 Nov 1 doi: 10.1016/j.nec.2018.08.008. PMID: 30470398

Curated

NCCN Clinical Practice Guidelines in Oncology (NCCN Guidelines®) Central Nervous System Cancers, 2023

Recent clinical studies

Etiology

Wen PY, Stein A, van den Bent M, De Greve J, Wick A, de Vos FYFL, von Bubnoff N, van Linde ME, Lai A, Prager GW, Campone M, Fasolo A, Lopez-Martin JA, Kim TM, Mason WP, Hofheinz RD, Blay JY, Cho DC, Gazzah A, Pouessel D, Yachnin J, Boran A, Burgess P, Ilankumaran P, Gasal E, Subbiah V
Lancet Oncol 2022 Jan;23(1):53-64. Epub 2021 Nov 24 doi: 10.1016/S1470-2045(21)00578-7. PMID: 34838156
Ryall S, Tabori U, Hawkins C
Acta Neuropathol Commun 2020 Mar 12;8(1):30. doi: 10.1186/s40478-020-00902-z. PMID: 32164789Free PMC Article
Fangusaro J, Onar-Thomas A, Young Poussaint T, Wu S, Ligon AH, Lindeman N, Banerjee A, Packer RJ, Kilburn LB, Goldman S, Pollack IF, Qaddoumi I, Jakacki RI, Fisher PG, Dhall G, Baxter P, Kreissman SG, Stewart CF, Jones DTW, Pfister SM, Vezina G, Stern JS, Panigrahy A, Patay Z, Tamrazi B, Jones JY, Haque SS, Enterline DS, Cha S, Fisher MJ, Doyle LA, Smith M, Dunkel IJ, Fouladi M
Lancet Oncol 2019 Jul;20(7):1011-1022. Epub 2019 May 28 doi: 10.1016/S1470-2045(19)30277-3. PMID: 31151904Free PMC Article
Chua J, Nafziger E, Leung D
Curr Oncol Rep 2019 Mar 5;21(4):30. doi: 10.1007/s11912-019-0783-5. PMID: 30835007
Kumthekar P, Raizer J, Singh S
Cancer Treat Res 2015;163:75-87. doi: 10.1007/978-3-319-12048-5_5. PMID: 25468226

Diagnosis

Deshmukh R, Allega MF, Tardito S
Trends Mol Med 2021 Nov;27(11):1045-1059. Epub 2021 Sep 3 doi: 10.1016/j.molmed.2021.07.011. PMID: 34489164
Li G, Wu F, Zeng F, Zhai Y, Feng Y, Chang Y, Wang D, Jiang T, Zhang W
CNS Neurosci Ther 2021 Feb;27(2):186-195. Epub 2020 Oct 16 doi: 10.1111/cns.13464. PMID: 33063446Free PMC Article
Ryall S, Tabori U, Hawkins C
Acta Neuropathol Commun 2020 Mar 12;8(1):30. doi: 10.1186/s40478-020-00902-z. PMID: 32164789Free PMC Article
Fangusaro J, Onar-Thomas A, Young Poussaint T, Wu S, Ligon AH, Lindeman N, Banerjee A, Packer RJ, Kilburn LB, Goldman S, Pollack IF, Qaddoumi I, Jakacki RI, Fisher PG, Dhall G, Baxter P, Kreissman SG, Stewart CF, Jones DTW, Pfister SM, Vezina G, Stern JS, Panigrahy A, Patay Z, Tamrazi B, Jones JY, Haque SS, Enterline DS, Cha S, Fisher MJ, Doyle LA, Smith M, Dunkel IJ, Fouladi M
Lancet Oncol 2019 Jul;20(7):1011-1022. Epub 2019 May 28 doi: 10.1016/S1470-2045(19)30277-3. PMID: 31151904Free PMC Article
Chua J, Nafziger E, Leung D
Curr Oncol Rep 2019 Mar 5;21(4):30. doi: 10.1007/s11912-019-0783-5. PMID: 30835007

Therapy

Mellinghoff IK, van den Bent MJ, Blumenthal DT, Touat M, Peters KB, Clarke J, Mendez J, Yust-Katz S, Welsh L, Mason WP, Ducray F, Umemura Y, Nabors B, Holdhoff M, Hottinger AF, Arakawa Y, Sepulveda JM, Wick W, Soffietti R, Perry JR, Giglio P, de la Fuente M, Maher EA, Schoenfeld S, Zhao D, Pandya SS, Steelman L, Hassan I, Wen PY, Cloughesy TF; INDIGO Trial Investigators
N Engl J Med 2023 Aug 17;389(7):589-601. Epub 2023 Jun 4 doi: 10.1056/NEJMoa2304194. PMID: 37272516
Wen PY, Stein A, van den Bent M, De Greve J, Wick A, de Vos FYFL, von Bubnoff N, van Linde ME, Lai A, Prager GW, Campone M, Fasolo A, Lopez-Martin JA, Kim TM, Mason WP, Hofheinz RD, Blay JY, Cho DC, Gazzah A, Pouessel D, Yachnin J, Boran A, Burgess P, Ilankumaran P, Gasal E, Subbiah V
Lancet Oncol 2022 Jan;23(1):53-64. Epub 2021 Nov 24 doi: 10.1016/S1470-2045(21)00578-7. PMID: 34838156
Ryall S, Tabori U, Hawkins C
Acta Neuropathol Commun 2020 Mar 12;8(1):30. doi: 10.1186/s40478-020-00902-z. PMID: 32164789Free PMC Article
Pollack IF, Agnihotri S, Broniscer A
J Neurosurg Pediatr 2019 Mar 1;23(3):261-273. doi: 10.3171/2018.10.PEDS18377. PMID: 30835699Free PMC Article
Wang TJC, Mehta MP
Neurosurg Clin N Am 2019 Jan;30(1):111-118. Epub 2018 Nov 1 doi: 10.1016/j.nec.2018.08.008. PMID: 30470398

Prognosis

Zhang N, Zhang H, Wu W, Zhou R, Li S, Wang Z, Dai Z, Zhang L, Liu F, Liu Z, Zhang J, Luo P, Liu Z, Cheng Q
Theranostics 2022;12(13):5931-5948. Epub 2022 Aug 8 doi: 10.7150/thno.74281. PMID: 35966587Free PMC Article
Zhang Y, Yang X, Zhu XL, Bai H, Wang ZZ, Zhang JJ, Hao CY, Duan HB
Aging (Albany NY) 2021 Jun 8;13(11):15459-15478. doi: 10.18632/aging.203103. PMID: 34148033Free PMC Article
Li G, Wu F, Zeng F, Zhai Y, Feng Y, Chang Y, Wang D, Jiang T, Zhang W
CNS Neurosci Ther 2021 Feb;27(2):186-195. Epub 2020 Oct 16 doi: 10.1111/cns.13464. PMID: 33063446Free PMC Article
Wang TJC, Mehta MP
Neurosurg Clin N Am 2019 Jan;30(1):111-118. Epub 2018 Nov 1 doi: 10.1016/j.nec.2018.08.008. PMID: 30470398
Buckner JC, Shaw EG, Pugh SL, Chakravarti A, Gilbert MR, Barger GR, Coons S, Ricci P, Bullard D, Brown PD, Stelzer K, Brachman D, Suh JH, Schultz CJ, Bahary JP, Fisher BJ, Kim H, Murtha AD, Bell EH, Won M, Mehta MP, Curran WJ Jr
N Engl J Med 2016 Apr 7;374(14):1344-55. doi: 10.1056/NEJMoa1500925. PMID: 27050206Free PMC Article

Clinical prediction guides

Zhang N, Zhang H, Wu W, Zhou R, Li S, Wang Z, Dai Z, Zhang L, Liu F, Liu Z, Zhang J, Luo P, Liu Z, Cheng Q
Theranostics 2022;12(13):5931-5948. Epub 2022 Aug 8 doi: 10.7150/thno.74281. PMID: 35966587Free PMC Article
Li G, Wu F, Zeng F, Zhai Y, Feng Y, Chang Y, Wang D, Jiang T, Zhang W
CNS Neurosci Ther 2021 Feb;27(2):186-195. Epub 2020 Oct 16 doi: 10.1111/cns.13464. PMID: 33063446Free PMC Article
Fangusaro J, Onar-Thomas A, Young Poussaint T, Wu S, Ligon AH, Lindeman N, Banerjee A, Packer RJ, Kilburn LB, Goldman S, Pollack IF, Qaddoumi I, Jakacki RI, Fisher PG, Dhall G, Baxter P, Kreissman SG, Stewart CF, Jones DTW, Pfister SM, Vezina G, Stern JS, Panigrahy A, Patay Z, Tamrazi B, Jones JY, Haque SS, Enterline DS, Cha S, Fisher MJ, Doyle LA, Smith M, Dunkel IJ, Fouladi M
Lancet Oncol 2019 Jul;20(7):1011-1022. Epub 2019 May 28 doi: 10.1016/S1470-2045(19)30277-3. PMID: 31151904Free PMC Article
Chua J, Nafziger E, Leung D
Curr Oncol Rep 2019 Mar 5;21(4):30. doi: 10.1007/s11912-019-0783-5. PMID: 30835007
Wang TJC, Mehta MP
Neurosurg Clin N Am 2019 Jan;30(1):111-118. Epub 2018 Nov 1 doi: 10.1016/j.nec.2018.08.008. PMID: 30470398

Recent systematic reviews

Sherman SJ, Tanaka R, Qaddoumi I
J Psychiatr Res 2022 Apr;148:240-249. Epub 2022 Feb 2 doi: 10.1016/j.jpsychires.2022.01.056. PMID: 35149436
Seyedmirzaei H, Shobeiri P, Turgut M, Hanaei S, Rezaei N
Rev Neurosci 2021 Feb 23;32(2):191-202. Epub 2020 Nov 2 doi: 10.1515/revneuro-2020-0062. PMID: 33125340
Lawrie TA, Gillespie D, Dowswell T, Evans J, Erridge S, Vale L, Kernohan A, Grant R
Cochrane Database Syst Rev 2019 Aug 5;8(8):CD013047. doi: 10.1002/14651858.CD013047.pub2. PMID: 31425631Free PMC Article
Yang M, Guo W, Yang C, Tang J, Huang Q, Feng S, Jiang A, Xu X, Jiang G
PLoS One 2017;12(5):e0175136. Epub 2017 May 4 doi: 10.1371/journal.pone.0175136. PMID: 28472042Free PMC Article
Koekkoek JA, Kerkhof M, Dirven L, Heimans JJ, Reijneveld JC, Taphoorn MJ
Neuro Oncol 2015 Jul;17(7):924-34. Epub 2015 Mar 25 doi: 10.1093/neuonc/nov032. PMID: 25813469Free PMC Article

Supplemental Content

Table of contents

    Clinical resources

    Practice guidelines

    • PubMed
      See practice and clinical guidelines in PubMed. The search results may include broader topics and may not capture all published guidelines. See the FAQ for details.
    • Bookshelf
      See practice and clinical guidelines in NCBI Bookshelf. The search results may include broader topics and may not capture all published guidelines. See the FAQ for details.

    Curated

    • NCCN, 2023
      NCCN Clinical Practice Guidelines in Oncology (NCCN Guidelines®) Central Nervous System Cancers, 2023

    Consumer resources

    Recent activity

    Your browsing activity is empty.

    Activity recording is turned off.

    Turn recording back on

    See more...