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Sensorineural hearing loss disorder

MedGen UID:
9164
Concept ID:
C0018784
Disease or Syndrome
Synonyms: Sensorineural hearing impairment; Sensorineural hearing loss
SNOMED CT: Sensorineural hearing loss (60700002); Sensorineural deafness (60700002); Neurosensory deafness (60700002); Perceptive hearing loss (60700002); Perceptive deafness (60700002); SND - Sensorineural deafness (60700002); Sensory-neural deafness (60700002); Sensory-neural hearing loss (60700002); SNHL - Sensorineural hearing loss (60700002); PD - Perceptive deafness (60700002)
 
HPO: HP:0000407
Monarch Initiative: MONDO:0020678

Definition

A type of hearing impairment in one or both ears related to an abnormal functionality of the cochlear nerve. [from HPO]

Conditions with this feature

Professional guidelines

PubMed

Kashtan CE
Am J Kidney Dis 2021 Feb;77(2):272-279. Epub 2020 Jul 22 doi: 10.1053/j.ajkd.2020.03.026. PMID: 32712016
Basura GJ, Adams ME, Monfared A, Schwartz SR, Antonelli PJ, Burkard R, Bush ML, Bykowski J, Colandrea M, Derebery J, Kelly EA, Kerber KA, Koopman CF, Kuch AA, Marcolini E, McKinnon BJ, Ruckenstein MJ, Valenzuela CV, Vosooney A, Walsh SA, Nnacheta LC, Dhepyasuwan N, Buchanan EM
Otolaryngol Head Neck Surg 2020 Apr;162(2_suppl):S1-S55. doi: 10.1177/0194599820909438. PMID: 32267799
Chandrasekhar SS, Tsai Do BS, Schwartz SR, Bontempo LJ, Faucett EA, Finestone SA, Hollingsworth DB, Kelley DM, Kmucha ST, Moonis G, Poling GL, Roberts JK, Stachler RJ, Zeitler DM, Corrigan MD, Nnacheta LC, Satterfield L
Otolaryngol Head Neck Surg 2019 Aug;161(1_suppl):S1-S45. doi: 10.1177/0194599819859885. PMID: 31369359

Recent clinical studies

Etiology

Young YH
Int J Audiol 2020 Apr;59(4):243-253. Epub 2019 Nov 12 doi: 10.1080/14992027.2019.1689432. PMID: 31714154
Furlano M, Arlandis R, Venegas MDP, Novelli S, Crespi J, Bullich G, Ayasreh N, Remacha Á, Ruiz P, Lorente L, Ballarín J, Matamala A, Ars E, Torra R
Nefrologia (Engl Ed) 2019 Mar-Apr;39(2):133-140. Epub 2018 Nov 22 doi: 10.1016/j.nefro.2018.08.008. PMID: 30471777
Blacker CJ
Am J Psychiatry 2017 May 1;174(5):419-420. doi: 10.1176/appi.ajp.2017.17020153. PMID: 28457158
Aviv U, Ben Ner D, Sharif N, Gur Z, Achiron A
Isr Med Assoc J 2017 Jan;19(1):49-54. PMID: 28457115
Braverman NE, Raymond GV, Rizzo WB, Moser AB, Wilkinson ME, Stone EM, Steinberg SJ, Wangler MF, Rush ET, Hacia JG, Bose M
Mol Genet Metab 2016 Mar;117(3):313-21. Epub 2015 Dec 23 doi: 10.1016/j.ymgme.2015.12.009. PMID: 26750748Free PMC Article

Diagnosis

Finsterer J, Scorza FA, Fiorini AC, Scorza CA
Pediatr Neurol 2020 Sep;110:25-29. Epub 2020 Jul 16 doi: 10.1016/j.pediatrneurol.2020.03.009. PMID: 32684373
Young YH
Int J Audiol 2020 Apr;59(4):243-253. Epub 2019 Nov 12 doi: 10.1080/14992027.2019.1689432. PMID: 31714154
Barakat AJ, Raygada M, Rennert OM
Am J Med Genet A 2018 Jun;176(6):1341-1348. Epub 2018 Apr 16 doi: 10.1002/ajmg.a.38693. PMID: 29663634
Wémeau JL, Kopp P
Best Pract Res Clin Endocrinol Metab 2017 Mar;31(2):213-224. Epub 2017 May 10 doi: 10.1016/j.beem.2017.04.011. PMID: 28648509
Girish M, Mujawar N, Salodkar A
Indian Pediatr 2011 Jun;48(6):479-81. doi: 10.1007/s13312-011-0068-z. PMID: 21743113

Therapy

Tan WJT, Song L
Hear Res 2023 Jul;434:108783. Epub 2023 Apr 29 doi: 10.1016/j.heares.2023.108783. PMID: 37167889
Joshua TG, Ayub A, Wijesinghe P, Nunez DA
JAMA Otolaryngol Head Neck Surg 2022 Jan 1;148(1):5-11. doi: 10.1001/jamaoto.2021.2685. PMID: 34709348Free PMC Article
Kuhn M, Heman-Ackah SE, Shaikh JA, Roehm PC
Trends Amplif 2011 Sep;15(3):91-105. Epub 2011 May 22 doi: 10.1177/1084713811408349. PMID: 21606048Free PMC Article
Rauch SD
N Engl J Med 2008 Aug 21;359(8):833-40. doi: 10.1056/NEJMcp0802129. PMID: 18716300
Causse JR, Causse JB, Uriel J, Berges J, Shambaugh GE Jr, Bretlau P
Am J Otol 1993 Sep;14(5):482-90. doi: 10.1097/00129492-199309000-00013. PMID: 8122713

Prognosis

Young YH
Int J Audiol 2020 Apr;59(4):243-253. Epub 2019 Nov 12 doi: 10.1080/14992027.2019.1689432. PMID: 31714154
Phillips JS, Gaunt A, Phillips DR
Otol Neurotol 2014 Jul;35(6):1011-3. doi: 10.1097/MAO.0000000000000361. PMID: 24643028
Karki P, Shrestha JK
Nepal J Ophthalmol 2009 Jul-Dec;1(2):139-40. doi: 10.3126/nepjoph.v1i2.3690. PMID: 21141008
Gifford KA, Holmes MG, Bernstein HH
Pediatr Rev 2009 Jun;30(6):207-15; quiz 216. doi: 10.1542/pir.30-6-207. PMID: 19487429
Gates P
Intern Med J 2005 Aug;35(8):488-9. doi: 10.1111/j.1445-5994.2005.00891.x. PMID: 16176473

Clinical prediction guides

Kalinousky AJ, Luperchio TR, Schrode KM, Harris JR, Zhang L, DeLeon VB, Fahrner JA, Lauer AM, Bjornsson HT
Genes (Basel) 2023 Dec 28;15(1) doi: 10.3390/genes15010048. PMID: 38254937Free PMC Article
McDermott JH, Wolf J, Hoshitsuki K, Huddart R, Caudle KE, Whirl-Carrillo M, Steyger PS, Smith RJH, Cody N, Rodriguez-Antona C, Klein TE, Newman WG
Clin Pharmacol Ther 2022 Feb;111(2):366-372. Epub 2021 Jun 20 doi: 10.1002/cpt.2309. PMID: 34032273Free PMC Article
Wémeau JL, Kopp P
Best Pract Res Clin Endocrinol Metab 2017 Mar;31(2):213-224. Epub 2017 May 10 doi: 10.1016/j.beem.2017.04.011. PMID: 28648509
Kuhn M, Heman-Ackah SE, Shaikh JA, Roehm PC
Trends Amplif 2011 Sep;15(3):91-105. Epub 2011 May 22 doi: 10.1177/1084713811408349. PMID: 21606048Free PMC Article
Jerger J
J Am Acad Audiol 2011 Mar;22(3):128. doi: 10.3766/jaaa.22.3.1. PMID: 21545765

Recent systematic reviews

Plontke SK, Meisner C, Agrawal S, Cayé-Thomasen P, Galbraith K, Mikulec AA, Parnes L, Premakumar Y, Reiber J, Schilder AG, Liebau A
Cochrane Database Syst Rev 2022 Jul 22;7(7):CD008080. doi: 10.1002/14651858.CD008080.pub2. PMID: 35867413Free PMC Article
Joshua TG, Ayub A, Wijesinghe P, Nunez DA
JAMA Otolaryngol Head Neck Surg 2022 Jan 1;148(1):5-11. doi: 10.1001/jamaoto.2021.2685. PMID: 34709348Free PMC Article
Fancello V, Hatzopoulos S, Corazzi V, Bianchini C, Skarżyńska MB, Pelucchi S, Skarżyński PH, Ciorba A
Int J Immunopathol Pharmacol 2021 Jan-Dec;35:20587384211027373. doi: 10.1177/20587384211027373. PMID: 34142589Free PMC Article
Loughrey DG, Kelly ME, Kelley GA, Brennan S, Lawlor BA
JAMA Otolaryngol Head Neck Surg 2018 Feb 1;144(2):115-126. doi: 10.1001/jamaoto.2017.2513. PMID: 29222544Free PMC Article
Lie A, Skogstad M, Johannessen HA, Tynes T, Mehlum IS, Nordby KC, Engdahl B, Tambs K
Int Arch Occup Environ Health 2016 Apr;89(3):351-72. Epub 2015 Aug 7 doi: 10.1007/s00420-015-1083-5. PMID: 26249711Free PMC Article

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